Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease?
Systemic sclerosis is a complex and heterogeneous autoimmune condition in which skin and internal organ involvement progresses through interrelated processes of vasculopathy, immune activation, and fibrosis. Although considered an uncommon disease, its impact is disproportionate due to delayed diag...
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| Format: | Article |
| Language: | English |
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Nicolaus Copernicus University in Toruń
2025-06-01
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| Series: | Quality in Sport |
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| Online Access: | https://apcz.umk.pl/QS/article/view/60484 |
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| author | Olga Kądziołka Karolina Skonieczna Magdalena Badziąg Paulina Szulc Laura Kurczoba Martyna Kłossowska Olimpia Wiciun Kacper Ordon |
| author_facet | Olga Kądziołka Karolina Skonieczna Magdalena Badziąg Paulina Szulc Laura Kurczoba Martyna Kłossowska Olimpia Wiciun Kacper Ordon |
| author_sort | Olga Kądziołka |
| collection | DOAJ |
| description |
Systemic sclerosis is a complex and heterogeneous autoimmune condition in which skin and internal organ involvement progresses through interrelated processes of vasculopathy, immune activation, and fibrosis. Although considered an uncommon disease, its impact is disproportionate due to delayed diagnosis and potential for multiorgan complications. This review aims to synthesize current knowledge on the underlying mechanisms, clinical spectrum, and management strategies of systemic sclerosis, with particular attention to validated classification criteria and therapeutic recommendations. The paper emphasizes the role of early clinical suspicion, specific serologic and capillaroscopic findings, and the significance of evolving immunomodulatory and antifibrotic therapies. An individualized and multidisciplinary approach remains essential in improving patient outcomes and quality of life.
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| format | Article |
| id | doaj-art-4dd251ec852a42ceb2e61cf72b8a907e |
| institution | OA Journals |
| issn | 2450-3118 |
| language | English |
| publishDate | 2025-06-01 |
| publisher | Nicolaus Copernicus University in Toruń |
| record_format | Article |
| series | Quality in Sport |
| spelling | doaj-art-4dd251ec852a42ceb2e61cf72b8a907e2025-08-20T02:33:15ZengNicolaus Copernicus University in ToruńQuality in Sport2450-31182025-06-014210.12775/QS.2025.42.60484Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease?Olga Kądziołkahttps://orcid.org/0009-0006-1052-4504Karolina Skonieczna0https://orcid.org/0009-0009-0153-7444Magdalena Badziąghttps://orcid.org/0009-0008-8598-1034Paulina Szulchttps://orcid.org/0009-0007-7614-9214Laura Kurczobahttps://orcid.org/0009-0004-1330-991XMartyna Kłossowskahttps://orcid.org/0009-0002-7444-1637Olimpia Wiciunhttps://orcid.org/0009-0005-0318-5527Kacper Ordonhttps://orcid.org/0009-0000-1764-3422Uniwersytet Mikołaja Kopernika w Toruniu Systemic sclerosis is a complex and heterogeneous autoimmune condition in which skin and internal organ involvement progresses through interrelated processes of vasculopathy, immune activation, and fibrosis. Although considered an uncommon disease, its impact is disproportionate due to delayed diagnosis and potential for multiorgan complications. This review aims to synthesize current knowledge on the underlying mechanisms, clinical spectrum, and management strategies of systemic sclerosis, with particular attention to validated classification criteria and therapeutic recommendations. The paper emphasizes the role of early clinical suspicion, specific serologic and capillaroscopic findings, and the significance of evolving immunomodulatory and antifibrotic therapies. An individualized and multidisciplinary approach remains essential in improving patient outcomes and quality of life. https://apcz.umk.pl/QS/article/view/60484systemic sclerosissclerodermaautoimmunityvasculopathyfibrosisEULAR recommendations |
| spellingShingle | Olga Kądziołka Karolina Skonieczna Magdalena Badziąg Paulina Szulc Laura Kurczoba Martyna Kłossowska Olimpia Wiciun Kacper Ordon Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease? Quality in Sport systemic sclerosis scleroderma autoimmunity vasculopathy fibrosis EULAR recommendations |
| title | Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease? |
| title_full | Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease? |
| title_fullStr | Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease? |
| title_full_unstemmed | Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease? |
| title_short | Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease? |
| title_sort | systemic sclerosis a diagnostic challenge or a clinically controllable disease |
| topic | systemic sclerosis scleroderma autoimmunity vasculopathy fibrosis EULAR recommendations |
| url | https://apcz.umk.pl/QS/article/view/60484 |
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