A Rare Combination of Tetralogy of Fallot and a Complete Atrioventricular Septal Defect: A Case Report

Tetralogy of Fallot (TOF) and a complete atrioventricular septal defect—TOF-atrioventricular (AV) canal defect is a very rare complex congenital heart defect. A very high index of suspicion is crucial for making a diagnosis. AYZ is a 7-year-old male who presented with breathlessness, bluish discolor...

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Main Authors: Josephat M. Chinawa, Awoere T. Chinawa, Jude T. Onyia, Chiesonu D. Nzeduba, Nonyelum C. Maduka, Ogonna O. Nwankwo, Samuel Agwu
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2025-07-01
Series:International Journal of Medicine and Health Development
Subjects:
Online Access:https://doi.org/10.4103/ijmh.ijmh_73_24
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author Josephat M. Chinawa
Awoere T. Chinawa
Jude T. Onyia
Chiesonu D. Nzeduba
Nonyelum C. Maduka
Ogonna O. Nwankwo
Samuel Agwu
author_facet Josephat M. Chinawa
Awoere T. Chinawa
Jude T. Onyia
Chiesonu D. Nzeduba
Nonyelum C. Maduka
Ogonna O. Nwankwo
Samuel Agwu
author_sort Josephat M. Chinawa
collection DOAJ
description Tetralogy of Fallot (TOF) and a complete atrioventricular septal defect—TOF-atrioventricular (AV) canal defect is a very rare complex congenital heart defect. A very high index of suspicion is crucial for making a diagnosis. AYZ is a 7-year-old male who presented with breathlessness, bluish discoloration of the buccal mucosa, and easy tiredness. Examination showed a child in mild respiratory distress, with hyperemic conjunctiva, and saturates at 80% in room air with grade 4 finger clubbing and grade 3 ejection systolic murmur maximal at the second upper inter-space and soft second heart sound. Echocardiography showed a diagnosis of TOF-AV canal defect. The child was commenced on oral propranolol and an anti-failure regimen and is now being worked up for surgery. A very high index of suspicion is key in the early diagnosis and management of this rare complex cardiac anomaly.
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spelling doaj-art-5beec6566af143e782f05dfe8d0e3ca62025-08-20T03:49:56ZengWolters Kluwer Medknow PublicationsInternational Journal of Medicine and Health Development2635-36952667-28632025-07-0130331731910.4103/ijmh.ijmh_73_24A Rare Combination of Tetralogy of Fallot and a Complete Atrioventricular Septal Defect: A Case ReportJosephat M. ChinawaAwoere T. ChinawaJude T. OnyiaChiesonu D. NzedubaNonyelum C. MadukaOgonna O. NwankwoSamuel AgwuTetralogy of Fallot (TOF) and a complete atrioventricular septal defect—TOF-atrioventricular (AV) canal defect is a very rare complex congenital heart defect. A very high index of suspicion is crucial for making a diagnosis. AYZ is a 7-year-old male who presented with breathlessness, bluish discoloration of the buccal mucosa, and easy tiredness. Examination showed a child in mild respiratory distress, with hyperemic conjunctiva, and saturates at 80% in room air with grade 4 finger clubbing and grade 3 ejection systolic murmur maximal at the second upper inter-space and soft second heart sound. Echocardiography showed a diagnosis of TOF-AV canal defect. The child was commenced on oral propranolol and an anti-failure regimen and is now being worked up for surgery. A very high index of suspicion is key in the early diagnosis and management of this rare complex cardiac anomaly.https://doi.org/10.4103/ijmh.ijmh_73_24childrencomplete atrioventricular septal defectechocardiographyejection systolic murmurraretetralogy of fallot
spellingShingle Josephat M. Chinawa
Awoere T. Chinawa
Jude T. Onyia
Chiesonu D. Nzeduba
Nonyelum C. Maduka
Ogonna O. Nwankwo
Samuel Agwu
A Rare Combination of Tetralogy of Fallot and a Complete Atrioventricular Septal Defect: A Case Report
International Journal of Medicine and Health Development
children
complete atrioventricular septal defect
echocardiography
ejection systolic murmur
rare
tetralogy of fallot
title A Rare Combination of Tetralogy of Fallot and a Complete Atrioventricular Septal Defect: A Case Report
title_full A Rare Combination of Tetralogy of Fallot and a Complete Atrioventricular Septal Defect: A Case Report
title_fullStr A Rare Combination of Tetralogy of Fallot and a Complete Atrioventricular Septal Defect: A Case Report
title_full_unstemmed A Rare Combination of Tetralogy of Fallot and a Complete Atrioventricular Septal Defect: A Case Report
title_short A Rare Combination of Tetralogy of Fallot and a Complete Atrioventricular Septal Defect: A Case Report
title_sort rare combination of tetralogy of fallot and a complete atrioventricular septal defect a case report
topic children
complete atrioventricular septal defect
echocardiography
ejection systolic murmur
rare
tetralogy of fallot
url https://doi.org/10.4103/ijmh.ijmh_73_24
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