A case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilization
Background. Aplasia cutis congenita (ACC) is a rare congenital localized skin defect that is mostly diagnosed in the newborn or infant period. ACC type 5 often involves the trunk or extremities accompanied by fetus papyraceous (FP) or placental infarcts. The etiology and pathogenesis of this...
Saved in:
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Hacettepe University Institute of Child Health
2022-02-01
|
| Series: | The Turkish Journal of Pediatrics |
| Subjects: | |
| Online Access: | https://turkjpediatr.org/article/view/137 |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1850024275769032704 |
|---|---|
| author | Sae Yun Kim Eun Sun Kim Joonhong Min Kyungyul Lee |
| author_facet | Sae Yun Kim Eun Sun Kim Joonhong Min Kyungyul Lee |
| author_sort | Sae Yun Kim |
| collection | DOAJ |
| description |
Background. Aplasia cutis congenita (ACC) is a rare congenital localized skin defect that is mostly diagnosed in the newborn or infant period. ACC type 5 often involves the trunk or extremities accompanied by fetus papyraceous (FP) or placental infarcts. The etiology and pathogenesis of this rare type of ACC are not well known. In this case, we report an ACC type 5 with a definite etiology.
Case. We report a preterm infant with ACC type 5, with diffuse bilateral leg lesions found at birth. He was the first baby of dichorionic twin after reduction from a dichorionic triplet pregnancy conceived through in vitro fertilization. A fetus papyraceous was found in juxtaposition with the affected baby`s placenta. After 37 days of hospitalization, his leg lesions were successfully epithelized with supportive care. He is regularly visiting the Dermatology clinic for scar care and shows normal development without motor limitation.
Conclusions. Herein, we present a preterm infant with ACC type 5 and the placental pathology with fetus papyraceous of the artificially reduced monochorionic co-twin of the affected infant. We suggest a precautious decision in multifetal pregnancy reduction (MFPR) in dichorionic triplets, presenting ACC type 5 as an adverse outcome of MFPR.
|
| format | Article |
| id | doaj-art-4df2fb99e70b422e89ef64595d6e83c2 |
| institution | DOAJ |
| issn | 0041-4301 2791-6421 |
| language | English |
| publishDate | 2022-02-01 |
| publisher | Hacettepe University Institute of Child Health |
| record_format | Article |
| series | The Turkish Journal of Pediatrics |
| spelling | doaj-art-4df2fb99e70b422e89ef64595d6e83c22025-08-20T03:01:10ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64212022-02-0164110.24953/turkjped.2020.1787A case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilizationSae Yun Kim0Eun Sun Kim1Joonhong Min2Kyungyul Lee3Department of Pediatrics, Yeouido St. Mary's Hospital, The Catholic University of Korea, Seoul, Korea.Departments of Pediatrics, Kangwon National University School of Medicine, Chuncheon, Gangwon-do, Korea.Departments of Dermatology, Kangwon National University School of Medicine, Chuncheon, Gangwon-do, Korea.Departments of Pathology, Kangwon National University School of Medicine, Chuncheon, Gangwon-do, Korea. Background. Aplasia cutis congenita (ACC) is a rare congenital localized skin defect that is mostly diagnosed in the newborn or infant period. ACC type 5 often involves the trunk or extremities accompanied by fetus papyraceous (FP) or placental infarcts. The etiology and pathogenesis of this rare type of ACC are not well known. In this case, we report an ACC type 5 with a definite etiology. Case. We report a preterm infant with ACC type 5, with diffuse bilateral leg lesions found at birth. He was the first baby of dichorionic twin after reduction from a dichorionic triplet pregnancy conceived through in vitro fertilization. A fetus papyraceous was found in juxtaposition with the affected baby`s placenta. After 37 days of hospitalization, his leg lesions were successfully epithelized with supportive care. He is regularly visiting the Dermatology clinic for scar care and shows normal development without motor limitation. Conclusions. Herein, we present a preterm infant with ACC type 5 and the placental pathology with fetus papyraceous of the artificially reduced monochorionic co-twin of the affected infant. We suggest a precautious decision in multifetal pregnancy reduction (MFPR) in dichorionic triplets, presenting ACC type 5 as an adverse outcome of MFPR. https://turkjpediatr.org/article/view/137aplasia cutis congenitafetus papyraceousin vitro fertilizationmultifetal pregnancy reduction |
| spellingShingle | Sae Yun Kim Eun Sun Kim Joonhong Min Kyungyul Lee A case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilization The Turkish Journal of Pediatrics aplasia cutis congenita fetus papyraceous in vitro fertilization multifetal pregnancy reduction |
| title | A case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilization |
| title_full | A case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilization |
| title_fullStr | A case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilization |
| title_full_unstemmed | A case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilization |
| title_short | A case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilization |
| title_sort | case of aplasia cutis congenita following fetal reduction of triplet pregnancy conceived through in vitro fertilization |
| topic | aplasia cutis congenita fetus papyraceous in vitro fertilization multifetal pregnancy reduction |
| url | https://turkjpediatr.org/article/view/137 |
| work_keys_str_mv | AT saeyunkim acaseofaplasiacutiscongenitafollowingfetalreductionoftripletpregnancyconceivedthroughinvitrofertilization AT eunsunkim acaseofaplasiacutiscongenitafollowingfetalreductionoftripletpregnancyconceivedthroughinvitrofertilization AT joonhongmin acaseofaplasiacutiscongenitafollowingfetalreductionoftripletpregnancyconceivedthroughinvitrofertilization AT kyungyullee acaseofaplasiacutiscongenitafollowingfetalreductionoftripletpregnancyconceivedthroughinvitrofertilization AT saeyunkim caseofaplasiacutiscongenitafollowingfetalreductionoftripletpregnancyconceivedthroughinvitrofertilization AT eunsunkim caseofaplasiacutiscongenitafollowingfetalreductionoftripletpregnancyconceivedthroughinvitrofertilization AT joonhongmin caseofaplasiacutiscongenitafollowingfetalreductionoftripletpregnancyconceivedthroughinvitrofertilization AT kyungyullee caseofaplasiacutiscongenitafollowingfetalreductionoftripletpregnancyconceivedthroughinvitrofertilization |