Brazilian Thoracic Association recommendations for the management of lymphangioleiomyomatosis

ABSTRACT Lymphangioleiomyomatosis (LAM) is a rare disease, characterized as a low-grade neoplasm with metastatic potential that mainly affects women of reproductive age, in which there is proliferation of atypical smooth muscle cells (LAM cells) and formation of diffuse pulmonary cysts. It can occur...

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Main Authors: Bruno Guedes Baldi, Paulo Henrique Ramos Feitosa, Adalberto Sperb Rubin, Alexandre Franco Amaral, Carolina Salim Gonçalves Freitas, Cláudia Henrique da Costa, Eliane Viana Mancuzo, Ellen Caroline Toledo do Nascimento, Mariana Sponholz Araujo, Marcelo Jorge Jacó Rocha, Martina Rodrigues de Oliveira, Tatiana Senna Galvão, Pedro Paulo Teixeira e Silva Torres, Carlos Roberto Ribeiro Carvalho
Format: Article
Language:English
Published: Sociedade Brasileira de Pneumologia e Tisiologia 2025-02-01
Series:Jornal Brasileiro de Pneumologia
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Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132025000100700&lng=en&tlng=en
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