Atypical Parathyroid Adenoma Complicated with Protracted Hungry Bone Syndrome after Surgery: A Case Report and Literature Review

Hungry Bone Syndrome refers to the severe and prolonged hypocalcemia and hypophosphatemia, following parathyroidectomy in patients with hyperparathyroidism. We present the case of an eighteen-year-old woman with a four-year history of hyporexia, polydipsia, weight loss, growth retardation, and poor...

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Main Authors: Óscar Alfredo Juárez-León, Miguel Ángel Gómez-Sámano, Daniel Cuevas-Ramos, Paloma Almeda-Valdés, Manuel Alejandro López-Flores A La Torre, Alfredo Adolfo Reza-Albarrán, Francisco Javier Gómez-Pérez
Format: Article
Language:English
Published: Wiley 2015-01-01
Series:Case Reports in Endocrinology
Online Access:http://dx.doi.org/10.1155/2015/757951
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author Óscar Alfredo Juárez-León
Miguel Ángel Gómez-Sámano
Daniel Cuevas-Ramos
Paloma Almeda-Valdés
Manuel Alejandro López-Flores A La Torre
Alfredo Adolfo Reza-Albarrán
Francisco Javier Gómez-Pérez
author_facet Óscar Alfredo Juárez-León
Miguel Ángel Gómez-Sámano
Daniel Cuevas-Ramos
Paloma Almeda-Valdés
Manuel Alejandro López-Flores A La Torre
Alfredo Adolfo Reza-Albarrán
Francisco Javier Gómez-Pérez
author_sort Óscar Alfredo Juárez-León
collection DOAJ
description Hungry Bone Syndrome refers to the severe and prolonged hypocalcemia and hypophosphatemia, following parathyroidectomy in patients with hyperparathyroidism. We present the case of an eighteen-year-old woman with a four-year history of hyporexia, polydipsia, weight loss, growth retardation, and poor academic performance. The diagnostic work-up demonstrated primary hyperparathyroidism with hypercalcemia of 13.36 mg/dL, a PTH level of 2551 pg/mL, bone brown tumors, and microcalcifications within pancreas and kidneys. Neck ultrasonography revealed a parathyroid adenoma of 33 × 14 × 14 mm, also identified on 99Tc-sestamibi scan. Bone densitometry showed decreased Z-Score values (total lumbar Z-Score of −4.2). A right hemithyroidectomy and right lower parathyroidectomy were performed. Pathological examination showed an atypical parathyroid adenoma, of 3.8 g of weight and 2.8 cm in diameter. After surgery she developed hypocalcemia with tetany and QTc interval prolongation. The patient required 3 months of oral and intravenous calcium supplementation due to Hungry Bone Syndrome (HBS). After 42 months, she is still under oral calcium. Usually HBS lasts less than 12 months. Therefore we propose the term “Protracted HBS” in patients with particularly long recovery of 1 year. We present a literature review of the diagnosis, pathophysiology, and treatment of HBS.
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spelling doaj-art-5eeb4b67caaf4d8ba960e922ecf9b74a2025-08-20T03:34:22ZengWileyCase Reports in Endocrinology2090-65012090-651X2015-01-01201510.1155/2015/757951757951Atypical Parathyroid Adenoma Complicated with Protracted Hungry Bone Syndrome after Surgery: A Case Report and Literature ReviewÓscar Alfredo Juárez-León0Miguel Ángel Gómez-Sámano1Daniel Cuevas-Ramos2Paloma Almeda-Valdés3Manuel Alejandro López-Flores A La Torre4Alfredo Adolfo Reza-Albarrán5Francisco Javier Gómez-Pérez6Endocrinology and Metabolism Department, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, 14080 Mexico City, MexicoEndocrinology and Metabolism Department, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, 14080 Mexico City, MexicoEndocrinology and Metabolism Department, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, 14080 Mexico City, MexicoEndocrinology and Metabolism Department, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, 14080 Mexico City, MexicoSchool of Medicine, Universidad Panamericana, 03920 Mexico City, MexicoEndocrinology and Metabolism Department, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, 14080 Mexico City, MexicoEndocrinology and Metabolism Department, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, 14080 Mexico City, MexicoHungry Bone Syndrome refers to the severe and prolonged hypocalcemia and hypophosphatemia, following parathyroidectomy in patients with hyperparathyroidism. We present the case of an eighteen-year-old woman with a four-year history of hyporexia, polydipsia, weight loss, growth retardation, and poor academic performance. The diagnostic work-up demonstrated primary hyperparathyroidism with hypercalcemia of 13.36 mg/dL, a PTH level of 2551 pg/mL, bone brown tumors, and microcalcifications within pancreas and kidneys. Neck ultrasonography revealed a parathyroid adenoma of 33 × 14 × 14 mm, also identified on 99Tc-sestamibi scan. Bone densitometry showed decreased Z-Score values (total lumbar Z-Score of −4.2). A right hemithyroidectomy and right lower parathyroidectomy were performed. Pathological examination showed an atypical parathyroid adenoma, of 3.8 g of weight and 2.8 cm in diameter. After surgery she developed hypocalcemia with tetany and QTc interval prolongation. The patient required 3 months of oral and intravenous calcium supplementation due to Hungry Bone Syndrome (HBS). After 42 months, she is still under oral calcium. Usually HBS lasts less than 12 months. Therefore we propose the term “Protracted HBS” in patients with particularly long recovery of 1 year. We present a literature review of the diagnosis, pathophysiology, and treatment of HBS.http://dx.doi.org/10.1155/2015/757951
spellingShingle Óscar Alfredo Juárez-León
Miguel Ángel Gómez-Sámano
Daniel Cuevas-Ramos
Paloma Almeda-Valdés
Manuel Alejandro López-Flores A La Torre
Alfredo Adolfo Reza-Albarrán
Francisco Javier Gómez-Pérez
Atypical Parathyroid Adenoma Complicated with Protracted Hungry Bone Syndrome after Surgery: A Case Report and Literature Review
Case Reports in Endocrinology
title Atypical Parathyroid Adenoma Complicated with Protracted Hungry Bone Syndrome after Surgery: A Case Report and Literature Review
title_full Atypical Parathyroid Adenoma Complicated with Protracted Hungry Bone Syndrome after Surgery: A Case Report and Literature Review
title_fullStr Atypical Parathyroid Adenoma Complicated with Protracted Hungry Bone Syndrome after Surgery: A Case Report and Literature Review
title_full_unstemmed Atypical Parathyroid Adenoma Complicated with Protracted Hungry Bone Syndrome after Surgery: A Case Report and Literature Review
title_short Atypical Parathyroid Adenoma Complicated with Protracted Hungry Bone Syndrome after Surgery: A Case Report and Literature Review
title_sort atypical parathyroid adenoma complicated with protracted hungry bone syndrome after surgery a case report and literature review
url http://dx.doi.org/10.1155/2015/757951
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