Haemangioendothelioma of Different Sites: A Series of Four Cases

Haemangioendothelioma is a rare vascular tumour of endothelial origin. It is considered a tumour with intermediate malignant potential. It is locally aggressive and can occasionally metastasize. Four cases of epithelioid haemangioendothelioma have been reported in a tertiary medical centre in the De...

Full description

Saved in:
Bibliographic Details
Main Authors: Reshma Rachel Alex, Neetha Unnikrishnan, PV Priya, V Letha, S Sankar
Format: Article
Language:English
Published: JCDR Research and Publications Private Limited 2025-05-01
Series:Journal of Clinical and Diagnostic Research
Subjects:
Online Access:https://jcdr.net/articles/PDF/20982/76234_CE[Ra1]_F(IS)_QC(PS_SS)_PF1(RI_SL)_redo_PFA(IS)_PB(RI_IS)_PN(IS).pdf
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Haemangioendothelioma is a rare vascular tumour of endothelial origin. It is considered a tumour with intermediate malignant potential. It is locally aggressive and can occasionally metastasize. Four cases of epithelioid haemangioendothelioma have been reported in a tertiary medical centre in the Department of Pathology, Government Medical College, Kottayam, Kerala, India, over a span of two years, specifically between August 2022 and August 2024. Two of the cases involved 10-year-old girls who presented with hoarseness of voice for six months and swelling in the thigh for three years, respectively. The third case was that of a 43-year-old female with a lesion in the liver. The fourth case involved a 48-year-old male who presented with swelling in the left arm. Microscopy of all cases revealed a neoplasm with numerous small-sized blood vessels lined by plump endothelial cells. Immunohistochemistry (IHC) was performed, leading to a diagnosis of haemangioendothelioma. The estimated prevalence of this tumour is less than one in a million, which makes the present study the first of its kind.
ISSN:2249-782X
0973-709X