Doença de Pompe: estudo clínico e anatomopatológico de um caso Pompe's disease: a clinical and anatomopathological case report

Os autores apresentam um caso de doença de Pompe, estudado do ponto de vista clínico e anatomopatológico, sendo feita revisão da literatura.<br>A case of peculiar form of Pompe's disease is reported and the medical literature is reviewed. The diagnosis was ascertained by necroscopic study...

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Main Authors: Abram Topczewski, Wilson L. Sanvito, Maria Fátima Araújo, Elia Gomes
Format: Article
Language:English
Published: Thieme Revinter Publicações 1974-06-01
Series:Arquivos de Neuro-Psiquiatria
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1974000200009
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author Abram Topczewski
Wilson L. Sanvito
Maria Fátima Araújo
Elia Gomes
author_facet Abram Topczewski
Wilson L. Sanvito
Maria Fátima Araújo
Elia Gomes
author_sort Abram Topczewski
collection DOAJ
description Os autores apresentam um caso de doença de Pompe, estudado do ponto de vista clínico e anatomopatológico, sendo feita revisão da literatura.<br>A case of peculiar form of Pompe's disease is reported and the medical literature is reviewed. The diagnosis was ascertained by necroscopic study. The clinical and eletromyographics aspects are discussed.
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institution OA Journals
issn 0004-282X
1678-4227
language English
publishDate 1974-06-01
publisher Thieme Revinter Publicações
record_format Article
series Arquivos de Neuro-Psiquiatria
spelling doaj-art-6021ef1d61a84d7895f0e3025ef7e9b12025-08-20T01:57:29ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria0004-282X1678-42271974-06-01322147151Doença de Pompe: estudo clínico e anatomopatológico de um caso Pompe's disease: a clinical and anatomopathological case reportAbram TopczewskiWilson L. SanvitoMaria Fátima AraújoElia GomesOs autores apresentam um caso de doença de Pompe, estudado do ponto de vista clínico e anatomopatológico, sendo feita revisão da literatura.<br>A case of peculiar form of Pompe's disease is reported and the medical literature is reviewed. The diagnosis was ascertained by necroscopic study. The clinical and eletromyographics aspects are discussed.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1974000200009
spellingShingle Abram Topczewski
Wilson L. Sanvito
Maria Fátima Araújo
Elia Gomes
Doença de Pompe: estudo clínico e anatomopatológico de um caso Pompe's disease: a clinical and anatomopathological case report
Arquivos de Neuro-Psiquiatria
title Doença de Pompe: estudo clínico e anatomopatológico de um caso Pompe's disease: a clinical and anatomopathological case report
title_full Doença de Pompe: estudo clínico e anatomopatológico de um caso Pompe's disease: a clinical and anatomopathological case report
title_fullStr Doença de Pompe: estudo clínico e anatomopatológico de um caso Pompe's disease: a clinical and anatomopathological case report
title_full_unstemmed Doença de Pompe: estudo clínico e anatomopatológico de um caso Pompe's disease: a clinical and anatomopathological case report
title_short Doença de Pompe: estudo clínico e anatomopatológico de um caso Pompe's disease: a clinical and anatomopathological case report
title_sort doenca de pompe estudo clinico e anatomopatologico de um caso pompe s disease a clinical and anatomopathological case report
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1974000200009
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