Blue Rubber Bleb Nevus Syndrome with Long-Term Follow-Up: A Case Report and Review of the Literature
Blue rubber bleb nevus syndrome (BRBNS) is a rare disease in which venous malformations (VMs) involve any body organ, most commonly the skin and the gastrointestinal (GI) tract. Treatment of BRBNS aims at preserving the GI tract as much as possible. Although there are several dozen case reports abou...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Gastrointestinal Medicine |
| Online Access: | http://dx.doi.org/10.1155/2018/8087659 |
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| author | Hideaki Nakajima Hiroshi Nouso Naoto Urushihara Koji Fukumoto Masaya Yamoto Hiromu Miyake Akinori Sekioka Akiyoshi Nomura Yutaka Yamada |
| author_facet | Hideaki Nakajima Hiroshi Nouso Naoto Urushihara Koji Fukumoto Masaya Yamoto Hiromu Miyake Akinori Sekioka Akiyoshi Nomura Yutaka Yamada |
| author_sort | Hideaki Nakajima |
| collection | DOAJ |
| description | Blue rubber bleb nevus syndrome (BRBNS) is a rare disease in which venous malformations (VMs) involve any body organ, most commonly the skin and the gastrointestinal (GI) tract. Treatment of BRBNS aims at preserving the GI tract as much as possible. Although there are several dozen case reports about BRBNS that describe short-term clinical courses, a few provide an account of long-term clinical course. Here, we report a case of BRBNS in a girl that required multiple abdominal surgeries due to the GI VMs and a recurrence at an interval of 14 years. The preferred approach for gastrointestinal VMs involves the complete resection of all lesions without residual VMs. It is important to bear in mind the possibility of delayed recurrence of GI VMs after surgical or endoscopic treatment. |
| format | Article |
| id | doaj-art-4f0c5177f9c3453a92a8158bef98cf22 |
| institution | Kabale University |
| issn | 2090-6528 2090-6536 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Gastrointestinal Medicine |
| spelling | doaj-art-4f0c5177f9c3453a92a8158bef98cf222025-02-03T06:11:47ZengWileyCase Reports in Gastrointestinal Medicine2090-65282090-65362018-01-01201810.1155/2018/80876598087659Blue Rubber Bleb Nevus Syndrome with Long-Term Follow-Up: A Case Report and Review of the LiteratureHideaki Nakajima0Hiroshi Nouso1Naoto Urushihara2Koji Fukumoto3Masaya Yamoto4Hiromu Miyake5Akinori Sekioka6Akiyoshi Nomura7Yutaka Yamada8Department of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanDepartment of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanDepartment of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanDepartment of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanDepartment of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanDepartment of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanDepartment of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanDepartment of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanDepartment of Pediatric Surgery, Shizuoka Children’s Hospital, 860 Urushiyama, Aoi-ku, Shizuoka 420-8660, Shizuoka, JapanBlue rubber bleb nevus syndrome (BRBNS) is a rare disease in which venous malformations (VMs) involve any body organ, most commonly the skin and the gastrointestinal (GI) tract. Treatment of BRBNS aims at preserving the GI tract as much as possible. Although there are several dozen case reports about BRBNS that describe short-term clinical courses, a few provide an account of long-term clinical course. Here, we report a case of BRBNS in a girl that required multiple abdominal surgeries due to the GI VMs and a recurrence at an interval of 14 years. The preferred approach for gastrointestinal VMs involves the complete resection of all lesions without residual VMs. It is important to bear in mind the possibility of delayed recurrence of GI VMs after surgical or endoscopic treatment.http://dx.doi.org/10.1155/2018/8087659 |
| spellingShingle | Hideaki Nakajima Hiroshi Nouso Naoto Urushihara Koji Fukumoto Masaya Yamoto Hiromu Miyake Akinori Sekioka Akiyoshi Nomura Yutaka Yamada Blue Rubber Bleb Nevus Syndrome with Long-Term Follow-Up: A Case Report and Review of the Literature Case Reports in Gastrointestinal Medicine |
| title | Blue Rubber Bleb Nevus Syndrome with Long-Term Follow-Up: A Case Report and Review of the Literature |
| title_full | Blue Rubber Bleb Nevus Syndrome with Long-Term Follow-Up: A Case Report and Review of the Literature |
| title_fullStr | Blue Rubber Bleb Nevus Syndrome with Long-Term Follow-Up: A Case Report and Review of the Literature |
| title_full_unstemmed | Blue Rubber Bleb Nevus Syndrome with Long-Term Follow-Up: A Case Report and Review of the Literature |
| title_short | Blue Rubber Bleb Nevus Syndrome with Long-Term Follow-Up: A Case Report and Review of the Literature |
| title_sort | blue rubber bleb nevus syndrome with long term follow up a case report and review of the literature |
| url | http://dx.doi.org/10.1155/2018/8087659 |
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