Heart failure induced by a tumor in a young adult woman: A case report of dilated cardiomyopathy triggered by paraganglioma
Paragangliomas are rare neuroendocrine tumors that can secrete catecholamines, resulting in cardiovascular consequences such as catecholamine-induced cardiomyopathy and heart failure.The pathogenesis involves excessive catecholamine exposure, which causes myocardial damage, decreased cardiac functio...
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| Format: | Article |
| Language: | English |
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Elsevier
2025-07-01
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| Series: | Radiology Case Reports |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043325002341 |
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| author | Hamza El Abidi Ahmed Ibrahimi Mohamed Ali Mikou Imane Iraqui Imad Boualaoui Zined Labbi Sabrine Derqaoui Zakiya Bernoussi Hashem El Sayegh Yassine Nouini |
| author_facet | Hamza El Abidi Ahmed Ibrahimi Mohamed Ali Mikou Imane Iraqui Imad Boualaoui Zined Labbi Sabrine Derqaoui Zakiya Bernoussi Hashem El Sayegh Yassine Nouini |
| author_sort | Hamza El Abidi |
| collection | DOAJ |
| description | Paragangliomas are rare neuroendocrine tumors that can secrete catecholamines, resulting in cardiovascular consequences such as catecholamine-induced cardiomyopathy and heart failure.The pathogenesis involves excessive catecholamine exposure, which causes myocardial damage, decreased cardiac function, and systemic consequences. We discuss the case of a 26-year-old adult woman who presented with dyspnea, orthopnea, and lower limb edema and was finally diagnosed with dilated cardiomyopathy. Echocardiography revealed an LVEF of 35%. Further investigation, including imaging and biochemical testing, revealed an abdominal paraganglioma compressing the renal arteries and markedly high plasma and urinary normetanephrine levels.A multidisciplinary team of cardiologists, endocrinologists, surgeons, and anesthesiologists worked together to enhance preoperative, intraoperative, and postoperative treatment.Preoperative alpha-blockade using phenoxybenzamine, followed by conservative beta-blockade, ensured hemodynamic stability. To avoid excessive catecholamine release, the tumor was carefully handled intraoperatively during surgical excision. The patient's clinical condition improved significantly after surgery, with catecholamine levels and heart function returning to normal. |
| format | Article |
| id | doaj-art-565c2ee310014f0ca999e91098a22fb2 |
| institution | DOAJ |
| issn | 1930-0433 |
| language | English |
| publishDate | 2025-07-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj-art-565c2ee310014f0ca999e91098a22fb22025-08-20T03:09:57ZengElsevierRadiology Case Reports1930-04332025-07-012073309331310.1016/j.radcr.2025.03.024Heart failure induced by a tumor in a young adult woman: A case report of dilated cardiomyopathy triggered by paragangliomaHamza El Abidi0Ahmed Ibrahimi1Mohamed Ali Mikou2Imane Iraqui3Imad Boualaoui4Zined Labbi5Sabrine Derqaoui6Zakiya Bernoussi7Hashem El Sayegh8Yassine Nouini9Urology A Departement, University Hospital Ibn Sina, Rabat, Morocco; Corresponding author.Urology A Departement, University Hospital Ibn Sina, Rabat, MoroccoUrology A Departement, University Hospital Ibn Sina, Rabat, MoroccoPathology Department, University Hospital Ibn Sina, Rabat, MoroccoUrology A Departement, University Hospital Ibn Sina, Rabat, MoroccoRadiology Departement, University Hospital Ibn Sina, Rabat, MoroccoRadiology Departement, University Hospital Ibn Sina, Rabat, MoroccoRadiology Departement, University Hospital Ibn Sina, Rabat, MoroccoUrology A Departement, University Hospital Ibn Sina, Rabat, MoroccoUrology A Departement, University Hospital Ibn Sina, Rabat, MoroccoParagangliomas are rare neuroendocrine tumors that can secrete catecholamines, resulting in cardiovascular consequences such as catecholamine-induced cardiomyopathy and heart failure.The pathogenesis involves excessive catecholamine exposure, which causes myocardial damage, decreased cardiac function, and systemic consequences. We discuss the case of a 26-year-old adult woman who presented with dyspnea, orthopnea, and lower limb edema and was finally diagnosed with dilated cardiomyopathy. Echocardiography revealed an LVEF of 35%. Further investigation, including imaging and biochemical testing, revealed an abdominal paraganglioma compressing the renal arteries and markedly high plasma and urinary normetanephrine levels.A multidisciplinary team of cardiologists, endocrinologists, surgeons, and anesthesiologists worked together to enhance preoperative, intraoperative, and postoperative treatment.Preoperative alpha-blockade using phenoxybenzamine, followed by conservative beta-blockade, ensured hemodynamic stability. To avoid excessive catecholamine release, the tumor was carefully handled intraoperatively during surgical excision. The patient's clinical condition improved significantly after surgery, with catecholamine levels and heart function returning to normal.http://www.sciencedirect.com/science/article/pii/S1930043325002341ParagangliomaDilated cardiomyopathyHeart failureCatecholamine-induced CardiomyopathyTumor resection |
| spellingShingle | Hamza El Abidi Ahmed Ibrahimi Mohamed Ali Mikou Imane Iraqui Imad Boualaoui Zined Labbi Sabrine Derqaoui Zakiya Bernoussi Hashem El Sayegh Yassine Nouini Heart failure induced by a tumor in a young adult woman: A case report of dilated cardiomyopathy triggered by paraganglioma Radiology Case Reports Paraganglioma Dilated cardiomyopathy Heart failure Catecholamine-induced Cardiomyopathy Tumor resection |
| title | Heart failure induced by a tumor in a young adult woman: A case report of dilated cardiomyopathy triggered by paraganglioma |
| title_full | Heart failure induced by a tumor in a young adult woman: A case report of dilated cardiomyopathy triggered by paraganglioma |
| title_fullStr | Heart failure induced by a tumor in a young adult woman: A case report of dilated cardiomyopathy triggered by paraganglioma |
| title_full_unstemmed | Heart failure induced by a tumor in a young adult woman: A case report of dilated cardiomyopathy triggered by paraganglioma |
| title_short | Heart failure induced by a tumor in a young adult woman: A case report of dilated cardiomyopathy triggered by paraganglioma |
| title_sort | heart failure induced by a tumor in a young adult woman a case report of dilated cardiomyopathy triggered by paraganglioma |
| topic | Paraganglioma Dilated cardiomyopathy Heart failure Catecholamine-induced Cardiomyopathy Tumor resection |
| url | http://www.sciencedirect.com/science/article/pii/S1930043325002341 |
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