Dermatomyositis-Associated Interstitial Lung Disease Misdiagnosed as Pulmonary Tuberculosis
Dermatomyositis (DM) is a rare idiopathic inflammatory myopathy with hallmark skin manifestations and, in some cases, interstitial lung disease (ILD). This case report presents a 35-year-old male with chronic cough and constitutional symptoms, initially resembling pulmonary tuberculosis (TB). As the...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2025-01-01
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| Series: | Nigerian Journal of Medicine |
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| Online Access: | https://journals.lww.com/10.4103/NJM.NJM_105_24 |
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| author | Abubakar Sadiq Maiyaki Aminu Abbas Ibrahim Abdullahi Isa Musa Wasagu Nasiru Aaltine Dankiri Olisa Ochiagha Farouk Kabir Umar Aliyu Abullahi |
| author_facet | Abubakar Sadiq Maiyaki Aminu Abbas Ibrahim Abdullahi Isa Musa Wasagu Nasiru Aaltine Dankiri Olisa Ochiagha Farouk Kabir Umar Aliyu Abullahi |
| author_sort | Abubakar Sadiq Maiyaki |
| collection | DOAJ |
| description | Dermatomyositis (DM) is a rare idiopathic inflammatory myopathy with hallmark skin manifestations and, in some cases, interstitial lung disease (ILD). This case report presents a 35-year-old male with chronic cough and constitutional symptoms, initially resembling pulmonary tuberculosis (TB). As the condition progressed, the patient developed proximal muscle weakness, arthralgia, Gottron’s papules and the holster sign. Further testing revealed positive antinuclear antibodies, anti-Mi-2, and anti-Jo-1 antibodies, restrictive lung pattern on pulmonary function test and high-resolution computer tomography (HRCT) features of non-specific interstitial pneumonia (NSIP), confirming dermatomyositis-associated interstitial lung disease (DM-ILD). This report discusses the diagnostic challenges posed by DM-ILD when it mimics pulmonary TB and highlights the importance of a comprehensive autoimmune workup in cases with atypical presentations. A timely diagnosis and management of DM-ILD are crucial to prevent disease progression and improve patient outcomes. |
| format | Article |
| id | doaj-art-5d6420cfd88e45c387f72bca478839e5 |
| institution | OA Journals |
| issn | 1115-2613 2667-0526 |
| language | English |
| publishDate | 2025-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Nigerian Journal of Medicine |
| spelling | doaj-art-5d6420cfd88e45c387f72bca478839e52025-08-20T02:02:51ZengWolters Kluwer Medknow PublicationsNigerian Journal of Medicine1115-26132667-05262025-01-01341808210.4103/NJM.NJM_105_24Dermatomyositis-Associated Interstitial Lung Disease Misdiagnosed as Pulmonary TuberculosisAbubakar Sadiq MaiyakiAminu AbbasIbrahim AbdullahiIsa Musa WasaguNasiru Aaltine DankiriOlisa OchiaghaFarouk Kabir UmarAliyu AbullahiDermatomyositis (DM) is a rare idiopathic inflammatory myopathy with hallmark skin manifestations and, in some cases, interstitial lung disease (ILD). This case report presents a 35-year-old male with chronic cough and constitutional symptoms, initially resembling pulmonary tuberculosis (TB). As the condition progressed, the patient developed proximal muscle weakness, arthralgia, Gottron’s papules and the holster sign. Further testing revealed positive antinuclear antibodies, anti-Mi-2, and anti-Jo-1 antibodies, restrictive lung pattern on pulmonary function test and high-resolution computer tomography (HRCT) features of non-specific interstitial pneumonia (NSIP), confirming dermatomyositis-associated interstitial lung disease (DM-ILD). This report discusses the diagnostic challenges posed by DM-ILD when it mimics pulmonary TB and highlights the importance of a comprehensive autoimmune workup in cases with atypical presentations. A timely diagnosis and management of DM-ILD are crucial to prevent disease progression and improve patient outcomes.https://journals.lww.com/10.4103/NJM.NJM_105_24dermatomyositisidiopathic inflammatory myositisinterstitial lung diseasepulmonary tuberculosis |
| spellingShingle | Abubakar Sadiq Maiyaki Aminu Abbas Ibrahim Abdullahi Isa Musa Wasagu Nasiru Aaltine Dankiri Olisa Ochiagha Farouk Kabir Umar Aliyu Abullahi Dermatomyositis-Associated Interstitial Lung Disease Misdiagnosed as Pulmonary Tuberculosis Nigerian Journal of Medicine dermatomyositis idiopathic inflammatory myositis interstitial lung disease pulmonary tuberculosis |
| title | Dermatomyositis-Associated Interstitial Lung Disease Misdiagnosed as Pulmonary Tuberculosis |
| title_full | Dermatomyositis-Associated Interstitial Lung Disease Misdiagnosed as Pulmonary Tuberculosis |
| title_fullStr | Dermatomyositis-Associated Interstitial Lung Disease Misdiagnosed as Pulmonary Tuberculosis |
| title_full_unstemmed | Dermatomyositis-Associated Interstitial Lung Disease Misdiagnosed as Pulmonary Tuberculosis |
| title_short | Dermatomyositis-Associated Interstitial Lung Disease Misdiagnosed as Pulmonary Tuberculosis |
| title_sort | dermatomyositis associated interstitial lung disease misdiagnosed as pulmonary tuberculosis |
| topic | dermatomyositis idiopathic inflammatory myositis interstitial lung disease pulmonary tuberculosis |
| url | https://journals.lww.com/10.4103/NJM.NJM_105_24 |
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