Dowling–Degos disease in a 23-year-old Jordanian male: a case report

Abstract Background Dowling–Degos disease is a rare genodermatosis disorder that presents as an autosomal dominant trait during late childhood or in adolescence and is also known as reticulate pigmented anomaly of flexures, Dowling–Degos–Kitamura, or dark dot disease. Dowling–Degos disease is charac...

Full description

Saved in:
Bibliographic Details
Main Authors: Hamdah Hanifa, Aya Mohannad Hamdan, Ansam Zakaria Baniamer, Jihan Mohammed Muhaidat, Sultan Hussein Al-Sahoud, Mohammad Raed AlGhzawi, Mohammad Tareq Alfaqeh
Format: Article
Language:English
Published: BMC 2025-07-01
Series:Journal of Medical Case Reports
Subjects:
Online Access:https://doi.org/10.1186/s13256-025-05398-6
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849763472026370048
author Hamdah Hanifa
Aya Mohannad Hamdan
Ansam Zakaria Baniamer
Jihan Mohammed Muhaidat
Sultan Hussein Al-Sahoud
Mohammad Raed AlGhzawi
Mohammad Tareq Alfaqeh
author_facet Hamdah Hanifa
Aya Mohannad Hamdan
Ansam Zakaria Baniamer
Jihan Mohammed Muhaidat
Sultan Hussein Al-Sahoud
Mohammad Raed AlGhzawi
Mohammad Tareq Alfaqeh
author_sort Hamdah Hanifa
collection DOAJ
description Abstract Background Dowling–Degos disease is a rare genodermatosis disorder that presents as an autosomal dominant trait during late childhood or in adolescence and is also known as reticulate pigmented anomaly of flexures, Dowling–Degos–Kitamura, or dark dot disease. Dowling–Degos disease is characterized by acquired reticular hyperpigmentation, and manifests as a clustered or reticulated pattern mainly at flexural sites, especially in the folds of the skin with comedone-like follicular papules and pitted perioral scars. It appears in both genders but is more likely in females. Case presentation A 23-year-old Jordanian male presented with progressive hyperpigmented macules and papules on his forehead, initially managed with Triderma cream without improvement. Histopathological examination via punch biopsies revealed features consistent with Dowling–Degos disease, excluding malignancy. Treatment was transitioned to sunblock, depigmenting agents (Isis Unit One 4 White), and moisturizers, resulting in significant fading of lesions after 8 months. Genetic counseling was provided owing to the hereditary nature of Dowling–Degos disease, and long-term management strategies were emphasized. Conclusion Dowling–Degos disease is a rare genodermatosis that can cause significant psychological distress and a decline in quality of life. Despite challenging treatment, a multidisciplinary approach is essential for improving patient outcomes and managing the elevated risk of skin cancers.
format Article
id doaj-art-4fe36c6d56aa4e1f97c47c1709ee0807
institution DOAJ
issn 1752-1947
language English
publishDate 2025-07-01
publisher BMC
record_format Article
series Journal of Medical Case Reports
spelling doaj-art-4fe36c6d56aa4e1f97c47c1709ee08072025-08-20T03:05:23ZengBMCJournal of Medical Case Reports1752-19472025-07-011911610.1186/s13256-025-05398-6Dowling–Degos disease in a 23-year-old Jordanian male: a case reportHamdah Hanifa0Aya Mohannad Hamdan1Ansam Zakaria Baniamer2Jihan Mohammed Muhaidat3Sultan Hussein Al-Sahoud4Mohammad Raed AlGhzawi5Mohammad Tareq Alfaqeh6Faculty of Medicine, University of KalamoonFaculty of Medicine, Independent ResearcherFaculty of Medicine, Yarmouk UniversityDepartment of Dermatology, Faculty of Medicine, Jordan University of Science and TechnologyFaculty of Medicine, Jordan University of Science and TechnologyFaculty of Medicine, Yarmouk UniversityFaculty of Medicine, Yarmouk UniversityAbstract Background Dowling–Degos disease is a rare genodermatosis disorder that presents as an autosomal dominant trait during late childhood or in adolescence and is also known as reticulate pigmented anomaly of flexures, Dowling–Degos–Kitamura, or dark dot disease. Dowling–Degos disease is characterized by acquired reticular hyperpigmentation, and manifests as a clustered or reticulated pattern mainly at flexural sites, especially in the folds of the skin with comedone-like follicular papules and pitted perioral scars. It appears in both genders but is more likely in females. Case presentation A 23-year-old Jordanian male presented with progressive hyperpigmented macules and papules on his forehead, initially managed with Triderma cream without improvement. Histopathological examination via punch biopsies revealed features consistent with Dowling–Degos disease, excluding malignancy. Treatment was transitioned to sunblock, depigmenting agents (Isis Unit One 4 White), and moisturizers, resulting in significant fading of lesions after 8 months. Genetic counseling was provided owing to the hereditary nature of Dowling–Degos disease, and long-term management strategies were emphasized. Conclusion Dowling–Degos disease is a rare genodermatosis that can cause significant psychological distress and a decline in quality of life. Despite challenging treatment, a multidisciplinary approach is essential for improving patient outcomes and managing the elevated risk of skin cancers.https://doi.org/10.1186/s13256-025-05398-6Dowling–Degos diseaseGenodermatosisSkin biopsySkin rashCase report
spellingShingle Hamdah Hanifa
Aya Mohannad Hamdan
Ansam Zakaria Baniamer
Jihan Mohammed Muhaidat
Sultan Hussein Al-Sahoud
Mohammad Raed AlGhzawi
Mohammad Tareq Alfaqeh
Dowling–Degos disease in a 23-year-old Jordanian male: a case report
Journal of Medical Case Reports
Dowling–Degos disease
Genodermatosis
Skin biopsy
Skin rash
Case report
title Dowling–Degos disease in a 23-year-old Jordanian male: a case report
title_full Dowling–Degos disease in a 23-year-old Jordanian male: a case report
title_fullStr Dowling–Degos disease in a 23-year-old Jordanian male: a case report
title_full_unstemmed Dowling–Degos disease in a 23-year-old Jordanian male: a case report
title_short Dowling–Degos disease in a 23-year-old Jordanian male: a case report
title_sort dowling degos disease in a 23 year old jordanian male a case report
topic Dowling–Degos disease
Genodermatosis
Skin biopsy
Skin rash
Case report
url https://doi.org/10.1186/s13256-025-05398-6
work_keys_str_mv AT hamdahhanifa dowlingdegosdiseaseina23yearoldjordanianmaleacasereport
AT ayamohannadhamdan dowlingdegosdiseaseina23yearoldjordanianmaleacasereport
AT ansamzakariabaniamer dowlingdegosdiseaseina23yearoldjordanianmaleacasereport
AT jihanmohammedmuhaidat dowlingdegosdiseaseina23yearoldjordanianmaleacasereport
AT sultanhusseinalsahoud dowlingdegosdiseaseina23yearoldjordanianmaleacasereport
AT mohammadraedalghzawi dowlingdegosdiseaseina23yearoldjordanianmaleacasereport
AT mohammadtareqalfaqeh dowlingdegosdiseaseina23yearoldjordanianmaleacasereport