Pituitary Gland and Neurological Involvement in a Case of Hemophagocytic Syndrome Revealing an Intravascular Large B-Cell Lymphoma
Intravascular large B-cell lymphoma is a rare entity characterized by the proliferation of neoplastic lymphocytes in the lumen of small blood vessels and high mortality. Diagnosis of intravascular lymphoma is often delayed or established postmortem. Here, we report the case of a 48-year-old woman pr...
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| Format: | Article |
| Language: | English |
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Wiley
2019-01-01
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| Series: | Case Reports in Hematology |
| Online Access: | http://dx.doi.org/10.1155/2019/9625075 |
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| author | Sylvain Raoul Simeni Njonnou Bruno Couturier Yannick Gombeir Sylvain Verbanck France Devuyst Georges El Hachem Ivan Theate Anne-Laure Trepant Virginie De Wilde Frédéric-Alain Vandergheynst |
| author_facet | Sylvain Raoul Simeni Njonnou Bruno Couturier Yannick Gombeir Sylvain Verbanck France Devuyst Georges El Hachem Ivan Theate Anne-Laure Trepant Virginie De Wilde Frédéric-Alain Vandergheynst |
| author_sort | Sylvain Raoul Simeni Njonnou |
| collection | DOAJ |
| description | Intravascular large B-cell lymphoma is a rare entity characterized by the proliferation of neoplastic lymphocytes in the lumen of small blood vessels and high mortality. Diagnosis of intravascular lymphoma is often delayed or established postmortem. Here, we report the case of a 48-year-old woman presenting hemophagocytic syndrome, with pituitary gland and neurological involvement. Diagnosis of intravascular large B-cell lymphoma was made on perisplenic vessels, while liver and bone marrow biopsy was noncontributive. This case demonstrates the importance of thorough histopathologic investigations in the setting of high suspicion. |
| format | Article |
| id | doaj-art-5dbf1cda94634e1fbc9a1819eb2722eb |
| institution | OA Journals |
| issn | 2090-6560 2090-6579 |
| language | English |
| publishDate | 2019-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Hematology |
| spelling | doaj-art-5dbf1cda94634e1fbc9a1819eb2722eb2025-08-20T02:06:03ZengWileyCase Reports in Hematology2090-65602090-65792019-01-01201910.1155/2019/96250759625075Pituitary Gland and Neurological Involvement in a Case of Hemophagocytic Syndrome Revealing an Intravascular Large B-Cell LymphomaSylvain Raoul Simeni Njonnou0Bruno Couturier1Yannick Gombeir2Sylvain Verbanck3France Devuyst4Georges El Hachem5Ivan Theate6Anne-Laure Trepant7Virginie De Wilde8Frédéric-Alain Vandergheynst9Department of Internal Medicine and Specialties, Faculty of Medicine and Biomedical Sciences, University of Yaounde I, Yaoundé, CameroonDepartment of Internal Medicine, Hôpital Erasme, Université Libre de Bruxelles, Brussels, BelgiumDepartment of Internal Medicine, Hôpital Erasme, Université Libre de Bruxelles, Brussels, BelgiumDepartment of Internal Medicine, Hôpital Erasme, Université Libre de Bruxelles, Brussels, BelgiumDepartment of Endocrinology, Hôpital Erasme, Université Libre de Bruxelles, Brussels, BelgiumDepartment of Internal Medicine, Hôpital Erasme, Université Libre de Bruxelles, Brussels, BelgiumInstitute of Pathology and Genetics, Gosselies, Charleroi, BelgiumDepartment of Pathology, Hôpital Erasme, Université Libre de Bruxelles, Brussels, BelgiumDepartment of Hematology, Hôpital Erasme, Université Libre de Bruxelles, Brussels, BelgiumDepartment of Internal Medicine, Hôpital Erasme, Université Libre de Bruxelles, Brussels, BelgiumIntravascular large B-cell lymphoma is a rare entity characterized by the proliferation of neoplastic lymphocytes in the lumen of small blood vessels and high mortality. Diagnosis of intravascular lymphoma is often delayed or established postmortem. Here, we report the case of a 48-year-old woman presenting hemophagocytic syndrome, with pituitary gland and neurological involvement. Diagnosis of intravascular large B-cell lymphoma was made on perisplenic vessels, while liver and bone marrow biopsy was noncontributive. This case demonstrates the importance of thorough histopathologic investigations in the setting of high suspicion.http://dx.doi.org/10.1155/2019/9625075 |
| spellingShingle | Sylvain Raoul Simeni Njonnou Bruno Couturier Yannick Gombeir Sylvain Verbanck France Devuyst Georges El Hachem Ivan Theate Anne-Laure Trepant Virginie De Wilde Frédéric-Alain Vandergheynst Pituitary Gland and Neurological Involvement in a Case of Hemophagocytic Syndrome Revealing an Intravascular Large B-Cell Lymphoma Case Reports in Hematology |
| title | Pituitary Gland and Neurological Involvement in a Case of Hemophagocytic Syndrome Revealing an Intravascular Large B-Cell Lymphoma |
| title_full | Pituitary Gland and Neurological Involvement in a Case of Hemophagocytic Syndrome Revealing an Intravascular Large B-Cell Lymphoma |
| title_fullStr | Pituitary Gland and Neurological Involvement in a Case of Hemophagocytic Syndrome Revealing an Intravascular Large B-Cell Lymphoma |
| title_full_unstemmed | Pituitary Gland and Neurological Involvement in a Case of Hemophagocytic Syndrome Revealing an Intravascular Large B-Cell Lymphoma |
| title_short | Pituitary Gland and Neurological Involvement in a Case of Hemophagocytic Syndrome Revealing an Intravascular Large B-Cell Lymphoma |
| title_sort | pituitary gland and neurological involvement in a case of hemophagocytic syndrome revealing an intravascular large b cell lymphoma |
| url | http://dx.doi.org/10.1155/2019/9625075 |
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