Ilizarov-assisted periosteal distraction for refractory arteriovenous malformation ulcers: first clinical report in Asia

Abstract Refractory ulcers caused by high-flow arteriovenous malformations (AVMs) pose significant therapeutic challenges due to persistent tissue ischemia and shear stress-induced graft failure. Traditional embolization or flap reconstruction strategies often yield suboptimal outcomes, particularly...

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Main Authors: Xiangyi Wu, Ren Cai, Mao Ye, Xitao Yang, Dachuan Sun, Yifeng Han, Xindong Fan, Jiaxue Zhu
Format: Article
Language:English
Published: BMC 2025-06-01
Series:Hereditas
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Online Access:https://doi.org/10.1186/s41065-025-00479-4
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author Xiangyi Wu
Ren Cai
Mao Ye
Xitao Yang
Dachuan Sun
Yifeng Han
Xindong Fan
Jiaxue Zhu
author_facet Xiangyi Wu
Ren Cai
Mao Ye
Xitao Yang
Dachuan Sun
Yifeng Han
Xindong Fan
Jiaxue Zhu
author_sort Xiangyi Wu
collection DOAJ
description Abstract Refractory ulcers caused by high-flow arteriovenous malformations (AVMs) pose significant therapeutic challenges due to persistent tissue ischemia and shear stress-induced graft failure. Traditional embolization or flap reconstruction strategies often yield suboptimal outcomes, particularly in weight-bearing regions. We present a 28-year-old female with a non-healing dorsal foot AVM ulcer despite multiple embolizations and radical toe amputations. Genetic testing revealed a KRAS mutation, confirming a somatic etiology of AVM. After a debridement and local flap repair, we employed Ilizarov-assisted periosteal distraction to improve local perfusion. 75% of the wound epithelialized and the infection resolved within 4 weeks postoperatively, with granulation tissue covering the remainder. This case highlights the mechanobiological advantages of Ilizarov-based neovascular stimulation in AVM-related ischemic ulcers.
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institution Kabale University
issn 1601-5223
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publishDate 2025-06-01
publisher BMC
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series Hereditas
spelling doaj-art-52dc961d4e4e413fbb00c930616e87502025-08-20T03:47:14ZengBMCHereditas1601-52232025-06-0116211410.1186/s41065-025-00479-4Ilizarov-assisted periosteal distraction for refractory arteriovenous malformation ulcers: first clinical report in AsiaXiangyi Wu0Ren Cai1Mao Ye2Xitao Yang3Dachuan Sun4Yifeng Han5Xindong Fan6Jiaxue Zhu7Department of Interventional Therapy, Multidisciplinary Team of Vascular Anomalies, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of MedicineDepartment of Interventional Therapy, Multidisciplinary Team of Vascular Anomalies, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of MedicineDepartment of Orthopedics, Fengcheng Hospital Affiliated to Shanghai Ninth People’s Hospital, Shanghai Jiao Tong UniversityDepartment of Interventional Therapy, Multidisciplinary Team of Vascular Anomalies, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of MedicineDepartment of Orthopedics, Fengcheng Hospital Affiliated to Shanghai Ninth People’s Hospital, Shanghai Jiao Tong UniversityDepartment of Interventional Therapy, Multidisciplinary Team of Vascular Anomalies, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of MedicineDepartment of Interventional Therapy, Multidisciplinary Team of Vascular Anomalies, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of MedicineDepartment of Interventional Therapy, Multidisciplinary Team of Vascular Anomalies, Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of MedicineAbstract Refractory ulcers caused by high-flow arteriovenous malformations (AVMs) pose significant therapeutic challenges due to persistent tissue ischemia and shear stress-induced graft failure. Traditional embolization or flap reconstruction strategies often yield suboptimal outcomes, particularly in weight-bearing regions. We present a 28-year-old female with a non-healing dorsal foot AVM ulcer despite multiple embolizations and radical toe amputations. Genetic testing revealed a KRAS mutation, confirming a somatic etiology of AVM. After a debridement and local flap repair, we employed Ilizarov-assisted periosteal distraction to improve local perfusion. 75% of the wound epithelialized and the infection resolved within 4 weeks postoperatively, with granulation tissue covering the remainder. This case highlights the mechanobiological advantages of Ilizarov-based neovascular stimulation in AVM-related ischemic ulcers.https://doi.org/10.1186/s41065-025-00479-4Extracranial arteriovenous malformationIlizarov techniquePeriosteal distractionUlcer healingChemotherapy
spellingShingle Xiangyi Wu
Ren Cai
Mao Ye
Xitao Yang
Dachuan Sun
Yifeng Han
Xindong Fan
Jiaxue Zhu
Ilizarov-assisted periosteal distraction for refractory arteriovenous malformation ulcers: first clinical report in Asia
Hereditas
Extracranial arteriovenous malformation
Ilizarov technique
Periosteal distraction
Ulcer healing
Chemotherapy
title Ilizarov-assisted periosteal distraction for refractory arteriovenous malformation ulcers: first clinical report in Asia
title_full Ilizarov-assisted periosteal distraction for refractory arteriovenous malformation ulcers: first clinical report in Asia
title_fullStr Ilizarov-assisted periosteal distraction for refractory arteriovenous malformation ulcers: first clinical report in Asia
title_full_unstemmed Ilizarov-assisted periosteal distraction for refractory arteriovenous malformation ulcers: first clinical report in Asia
title_short Ilizarov-assisted periosteal distraction for refractory arteriovenous malformation ulcers: first clinical report in Asia
title_sort ilizarov assisted periosteal distraction for refractory arteriovenous malformation ulcers first clinical report in asia
topic Extracranial arteriovenous malformation
Ilizarov technique
Periosteal distraction
Ulcer healing
Chemotherapy
url https://doi.org/10.1186/s41065-025-00479-4
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