Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)

Osler-Weber-Rendu syndrome also known as hereditary hemorrhagic telangiectasia (HHT) is a rare vascular dysplasia affecting multiple organ systems in the body. Hepatic manifestations of HHT include telangiectasias, large confluent masses, hepatic perfusion abnormalities, and various types of intrahe...

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Main Authors: Anjali Sah, Rajendra Kumar Behera, Anuradha Sharma, Shivanand Gamanagatti, Ayush Agarwal, Soumya Jagannath Mahapatra
Format: Article
Language:English
Published: Thieme Medical and Scientific Publishers Pvt. Ltd.
Series:Indian Journal of Radiology and Imaging
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Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0045-1805005
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author Anjali Sah
Rajendra Kumar Behera
Anuradha Sharma
Shivanand Gamanagatti
Ayush Agarwal
Soumya Jagannath Mahapatra
author_facet Anjali Sah
Rajendra Kumar Behera
Anuradha Sharma
Shivanand Gamanagatti
Ayush Agarwal
Soumya Jagannath Mahapatra
author_sort Anjali Sah
collection DOAJ
description Osler-Weber-Rendu syndrome also known as hereditary hemorrhagic telangiectasia (HHT) is a rare vascular dysplasia affecting multiple organ systems in the body. Hepatic manifestations of HHT include telangiectasias, large confluent masses, hepatic perfusion abnormalities, and various types of intrahepatic vascular shunts. Spontaneous hepatic pseudoaneurysm (PA) in HHT is a less well-known phenomenon, with fewer than 20 cases reported in the literature so far. Even rarer is the use of percutaneous glue (N-butyl cyanoacrylate) embolization to manage multiple hepatic PAs in HHT syndrome. The purpose of this case report is to describe the successful management of multiple hepatic PAs by percutaneous embolization in a 56-year-old male diagnosed with HHT.
format Article
id doaj-art-4feae3088ee143b9a12887e9cc15ad5f
institution Kabale University
issn 0971-3026
1998-3808
language English
publisher Thieme Medical and Scientific Publishers Pvt. Ltd.
record_format Article
series Indian Journal of Radiology and Imaging
spelling doaj-art-4feae3088ee143b9a12887e9cc15ad5f2025-08-20T03:42:06ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Radiology and Imaging0971-30261998-380810.1055/s-0045-1805005Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)Anjali Sah0Rajendra Kumar Behera1Anuradha Sharma2Shivanand Gamanagatti3https://orcid.org/0000-0002-2172-0109Ayush Agarwal4Soumya Jagannath Mahapatra5Department of Radio-diagnosis & Interventional Radiology, All India Institute of Medical Sciences, New Delhi, IndiaDepartment of Radio-diagnosis & Interventional Radiology, All India Institute of Medical Sciences, New Delhi, IndiaDepartment of Radio-diagnosis & Interventional Radiology, All India Institute of Medical Sciences, New Delhi, IndiaDepartment of Radio-diagnosis & Interventional Radiology, All India Institute of Medical Sciences, New Delhi, IndiaDepartment of Gastroenterology and Human Nutrition, All India Institute of Medical Sciences, New Delhi, IndiaDepartment of Gastroenterology and Human Nutrition, All India Institute of Medical Sciences, New Delhi, IndiaOsler-Weber-Rendu syndrome also known as hereditary hemorrhagic telangiectasia (HHT) is a rare vascular dysplasia affecting multiple organ systems in the body. Hepatic manifestations of HHT include telangiectasias, large confluent masses, hepatic perfusion abnormalities, and various types of intrahepatic vascular shunts. Spontaneous hepatic pseudoaneurysm (PA) in HHT is a less well-known phenomenon, with fewer than 20 cases reported in the literature so far. Even rarer is the use of percutaneous glue (N-butyl cyanoacrylate) embolization to manage multiple hepatic PAs in HHT syndrome. The purpose of this case report is to describe the successful management of multiple hepatic PAs by percutaneous embolization in a 56-year-old male diagnosed with HHT.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0045-1805005hereditary hemorrhagic telangiectasiapseudoaneurysmsglue embolization
spellingShingle Anjali Sah
Rajendra Kumar Behera
Anuradha Sharma
Shivanand Gamanagatti
Ayush Agarwal
Soumya Jagannath Mahapatra
Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)
Indian Journal of Radiology and Imaging
hereditary hemorrhagic telangiectasia
pseudoaneurysms
glue embolization
title Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)
title_full Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)
title_fullStr Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)
title_full_unstemmed Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)
title_short Overcoming Complexity: Percutaneous Embolization for Hepatic Artery Pseudoaneurysms in Hereditary Hemorrhagic Telangiectasia (HHT)
title_sort overcoming complexity percutaneous embolization for hepatic artery pseudoaneurysms in hereditary hemorrhagic telangiectasia hht
topic hereditary hemorrhagic telangiectasia
pseudoaneurysms
glue embolization
url http://www.thieme-connect.de/DOI/DOI?10.1055/s-0045-1805005
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