Multiple Liver Nodules Mimicking Metastatic Disease as Initial Presentation of Multiple Myeloma

Multiple myeloma is a malignant clonal proliferation of plasma cells in the bone marrow preceded by monoclonal gammopathy of undetermined significance. Initial presentation of multiple myeloma as extramedullary spread in soft tissues particularly in the liver is uncommon. We report a case of a 74-ye...

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Main Authors: Andrew C. Tiu, Rashmika Potdar, Vivian Arguello-Gerra, Mark Morginstin
Format: Article
Language:English
Published: Wiley 2018-01-01
Series:Case Reports in Hematology
Online Access:http://dx.doi.org/10.1155/2018/7954816
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author Andrew C. Tiu
Rashmika Potdar
Vivian Arguello-Gerra
Mark Morginstin
author_facet Andrew C. Tiu
Rashmika Potdar
Vivian Arguello-Gerra
Mark Morginstin
author_sort Andrew C. Tiu
collection DOAJ
description Multiple myeloma is a malignant clonal proliferation of plasma cells in the bone marrow preceded by monoclonal gammopathy of undetermined significance. Initial presentation of multiple myeloma as extramedullary spread in soft tissues particularly in the liver is uncommon. We report a case of a 74-year-old African American female who presented with epigastric pain, hematemesis, elevated alkaline phosphatase, and gamma-glutamyl transferase. Initial impression was peptic ulcer disease; however, ultrasound and CT scan of the abdomen showed multiple liver nodules and perihepatic lymphadenopathy suggestive of metastatic disease. Biopsy of the liver nodules showed CD138 and kappa light chain-restricted positive cells consistent with extramedullary spread of multiple myeloma to the liver. The patient achieved partial response after 6 months of treatment with Velcade, cyclophosphamide, and dexamethasone (VCD). Due to severe neutropenia from cyclophosphamide, regimen was switched to Velcade, Revlimid, and dexamethasone (VRD) which resulted to very good partial response in 1 year which eventually persisted after 4 years. No controlled prospective studies have defined the standard treatment for multiple myeloma with extramedullary spread particularly to the liver. Treatment of multiple myeloma with extramedullary disease follows guidelines for multiple myeloma.
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spelling doaj-art-58ff87bdcc1546e08a1e4821bcb8fecb2025-08-20T03:34:58ZengWileyCase Reports in Hematology2090-65602090-65792018-01-01201810.1155/2018/79548167954816Multiple Liver Nodules Mimicking Metastatic Disease as Initial Presentation of Multiple MyelomaAndrew C. Tiu0Rashmika Potdar1Vivian Arguello-Gerra2Mark Morginstin3Department of Medicine, Einstein Medical Center, Philadelphia, PA, USADivision of Hematology and Medical Oncology, Einstein Medical Center, Philadelphia, PA, USADepartment of Pathology and Laboratory Medicine, Einstein Medical Center, Philadelphia, PA, USADivision of Hematology and Medical Oncology, Einstein Medical Center, Philadelphia, PA, USAMultiple myeloma is a malignant clonal proliferation of plasma cells in the bone marrow preceded by monoclonal gammopathy of undetermined significance. Initial presentation of multiple myeloma as extramedullary spread in soft tissues particularly in the liver is uncommon. We report a case of a 74-year-old African American female who presented with epigastric pain, hematemesis, elevated alkaline phosphatase, and gamma-glutamyl transferase. Initial impression was peptic ulcer disease; however, ultrasound and CT scan of the abdomen showed multiple liver nodules and perihepatic lymphadenopathy suggestive of metastatic disease. Biopsy of the liver nodules showed CD138 and kappa light chain-restricted positive cells consistent with extramedullary spread of multiple myeloma to the liver. The patient achieved partial response after 6 months of treatment with Velcade, cyclophosphamide, and dexamethasone (VCD). Due to severe neutropenia from cyclophosphamide, regimen was switched to Velcade, Revlimid, and dexamethasone (VRD) which resulted to very good partial response in 1 year which eventually persisted after 4 years. No controlled prospective studies have defined the standard treatment for multiple myeloma with extramedullary spread particularly to the liver. Treatment of multiple myeloma with extramedullary disease follows guidelines for multiple myeloma.http://dx.doi.org/10.1155/2018/7954816
spellingShingle Andrew C. Tiu
Rashmika Potdar
Vivian Arguello-Gerra
Mark Morginstin
Multiple Liver Nodules Mimicking Metastatic Disease as Initial Presentation of Multiple Myeloma
Case Reports in Hematology
title Multiple Liver Nodules Mimicking Metastatic Disease as Initial Presentation of Multiple Myeloma
title_full Multiple Liver Nodules Mimicking Metastatic Disease as Initial Presentation of Multiple Myeloma
title_fullStr Multiple Liver Nodules Mimicking Metastatic Disease as Initial Presentation of Multiple Myeloma
title_full_unstemmed Multiple Liver Nodules Mimicking Metastatic Disease as Initial Presentation of Multiple Myeloma
title_short Multiple Liver Nodules Mimicking Metastatic Disease as Initial Presentation of Multiple Myeloma
title_sort multiple liver nodules mimicking metastatic disease as initial presentation of multiple myeloma
url http://dx.doi.org/10.1155/2018/7954816
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