Clinical and molecular characteristics of a Brazilian family with spinocerebellar ataxia type 1 Características clínicas e moleculares de uma família Brasileira com ataxia espinocerebelar tipo 1

The spinocerebellar ataxias (SCAs) are a clinically and genetically heterogeneous group of late onset neurodegenerative disorders. To date, seven different genes causing autosomal dominant SCA have been mapped: SCA1, SCA2, Machado-Joseph disease (MJD)/SCA3, SCA4, SCA5, SCA7 and dentatorubropallidolu...

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Bibliographic Details
Main Authors: Iscia Lopes-Cendes, Carlos E. Steiner, Isabel Silveira, Walter Pinto-Junior, Jayme A. Maciel, Guy A. Rouleau
Format: Article
Language:English
Published: Thieme Revinter Publicações 1996-09-01
Series:Arquivos de Neuro-Psiquiatria
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Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1996000300009
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