Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal Dysplasia

Summary:. Craniometaphyseal dysplasia is a rare congenital sclerosing skeletal dysplasia that presents with facial dimorphism and is clinically described by prominent supraorbital bridges, severe retrognathia, and respiratory problems. Fronto-orbital cranioplasty is necessary to achieve satisfactory...

Full description

Saved in:
Bibliographic Details
Main Authors: Bruno Nifossi Prado, DDS, MSc, Lucas Cavalieri-Pereira, DDS, PhD
Format: Article
Language:English
Published: Wolters Kluwer 2024-12-01
Series:Plastic and Reconstructive Surgery, Global Open
Online Access:http://journals.lww.com/prsgo/fulltext/10.1097/GOX.0000000000006347
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850131039715852288
author Bruno Nifossi Prado, DDS, MSc
Lucas Cavalieri-Pereira, DDS, PhD
author_facet Bruno Nifossi Prado, DDS, MSc
Lucas Cavalieri-Pereira, DDS, PhD
author_sort Bruno Nifossi Prado, DDS, MSc
collection DOAJ
description Summary:. Craniometaphyseal dysplasia is a rare congenital sclerosing skeletal dysplasia that presents with facial dimorphism and is clinically described by prominent supraorbital bridges, severe retrognathia, and respiratory problems. Fronto-orbital cranioplasty is necessary to achieve satisfactory aesthetic outcomes. The supraorbital arches were exposed to the nasal bone through coronal access, with the help of a saw and a wear drill, and osteotomy of the frontal and orbital regions with hyperostosis was performed. Our case report describes a rare and difficult to diagnose case with a few publications of a 24-year-old female patient, who presented with metaphyseal dysplasia associated with mandibular retrognathia. As a treatment, fronto-orbital cranioplasty was performed in association with orthognathic surgery. The resolution of the case resulted in excellent functional and aesthetic results, indicating that frontal cranioplasty associated with orthognathic surgery is a plausible treatment for facial dimorphism through craniometaphyseal dysplasia.
format Article
id doaj-art-65f4b63cfb324955ae105c86e6f4160f
institution OA Journals
issn 2169-7574
language English
publishDate 2024-12-01
publisher Wolters Kluwer
record_format Article
series Plastic and Reconstructive Surgery, Global Open
spelling doaj-art-65f4b63cfb324955ae105c86e6f4160f2025-08-20T02:32:31ZengWolters KluwerPlastic and Reconstructive Surgery, Global Open2169-75742024-12-011212e634710.1097/GOX.0000000000006347202412000-00023Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal DysplasiaBruno Nifossi Prado, DDS, MSc0Lucas Cavalieri-Pereira, DDS, PhD1From the Department of Oral & Maxillofacial Surgery, São Leopoldo Mandic, São Paulo, Brazil.From the Department of Oral & Maxillofacial Surgery, São Leopoldo Mandic, São Paulo, Brazil.Summary:. Craniometaphyseal dysplasia is a rare congenital sclerosing skeletal dysplasia that presents with facial dimorphism and is clinically described by prominent supraorbital bridges, severe retrognathia, and respiratory problems. Fronto-orbital cranioplasty is necessary to achieve satisfactory aesthetic outcomes. The supraorbital arches were exposed to the nasal bone through coronal access, with the help of a saw and a wear drill, and osteotomy of the frontal and orbital regions with hyperostosis was performed. Our case report describes a rare and difficult to diagnose case with a few publications of a 24-year-old female patient, who presented with metaphyseal dysplasia associated with mandibular retrognathia. As a treatment, fronto-orbital cranioplasty was performed in association with orthognathic surgery. The resolution of the case resulted in excellent functional and aesthetic results, indicating that frontal cranioplasty associated with orthognathic surgery is a plausible treatment for facial dimorphism through craniometaphyseal dysplasia.http://journals.lww.com/prsgo/fulltext/10.1097/GOX.0000000000006347
spellingShingle Bruno Nifossi Prado, DDS, MSc
Lucas Cavalieri-Pereira, DDS, PhD
Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal Dysplasia
Plastic and Reconstructive Surgery, Global Open
title Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal Dysplasia
title_full Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal Dysplasia
title_fullStr Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal Dysplasia
title_full_unstemmed Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal Dysplasia
title_short Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal Dysplasia
title_sort combined fronto orbital contouring and orthognathic surgery in craniometaphyseal dysplasia
url http://journals.lww.com/prsgo/fulltext/10.1097/GOX.0000000000006347
work_keys_str_mv AT brunonifossipradoddsmsc combinedfrontoorbitalcontouringandorthognathicsurgeryincraniometaphysealdysplasia
AT lucascavalieripereiraddsphd combinedfrontoorbitalcontouringandorthognathicsurgeryincraniometaphysealdysplasia