Pancreatic Acinar Cell Carcinoma in the Setting of a BRCA1 Germline Mutation

Pancreatic acinar cell carcinoma (PACC) is a rare neoplasm of the exocrine pancreas. PACC’s molecular and genetic features are poorly elucidated compared with pancreatic ductal cell carcinoma. Here, we present the patient case of a woman in her late 60s, with a BRCA1 germline mutation and a medical...

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Main Authors: Leticia Campoverde, Monika Vyas, Andrea Bullock
Format: Article
Language:English
Published: American College of Physicians 2022-09-01
Series:Annals of Internal Medicine: Clinical Cases
Online Access:https://www.acpjournals.org/doi/10.7326/aimcc.2022.0596
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author Leticia Campoverde
Monika Vyas
Andrea Bullock
author_facet Leticia Campoverde
Monika Vyas
Andrea Bullock
author_sort Leticia Campoverde
collection DOAJ
description Pancreatic acinar cell carcinoma (PACC) is a rare neoplasm of the exocrine pancreas. PACC’s molecular and genetic features are poorly elucidated compared with pancreatic ductal cell carcinoma. Here, we present the patient case of a woman in her late 60s, with a BRCA1 germline mutation and a medical history of breast and lung adenocarcinomas diagnosed with PACC. A literature search identified only 2 reported cases of PACC associated with a BRCA1 germline mutation.
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issn 2767-7664
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publishDate 2022-09-01
publisher American College of Physicians
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series Annals of Internal Medicine: Clinical Cases
spelling doaj-art-4f523e3ff32e4bd799ec592f7aba0c362025-08-20T02:11:46ZengAmerican College of PhysiciansAnnals of Internal Medicine: Clinical Cases2767-76642022-09-011710.7326/aimcc.2022.0596Pancreatic Acinar Cell Carcinoma in the Setting of a BRCA1 Germline MutationLeticia Campoverde0Monika Vyas1Andrea Bullock21Internal Medicine Residency Training Program, Division of Internal Medicine, Jackson Memorial Hospital-University of Miami, Miami, Florida2Medical Oncology, Beth Israel Deaconess Medical Center and Harvard Medical School, Boston, Massachusetts3Department of Pathology, Beth Israel Deaconess Medical Center, Harvard Medical School, Boston, MassachusettsPancreatic acinar cell carcinoma (PACC) is a rare neoplasm of the exocrine pancreas. PACC’s molecular and genetic features are poorly elucidated compared with pancreatic ductal cell carcinoma. Here, we present the patient case of a woman in her late 60s, with a BRCA1 germline mutation and a medical history of breast and lung adenocarcinomas diagnosed with PACC. A literature search identified only 2 reported cases of PACC associated with a BRCA1 germline mutation.https://www.acpjournals.org/doi/10.7326/aimcc.2022.0596
spellingShingle Leticia Campoverde
Monika Vyas
Andrea Bullock
Pancreatic Acinar Cell Carcinoma in the Setting of a BRCA1 Germline Mutation
Annals of Internal Medicine: Clinical Cases
title Pancreatic Acinar Cell Carcinoma in the Setting of a BRCA1 Germline Mutation
title_full Pancreatic Acinar Cell Carcinoma in the Setting of a BRCA1 Germline Mutation
title_fullStr Pancreatic Acinar Cell Carcinoma in the Setting of a BRCA1 Germline Mutation
title_full_unstemmed Pancreatic Acinar Cell Carcinoma in the Setting of a BRCA1 Germline Mutation
title_short Pancreatic Acinar Cell Carcinoma in the Setting of a BRCA1 Germline Mutation
title_sort pancreatic acinar cell carcinoma in the setting of a brca1 germline mutation
url https://www.acpjournals.org/doi/10.7326/aimcc.2022.0596
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AT monikavyas pancreaticacinarcellcarcinomainthesettingofabrca1germlinemutation
AT andreabullock pancreaticacinarcellcarcinomainthesettingofabrca1germlinemutation