A Case Report and Literature Review on Systemic Sclerosis Manifesting as Melena and Hematochezia
Systemic sclerosis (SSc) is a rare autoimmune disorder that leads to progressive fibrosis and vascular dysfunction, frequently affecting the gastrointestinal tract with around 90% of patients experiencing gastrointestinal complications, with severe manifestations such as gastric antral vascular ecta...
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| Format: | Article |
| Language: | English |
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SAGE Publishing
2025-06-01
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| Series: | Journal of Investigative Medicine High Impact Case Reports |
| Online Access: | https://doi.org/10.1177/23247096251348903 |
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| _version_ | 1849688997975031808 |
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| author | Anthony El Gharib MD Léa Nassif MD Karam Karam MD Elias Fiani MD |
| author_facet | Anthony El Gharib MD Léa Nassif MD Karam Karam MD Elias Fiani MD |
| author_sort | Anthony El Gharib MD |
| collection | DOAJ |
| description | Systemic sclerosis (SSc) is a rare autoimmune disorder that leads to progressive fibrosis and vascular dysfunction, frequently affecting the gastrointestinal tract with around 90% of patients experiencing gastrointestinal complications, with severe manifestations such as gastric antral vascular ectasia and rectal telangiectasia which lead to chronic bleeding and iron-deficiency anemia. This review and case report explore the pathophysiology of GI involvement in SSc, emphasizing fibrosis, microvascular damage, and dysmotility. It also highlights treatment options, including endoscopic interventions like argon plasma coagulation and pharmacological therapies. |
| format | Article |
| id | doaj-art-5fe5ce8f63ce4143b37ea5e399931732 |
| institution | DOAJ |
| issn | 2324-7096 |
| language | English |
| publishDate | 2025-06-01 |
| publisher | SAGE Publishing |
| record_format | Article |
| series | Journal of Investigative Medicine High Impact Case Reports |
| spelling | doaj-art-5fe5ce8f63ce4143b37ea5e3999317322025-08-20T03:21:47ZengSAGE PublishingJournal of Investigative Medicine High Impact Case Reports2324-70962025-06-011310.1177/23247096251348903A Case Report and Literature Review on Systemic Sclerosis Manifesting as Melena and HematocheziaAnthony El Gharib MD0Léa Nassif MD1Karam Karam MD2Elias Fiani MD3University of Balamand, Beirut, LebanonUniversity of Balamand, Beirut, LebanonUniversity of Balamand, Beirut, LebanonUniversity of Balamand, Beirut, LebanonSystemic sclerosis (SSc) is a rare autoimmune disorder that leads to progressive fibrosis and vascular dysfunction, frequently affecting the gastrointestinal tract with around 90% of patients experiencing gastrointestinal complications, with severe manifestations such as gastric antral vascular ectasia and rectal telangiectasia which lead to chronic bleeding and iron-deficiency anemia. This review and case report explore the pathophysiology of GI involvement in SSc, emphasizing fibrosis, microvascular damage, and dysmotility. It also highlights treatment options, including endoscopic interventions like argon plasma coagulation and pharmacological therapies.https://doi.org/10.1177/23247096251348903 |
| spellingShingle | Anthony El Gharib MD Léa Nassif MD Karam Karam MD Elias Fiani MD A Case Report and Literature Review on Systemic Sclerosis Manifesting as Melena and Hematochezia Journal of Investigative Medicine High Impact Case Reports |
| title | A Case Report and Literature Review on Systemic Sclerosis Manifesting as Melena and Hematochezia |
| title_full | A Case Report and Literature Review on Systemic Sclerosis Manifesting as Melena and Hematochezia |
| title_fullStr | A Case Report and Literature Review on Systemic Sclerosis Manifesting as Melena and Hematochezia |
| title_full_unstemmed | A Case Report and Literature Review on Systemic Sclerosis Manifesting as Melena and Hematochezia |
| title_short | A Case Report and Literature Review on Systemic Sclerosis Manifesting as Melena and Hematochezia |
| title_sort | case report and literature review on systemic sclerosis manifesting as melena and hematochezia |
| url | https://doi.org/10.1177/23247096251348903 |
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