Intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour - An important but almost forgotten differential diagnosis
Intrapancreatic accessory spleen (IPAS) is a rare condition resulting from the failure of embryological splenic buds to fuse. Found in approximately 1.1% to 3.4% of the population, IPAS can present significant diagnostic challenges, often mimicking pancreatic tumours such as pancreatic neuroendocrin...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2025-07-01
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| Series: | Journal of Minimal Access Surgery |
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| Online Access: | https://journals.lww.com/10.4103/jmas.jmas_245_24 |
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| author | Kaique Flavio Xavier Cardoso Filardi José Donizeti de Meira Júnior Thiago Nogueira Costa André Montagnini Ismael Dominguez-Rosado Carlos Chan José Jukemura Paulo Herman |
| author_facet | Kaique Flavio Xavier Cardoso Filardi José Donizeti de Meira Júnior Thiago Nogueira Costa André Montagnini Ismael Dominguez-Rosado Carlos Chan José Jukemura Paulo Herman |
| author_sort | Kaique Flavio Xavier Cardoso Filardi |
| collection | DOAJ |
| description | Intrapancreatic accessory spleen (IPAS) is a rare condition resulting from the failure of embryological splenic buds to fuse. Found in approximately 1.1% to 3.4% of the population, IPAS can present significant diagnostic challenges, often mimicking pancreatic tumours such as pancreatic neuroendocrine tumours. We report two cases of IPAS, each illustrating different diagnostic approaches and outcomes. These cases highlight the importance of considering IPAS in differential diagnoses for hypervascular pancreatic tail lesions. Advanced imaging techniques such as magnetic resonance imaging, computerised tomography, technetium-99m scintigraphy and endoscopic ultrasound-guided fine-needle aspiration are critical in distinguishing IPAS from malignant conditions, potentially preventing unwarranted surgical interventions. Comprehensive diagnostic protocols combining multiple modalities are recommended to enhance diagnostic accuracy and optimise patient outcomes. |
| format | Article |
| id | doaj-art-57295e8a6a3c44c0a3f5b43a4ffd3a84 |
| institution | DOAJ |
| issn | 0972-9941 1998-3921 |
| language | English |
| publishDate | 2025-07-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Minimal Access Surgery |
| spelling | doaj-art-57295e8a6a3c44c0a3f5b43a4ffd3a842025-08-20T03:03:01ZengWolters Kluwer Medknow PublicationsJournal of Minimal Access Surgery0972-99411998-39212025-07-0121332132510.4103/jmas.jmas_245_24Intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour - An important but almost forgotten differential diagnosisKaique Flavio Xavier Cardoso FilardiJosé Donizeti de Meira JúniorThiago Nogueira CostaAndré MontagniniIsmael Dominguez-RosadoCarlos ChanJosé JukemuraPaulo HermanIntrapancreatic accessory spleen (IPAS) is a rare condition resulting from the failure of embryological splenic buds to fuse. Found in approximately 1.1% to 3.4% of the population, IPAS can present significant diagnostic challenges, often mimicking pancreatic tumours such as pancreatic neuroendocrine tumours. We report two cases of IPAS, each illustrating different diagnostic approaches and outcomes. These cases highlight the importance of considering IPAS in differential diagnoses for hypervascular pancreatic tail lesions. Advanced imaging techniques such as magnetic resonance imaging, computerised tomography, technetium-99m scintigraphy and endoscopic ultrasound-guided fine-needle aspiration are critical in distinguishing IPAS from malignant conditions, potentially preventing unwarranted surgical interventions. Comprehensive diagnostic protocols combining multiple modalities are recommended to enhance diagnostic accuracy and optimise patient outcomes.https://journals.lww.com/10.4103/jmas.jmas_245_24accessory spleendistal pancreatectomypancreatic neuroendocrine tumour |
| spellingShingle | Kaique Flavio Xavier Cardoso Filardi José Donizeti de Meira Júnior Thiago Nogueira Costa André Montagnini Ismael Dominguez-Rosado Carlos Chan José Jukemura Paulo Herman Intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour - An important but almost forgotten differential diagnosis Journal of Minimal Access Surgery accessory spleen distal pancreatectomy pancreatic neuroendocrine tumour |
| title | Intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour - An important but almost forgotten differential diagnosis |
| title_full | Intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour - An important but almost forgotten differential diagnosis |
| title_fullStr | Intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour - An important but almost forgotten differential diagnosis |
| title_full_unstemmed | Intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour - An important but almost forgotten differential diagnosis |
| title_short | Intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour - An important but almost forgotten differential diagnosis |
| title_sort | intrapancreatic accessory spleen mimicking a pancreatic neuroendocrine tumour an important but almost forgotten differential diagnosis |
| topic | accessory spleen distal pancreatectomy pancreatic neuroendocrine tumour |
| url | https://journals.lww.com/10.4103/jmas.jmas_245_24 |
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