Imaging features of desmoplakin arrhythmogenic cardiomyopathy: A comparative cardiovascular magnetic resonance study

Imaging features of desmoplakin arrhythmogenic cardiomyopathy: A comparative cardiovascular magnetic resonance study

ABSTRACT: Background: Arrhythmogenic cardiomyopathy (ACM) related to Desmoplakin (DSP) mutations is a distinct condition associated with particularly severe outcomes, more frequent left ventricular (LV) involvement, including fibrosis, dysfunction, and inflammatory episodes. Whether DSP-ACM is asso...

Full description

Saved in:

Bibliographic Details
Main Authors:	Mikael Laredo, Etienne Charpentier, Shannon Soulez, Vincent Nguyen, Annamaria Martino, Leonardo Calò, Flavie Ader, Alexis Hermida, Véronique Fressart, Philippe Charron, Nadjia Kachenoura, Estelle Gandjbakhch, Alban Redheuil
Format:	Article
Language:	English
Published:	Elsevier 2025-01-01
Series:	Journal of Cardiovascular Magnetic Resonance
Subjects:	Arrhythmogenic cardiomyopathy Right or left dominant Biventricular Cardiac magnetic resonance imaging Myocardial fibrosis
Online Access:	http://www.sciencedirect.com/science/article/pii/S1097664725000298
Tags:	Add Tag No Tags, Be the first to tag this record!

Similar Items

Biventricular arrhythmogenic cardiomyopathy and sudden cardiac death: forensic perspectives based on autopsy case report
by: Nora Fnon, et al.
Published: (2025-07-01)

Desmoplakin and features of desmoplakin cardiomyopathy
by: R. P. Myasnikov, et al.
Published: (2023-11-01)

The Diagnostic and Prognostic Value of the 12-Lead ECG in Arrhythmogenic Left Ventricular Cardiomyopathy
by: Leonardo Calò, MD, et al.
Published: (2025-06-01)

Treatment of arrhythmogenic right ventricular cardiomyopathy (dysplasia)
by: M.Т. Vatutin, et al.
Published: (2016-03-01)

A paradigm shift in the concept of arrhythmogenic cardiomyopathy: expanding the clinical and genetic spectrum, new diagnostic criteria for left ventricular phenotypes
by: T. G. Vaikhanskaya, et al.
Published: (2020-11-01)

Signal‐Averaged ECG in the Diagnostic Workup for Arrhythmogenic Cardiomyopathy: Insights From the Nordic ARVC Registry
by: Aleksei A. Savelev, et al.
Published: (2025-03-01)

Identification of Biomarkers of Arrhythmogenic Cardiomyopathy (ACM) by Plasma Proteomics
by: Sinda Zarrouk, et al.
Published: (2025-01-01)

Oxidized LDL‐dependent pathway as new pathogenic trigger in arrhythmogenic cardiomyopathy
by: Elena Sommariva, et al.
Published: (2021-08-01)

An unusual thrombus in a patient with arrhythmogenic cardiomyopathy
by: Sezgin Atmaca, et al.
Published: (2025-03-01)

Exercise Prescription in Arrhythmogenic Cardiomyopathy: Finding the Right Balance Between Risks and Benefits
by: Lorenzo‐Lupo Dei, et al.
Published: (2025-06-01)

Arrhythmogenic right ventricular cardiomyopathy in recipients on heart transplant waiting list
by: M. A. Simonenko, et al.
Published: (2020-08-01)

Arrhythmic Risk Stratification in Patients with Arrhythmogenic Cardiomyopathy
by: Marisa Varrenti, et al.
Published: (2025-04-01)

Spectrum of desmosomal gene variations in patients with arrhythmogenic right ventricular cardiomyopathy
by: A. G. Shestak, et al.
Published: (2021-11-01)

Arrhythmogenic Cardiomyopathy in 8-Year-Old Girl: Clinical Case. Difficult Path to Diagnosis
by: Olga A. Kofeynikova, et al.
Published: (2023-12-01)

Arrhythmogenic Cardiomyopathy with Biventricular Involvement and Right Ventricular Thrombosis: A Multi-modality Imaging Approach
by: Fawaz Bardooli, et al.
Published: (2025-01-01)

Arrhythmogenic Cardiomyopathy in Children. Case Series and Review of the Literature
by: Hagau Asmaa Carla, et al.
Published: (2025-03-01)

A CASE OF DNA-DIAGNOSTICS APPLICATION FOR ARRHYTHMOGENIC RIGHT VENTRICLE CARDIOMYOPATHY
by: A. G. Shestak, et al.
Published: (2016-10-01)

A new prediction model for sustained ventricular tachycardia in arrhythmogenic cardiomyopathy
by: Baowei Zhang, et al.
Published: (2024-12-01)

