ANCA-associated Leucocytoclastic Vasculitis presenting with Bronchiectasis, GI Involvement and Hypertensive Urgency: A Complex Case without Renal Involvement

Introduction: Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitides (AAV) are autoimmune diseases characterized by inflammation of small to medium blood vessels. This case explores AAV pathophysiology, its link to bronchiectasis and leucocytoclasia, ANCA positivity, and current treatmen...

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Main Authors: N. M. M. Risly, I. K. Jayasinghe, N. Athauda, E. M. C. B. Ekanayake, S. Hettige, J. F. Sahana
Format: Article
Language:English
Published: The Kandy Society of Medicine 2024-12-01
Series:Sri Lanka Journal of Medicine
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Online Access:https://account.sljm.sljol.info/index.php/sljo-j-sljm2/article/view/552
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author N. M. M. Risly
I. K. Jayasinghe
N. Athauda
E. M. C. B. Ekanayake
S. Hettige
J. F. Sahana
author_facet N. M. M. Risly
I. K. Jayasinghe
N. Athauda
E. M. C. B. Ekanayake
S. Hettige
J. F. Sahana
author_sort N. M. M. Risly
collection DOAJ
description Introduction: Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitides (AAV) are autoimmune diseases characterized by inflammation of small to medium blood vessels. This case explores AAV pathophysiology, its link to bronchiectasis and leucocytoclasia, ANCA positivity, and current treatment guidelines. Case Presentation: A 48-year-old with abdominal pain, rash, hypertensive urgency, and respiratory symptoms was diagnosed with AAV, confirmed by skin biopsy and positive C-ANCA, stool occult blood with negative abdominal imaging along with bronchiectasis on HRCT. The patient initially failed to respond to broad-spectrum antibiotics but improved with high-dose corticosteroids. Conclusion: We highlight an atypical presentation of AAV, showing the importance of timely immunosuppressive therapy for favorable outcomes.
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publishDate 2024-12-01
publisher The Kandy Society of Medicine
record_format Article
series Sri Lanka Journal of Medicine
spelling doaj-art-5f231cad86fa42a58daff577a37f0b7e2025-08-20T01:58:27ZengThe Kandy Society of MedicineSri Lanka Journal of Medicine2579-19902024-12-01333667010.4038/sljm.v33i3.552552ANCA-associated Leucocytoclastic Vasculitis presenting with Bronchiectasis, GI Involvement and Hypertensive Urgency: A Complex Case without Renal InvolvementN. M. M. Risly0https://orcid.org/0009-0000-4743-5034I. K. Jayasinghe1N. Athauda2E. M. C. B. Ekanayake3S. Hettige4J. F. Sahana5National Hospital KandyNational Hospital KandyNational Hospital KandyNational Hospital KandyNational Hospital KandyUniversity of PeradeniyaIntroduction: Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitides (AAV) are autoimmune diseases characterized by inflammation of small to medium blood vessels. This case explores AAV pathophysiology, its link to bronchiectasis and leucocytoclasia, ANCA positivity, and current treatment guidelines. Case Presentation: A 48-year-old with abdominal pain, rash, hypertensive urgency, and respiratory symptoms was diagnosed with AAV, confirmed by skin biopsy and positive C-ANCA, stool occult blood with negative abdominal imaging along with bronchiectasis on HRCT. The patient initially failed to respond to broad-spectrum antibiotics but improved with high-dose corticosteroids. Conclusion: We highlight an atypical presentation of AAV, showing the importance of timely immunosuppressive therapy for favorable outcomes.https://account.sljm.sljol.info/index.php/sljo-j-sljm2/article/view/552anca associated vasculitisbronchiectasisleucocytoclastic vasculitis
spellingShingle N. M. M. Risly
I. K. Jayasinghe
N. Athauda
E. M. C. B. Ekanayake
S. Hettige
J. F. Sahana
ANCA-associated Leucocytoclastic Vasculitis presenting with Bronchiectasis, GI Involvement and Hypertensive Urgency: A Complex Case without Renal Involvement
Sri Lanka Journal of Medicine
anca associated vasculitis
bronchiectasis
leucocytoclastic vasculitis
title ANCA-associated Leucocytoclastic Vasculitis presenting with Bronchiectasis, GI Involvement and Hypertensive Urgency: A Complex Case without Renal Involvement
title_full ANCA-associated Leucocytoclastic Vasculitis presenting with Bronchiectasis, GI Involvement and Hypertensive Urgency: A Complex Case without Renal Involvement
title_fullStr ANCA-associated Leucocytoclastic Vasculitis presenting with Bronchiectasis, GI Involvement and Hypertensive Urgency: A Complex Case without Renal Involvement
title_full_unstemmed ANCA-associated Leucocytoclastic Vasculitis presenting with Bronchiectasis, GI Involvement and Hypertensive Urgency: A Complex Case without Renal Involvement
title_short ANCA-associated Leucocytoclastic Vasculitis presenting with Bronchiectasis, GI Involvement and Hypertensive Urgency: A Complex Case without Renal Involvement
title_sort anca associated leucocytoclastic vasculitis presenting with bronchiectasis gi involvement and hypertensive urgency a complex case without renal involvement
topic anca associated vasculitis
bronchiectasis
leucocytoclastic vasculitis
url https://account.sljm.sljol.info/index.php/sljo-j-sljm2/article/view/552
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