Autoimmune/autoinflammatory syndrome induced by adjuvants after multi-component meningococcal serogroup B vaccination in a 7-year-old girl: a case report

Background. Vaccines, which make it possible to be protected from many life-threatening infectious diseases, have been used safely and effectively for years. Most vaccines used today contain a variety of adjuvants and exogenous proteins. Severe reactions, in addition to transient and self-lim...

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Main Authors: Özge Atay, Suna Asilsoy, Gizem Atakul, Serdar Al, Özge Kangallı Boyacıoğlu, Tayfun Çinleti, Nevin Uzuner, Özlem Giray Bozkaya, Özkan Karaman
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2022-04-01
Series:The Turkish Journal of Pediatrics
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Online Access:https://turkjpediatr.org/article/view/158
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author Özge Atay
Suna Asilsoy
Gizem Atakul
Serdar Al
Özge Kangallı Boyacıoğlu
Tayfun Çinleti
Nevin Uzuner
Özlem Giray Bozkaya
Özkan Karaman
author_facet Özge Atay
Suna Asilsoy
Gizem Atakul
Serdar Al
Özge Kangallı Boyacıoğlu
Tayfun Çinleti
Nevin Uzuner
Özlem Giray Bozkaya
Özkan Karaman
author_sort Özge Atay
collection DOAJ
description Background. Vaccines, which make it possible to be protected from many life-threatening infectious diseases, have been used safely and effectively for years. Most vaccines used today contain a variety of adjuvants and exogenous proteins. Severe reactions, in addition to transient and self-limiting mild reactions, mostly caused by these components, have been reported. The effects of vaccine adjuvants on the pathogenesis of immunemediated diseases are still under investigation. The syndrome called Autoimmune/inflammatory syndrome induced by adjuvants (ASIA) has been defined in the literature. Case. We found a novel mutation of autoinflammatory diseases in the genetic analysis of our patient. The patient developed symptoms of prolonged fever, rash, arthritis and serositis after multicomponent serogroup B meningococcal (Bexsero®) vaccination, without a previously known rheumatic disease. In the presence of clinical findings in our patient, the diagnostic criteria of ASIA syndrome were met. Conclusion. To the best of our knowledge, this is the first case report of a patient diagnosed with the autoinflammatory disease with a novel mutation after Bexsero® vaccination. We consider that genetic examinations will be useful in patients with a systemic vaccine reaction in the presence of ASIA when diagnostic criteria are met.
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institution DOAJ
issn 0041-4301
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language English
publishDate 2022-04-01
publisher Hacettepe University Institute of Child Health
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series The Turkish Journal of Pediatrics
spelling doaj-art-5ea1708cfb4144b28124de4642c15e9c2025-08-20T02:55:41ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64212022-04-0164210.24953/turkjped.2020.2842Autoimmune/autoinflammatory syndrome induced by adjuvants after multi-component meningococcal serogroup B vaccination in a 7-year-old girl: a case reportÖzge Atay0Suna Asilsoy1Gizem Atakul2Serdar Al3Özge Kangallı Boyacıoğlu4Tayfun Çinleti5Nevin Uzuner6Özlem Giray Bozkaya7Özkan KaramanDepartments of Pediatric Immunology and Allergy, okuz Eylül University Faculty of Medicine, İzmir, Turkey.Departments of Pediatric Immunology and Allergy, okuz Eylül University Faculty of Medicine, İzmir, Turkey.Departments of Pediatric Immunology and Allergy, okuz Eylül University Faculty of Medicine, İzmir, Turkey.Departments of Pediatric Immunology and Allergy, okuz Eylül University Faculty of Medicine, İzmir, Turkey.Departments of Pediatric Immunology and Allergy, okuz Eylül University Faculty of Medicine, İzmir, Turkey.Departments of Pediatric Genetics, okuz Eylül University Faculty of Medicine, İzmir, Turkey.Departments of Pediatric Immunology and Allergy, okuz Eylül University Faculty of Medicine, İzmir, Turkey.Departments of Pediatric Genetics, okuz Eylül University Faculty of Medicine, İzmir, Turkey. Background. Vaccines, which make it possible to be protected from many life-threatening infectious diseases, have been used safely and effectively for years. Most vaccines used today contain a variety of adjuvants and exogenous proteins. Severe reactions, in addition to transient and self-limiting mild reactions, mostly caused by these components, have been reported. The effects of vaccine adjuvants on the pathogenesis of immunemediated diseases are still under investigation. The syndrome called Autoimmune/inflammatory syndrome induced by adjuvants (ASIA) has been defined in the literature. Case. We found a novel mutation of autoinflammatory diseases in the genetic analysis of our patient. The patient developed symptoms of prolonged fever, rash, arthritis and serositis after multicomponent serogroup B meningococcal (Bexsero®) vaccination, without a previously known rheumatic disease. In the presence of clinical findings in our patient, the diagnostic criteria of ASIA syndrome were met. Conclusion. To the best of our knowledge, this is the first case report of a patient diagnosed with the autoinflammatory disease with a novel mutation after Bexsero® vaccination. We consider that genetic examinations will be useful in patients with a systemic vaccine reaction in the presence of ASIA when diagnostic criteria are met. https://turkjpediatr.org/article/view/158ASIA syndromeadjuvantsautoimmune diseasescryopyrin-associated periodic syndromesvaccines
spellingShingle Özge Atay
Suna Asilsoy
Gizem Atakul
Serdar Al
Özge Kangallı Boyacıoğlu
Tayfun Çinleti
Nevin Uzuner
Özlem Giray Bozkaya
Özkan Karaman
Autoimmune/autoinflammatory syndrome induced by adjuvants after multi-component meningococcal serogroup B vaccination in a 7-year-old girl: a case report
The Turkish Journal of Pediatrics
ASIA syndrome
adjuvants
autoimmune diseases
cryopyrin-associated periodic syndromes
vaccines
title Autoimmune/autoinflammatory syndrome induced by adjuvants after multi-component meningococcal serogroup B vaccination in a 7-year-old girl: a case report
title_full Autoimmune/autoinflammatory syndrome induced by adjuvants after multi-component meningococcal serogroup B vaccination in a 7-year-old girl: a case report
title_fullStr Autoimmune/autoinflammatory syndrome induced by adjuvants after multi-component meningococcal serogroup B vaccination in a 7-year-old girl: a case report
title_full_unstemmed Autoimmune/autoinflammatory syndrome induced by adjuvants after multi-component meningococcal serogroup B vaccination in a 7-year-old girl: a case report
title_short Autoimmune/autoinflammatory syndrome induced by adjuvants after multi-component meningococcal serogroup B vaccination in a 7-year-old girl: a case report
title_sort autoimmune autoinflammatory syndrome induced by adjuvants after multi component meningococcal serogroup b vaccination in a 7 year old girl a case report
topic ASIA syndrome
adjuvants
autoimmune diseases
cryopyrin-associated periodic syndromes
vaccines
url https://turkjpediatr.org/article/view/158
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