Plasma CCL3 predicts adverse heart failure outcomes in patients with arrhythmogenic cardiomyopathy
by: Hao Cui, et al.
Published: (2025-04-01)

A rare case of arrhythmogenic right ventricular cardiomyopathy mimicking as myocarditis: A diagnostic pitfall
by: Rajshree Uttamrao Dhadve, et al.
Published: (2025-05-01)

Genetic insights into non-ischemic arrhythmogenic cardiomyopathy: a case report of desmoplakin mutation
by: Jas Virk, et al.
Published: (2025-07-01)

Pulmonary embolism and ventricular tachycardia as the first symptoms of arrhythmogenic right ventricular cardiomyopathy in a 71-year-old woman
by: Alexander Suchodolski, et al.
Published: (2025-06-01)

Acute myocardial infarction-like event in a young patient with biventricular arrhythmogenic cardiomyopathy
by: Y. V. Stavtseva, et al.
Published: (2024-03-01)

Electrocardiographic parameters and features of ventricular arrhythmias in various arrhythmogenic cardiomyopathy forms in the pediatric population: a systematic review and meta-analysis
by: D. Yu. Alekseeva, et al.
Published: (2022-09-01)

The mystery behind recurrent pericardial effusions: A hidden case of arrhythmogenic right ventricular cardiomyopathy
by: Salma Bouyaddid, et al.
Published: (2025-07-01)

Arrhythmogenic Right Ventricular Cardiomyopathy Diagnosed with 2020 International Criteria
by: Neelesh Damor, et al.
Published: (2024-11-01)

Prognostic Value of Strain by Speckle Tracking Echocardiography in Patients with Arrhythmogenic Right Ventricular Cardiomyopathy
by: Areej Aljehani, et al.
Published: (2024-12-01)

FOCUS-GUIDED ENDOMYOCARDIAL BYOPSY IN DIAGNOSTICS OF ARRHYTHMOGENIC DYSPLASIA OF THE RIGHT VENTRICLE IN PATIENTS SCHEDULED FOR CATHETER ABLATION OF VENTRICULAR ARRHYTHMIAS
by: K. A. Simonova, et al.
Published: (2016-07-01)

Navigating the Uncommon: Case Report of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) Successfully Managed with Implantable Cardioverter Defibrillator (ICD)
by: Sidhi Laksono Purwowiyoto, et al.
Published: (2024-10-01)

Clinical characteristics of various arrhythmogenic cardiomyopathy phenotypes in the pediatric population: a systematic review and meta-analysis
by: D. Yu. Alekseeva, et al.
Published: (2022-12-01)

Rapid progression of right ventricular dysfunction: a case report
by: Guoliang Li, et al.
Published: (2025-03-01)

Actionable Variants of Unknown Significance in Inherited Arrhythmogenic Syndromes: A Further Step Forward in Genetic Diagnosis
by: Estefanía Martínez-Barrios, et al.
Published: (2024-11-01)

Natural Course of Electrocardiographic Features in Arrhythmogenic Right Ventricular Cardiomyopathy and Their Relation to Ventricular Arrhythmic Events
by: Anneli Svensson, et al.
Published: (2024-08-01)

Analysis of the left ventricular involvement in patients with a biventricular phenotype of arrhythmogenic ardiomyopathy: a case series description
by: S. M. Komissarova, et al.
Published: (2023-03-01)

Evolution of diagnostic criteria for arrhythmogenic right ventricular cardiomyopathy and their application in clinical practice
by: Yu. A. Lutokhina, et al.
Published: (2021-12-01)

Case report: Severe arrhythmogenic cardiomyopathy in a young girl with compound heterozygous DSG2 and MYBPC3 variants with a 6-year follow-up
by: Ryotaro Hashizume, et al.
Published: (2025-03-01)

Contribution of concomitant myocarditis to the development of various clinical types of arrhythmogenic right ventricular cardiomyopathy
by: Yu. A. Lutokhina, et al.
Published: (2021-09-01)

Cardiac magnetic resonance imaging in arrhythmogenic cardiomyopathy: evolving diagnostic criteria and new capabilities
by: S A. Aleksandrova, et al.
Published: (2024-12-01)

CLINICAL TYPES (CLASSIFICATION) OF THE RIGHT VENTRICLE ARRHYTHMOGENIC DYSPLASIA: SPECIFICS OF DIAGNOSTICS AND MANAGEMENT
by: Yu. A. Lutokhina, et al.
Published: (2018-03-01)

Naxos Disease and Related Cardio-Cutaneous Syndromes
by: Alexandros Protonotarios, MD, et al.
Published: (2025-02-01)