Combined Fronto-orbital Contouring and Orthognathic Surgery in Craniometaphyseal Dysplasia

Summary:. Craniometaphyseal dysplasia is a rare congenital sclerosing skeletal dysplasia that presents with facial dimorphism and is clinically described by prominent supraorbital bridges, severe retrognathia, and respiratory problems. Fronto-orbital cranioplasty is necessary to achieve satisfactory...

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Bibliographic Details
Main Authors: Bruno Nifossi Prado, DDS, MSc, Lucas Cavalieri-Pereira, DDS, PhD
Format: Article
Language:English
Published: Wolters Kluwer 2024-12-01
Series:Plastic and Reconstructive Surgery, Global Open
Online Access:http://journals.lww.com/prsgo/fulltext/10.1097/GOX.0000000000006347
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Summary:Summary:. Craniometaphyseal dysplasia is a rare congenital sclerosing skeletal dysplasia that presents with facial dimorphism and is clinically described by prominent supraorbital bridges, severe retrognathia, and respiratory problems. Fronto-orbital cranioplasty is necessary to achieve satisfactory aesthetic outcomes. The supraorbital arches were exposed to the nasal bone through coronal access, with the help of a saw and a wear drill, and osteotomy of the frontal and orbital regions with hyperostosis was performed. Our case report describes a rare and difficult to diagnose case with a few publications of a 24-year-old female patient, who presented with metaphyseal dysplasia associated with mandibular retrognathia. As a treatment, fronto-orbital cranioplasty was performed in association with orthognathic surgery. The resolution of the case resulted in excellent functional and aesthetic results, indicating that frontal cranioplasty associated with orthognathic surgery is a plausible treatment for facial dimorphism through craniometaphyseal dysplasia.
ISSN:2169-7574