The Effect of Empowerment Program for Nurses Regarding Management of Children with Phenylketonuria

Context: Phenylketonuria (commonly known as PKU) is an inherited disorder that increases the levels of a substance called phenylalanine in the blood. If PKU did not diagnose early in life or the affected children with PKU do not be compliant with the treatment regimen (food), it leads to severe cog...

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Main Authors: Khadiga M. Said, Safaa F. Draz
Format: Article
Language:English
Published: Egyptian Electronic Publisher 2024-02-01
Series:Evidence-Based Nursing Research
Subjects:
Online Access:https://eepublisher.com/index.php/ebnr/article/view/107
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author Khadiga M. Said
Safaa F. Draz
author_facet Khadiga M. Said
Safaa F. Draz
author_sort Khadiga M. Said
collection DOAJ
description Context: Phenylketonuria (commonly known as PKU) is an inherited disorder that increases the levels of a substance called phenylalanine in the blood. If PKU did not diagnose early in life or the affected children with PKU do not be compliant with the treatment regimen (food), it leads to severe cognitive or behavioral problems, seizures, and autistic symptoms. Aim: The current study aimed to evaluate the effect of empowerment program on nurses' management of children with phenylketonuria. Methods: Quasi-experimental research (one group pre/post-test) design was used to conduct this study. The study was carried out in the hereditary unit, and hereditary outpatient clinics at Ain Shams Specialized Hospital for children affiliated to Ain shams University. A convenient sample of all available nurses working in the previously mentioned study settings (80 male and female bedside nurses) from the beginning of May 2018 to the end of October 2018. Two tools were utilized for data collection for the current study. They are the structured interview questionnaire to assess the nurses' knowledge regarding the management of children with phenylketonuria and the nurses’ performance observation checklists regarding nursing care provided for children with phenylketonuria Results: nurses' knowledge regarding phenylketonuria was unsatisfactory before the empowerment program, while there is a statistically significant improvement between pre and post empowerment program implementation. Nurses' practice regarding phenylketonuria was incompetent before the empowerment program compared to post empowerment program. There is a positive statistical relationship between nurses' knowledge and practice post-program implementation. Conclusion:  The study revealed that the empowerment program had a positive effect on the nurses' knowledge and practice towards the management of children with phenylketonuria. The current study recommended continuous education and training sessions about the management of children with phenylketonuria that should be provided to upgrade the knowledge and improve the practice of nurses caring for PKU children.  Availability and accessibility of printed guidelines, posters, and simple handouts regarding the management of children with phenylketonuria.
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spelling doaj-art-4e6a4174fa5241d8969de11e13476fb02025-08-20T03:52:19ZengEgyptian Electronic PublisherEvidence-Based Nursing Research2636-39922636-400X2024-02-011410.47104/ebnrojs3.v1i4.107The Effect of Empowerment Program for Nurses Regarding Management of Children with PhenylketonuriaKhadiga M. Said0Safaa F. Draz1Faculty of Nursing, Benha UniversityFaculty of Nursing, Benha University Context: Phenylketonuria (commonly known as PKU) is an inherited disorder that increases the levels of a substance called phenylalanine in the blood. If PKU did not diagnose early in life or the affected children with PKU do not be compliant with the treatment regimen (food), it leads to severe cognitive or behavioral problems, seizures, and autistic symptoms. Aim: The current study aimed to evaluate the effect of empowerment program on nurses' management of children with phenylketonuria. Methods: Quasi-experimental research (one group pre/post-test) design was used to conduct this study. The study was carried out in the hereditary unit, and hereditary outpatient clinics at Ain Shams Specialized Hospital for children affiliated to Ain shams University. A convenient sample of all available nurses working in the previously mentioned study settings (80 male and female bedside nurses) from the beginning of May 2018 to the end of October 2018. Two tools were utilized for data collection for the current study. They are the structured interview questionnaire to assess the nurses' knowledge regarding the management of children with phenylketonuria and the nurses’ performance observation checklists regarding nursing care provided for children with phenylketonuria Results: nurses' knowledge regarding phenylketonuria was unsatisfactory before the empowerment program, while there is a statistically significant improvement between pre and post empowerment program implementation. Nurses' practice regarding phenylketonuria was incompetent before the empowerment program compared to post empowerment program. There is a positive statistical relationship between nurses' knowledge and practice post-program implementation. Conclusion:  The study revealed that the empowerment program had a positive effect on the nurses' knowledge and practice towards the management of children with phenylketonuria. The current study recommended continuous education and training sessions about the management of children with phenylketonuria that should be provided to upgrade the knowledge and improve the practice of nurses caring for PKU children.  Availability and accessibility of printed guidelines, posters, and simple handouts regarding the management of children with phenylketonuria. https://eepublisher.com/index.php/ebnr/article/view/107Nurses' management, empowerment program, children and phenylketonuria
spellingShingle Khadiga M. Said
Safaa F. Draz
The Effect of Empowerment Program for Nurses Regarding Management of Children with Phenylketonuria
Evidence-Based Nursing Research
Nurses' management, empowerment program, children and phenylketonuria
title The Effect of Empowerment Program for Nurses Regarding Management of Children with Phenylketonuria
title_full The Effect of Empowerment Program for Nurses Regarding Management of Children with Phenylketonuria
title_fullStr The Effect of Empowerment Program for Nurses Regarding Management of Children with Phenylketonuria
title_full_unstemmed The Effect of Empowerment Program for Nurses Regarding Management of Children with Phenylketonuria
title_short The Effect of Empowerment Program for Nurses Regarding Management of Children with Phenylketonuria
title_sort effect of empowerment program for nurses regarding management of children with phenylketonuria
topic Nurses' management, empowerment program, children and phenylketonuria
url https://eepublisher.com/index.php/ebnr/article/view/107
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