Polycystic kidney with Caroli syndrome: a case report
<正>多囊肾是一种遗传性疾病,通常在40~60岁时导致终末期肾病,其特征是肾脏进行性增大,伴有较多囊肿、肾区疼痛、血尿和高血压。多囊肾常伴有肝、脾、卵巢等器官囊肿,以多囊肝最为多见。因此,有时会单纯认为多囊肝为多囊肾的并发症,但是这些囊性综合征与Caroli病之间的联系也是极其密切的。怀疑、筛查和及时诊断多囊肾患者中是否存在Caroli病,可延长患者的生存期及判断患者的预后<sup>[1]</sup>。病例资料患者,男性,34岁,于1997年因肉眼血尿发现有多囊肾,尿培养显示为结核菌感染,经正规治疗后痊愈。2010年...
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Editorial Department of Journal of Clinical Nephrology
2020-01-01
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| Series: | Linchuang shenzangbing zazhi |
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| author | ZHAN Tian-tian SHAO Ming-hai YE Chao-yang WANG Chen ZHOU Yuan CAO Xiao-juan QIAN Yi-ling |
| author_facet | ZHAN Tian-tian SHAO Ming-hai YE Chao-yang WANG Chen ZHOU Yuan CAO Xiao-juan QIAN Yi-ling |
| author_sort | ZHAN Tian-tian |
| collection | DOAJ |
| description | <正>多囊肾是一种遗传性疾病,通常在40~60岁时导致终末期肾病,其特征是肾脏进行性增大,伴有较多囊肿、肾区疼痛、血尿和高血压。多囊肾常伴有肝、脾、卵巢等器官囊肿,以多囊肝最为多见。因此,有时会单纯认为多囊肝为多囊肾的并发症,但是这些囊性综合征与Caroli病之间的联系也是极其密切的。怀疑、筛查和及时诊断多囊肾患者中是否存在Caroli病,可延长患者的生存期及判断患者的预后<sup>[1]</sup>。病例资料患者,男性,34岁,于1997年因肉眼血尿发现有多囊肾,尿培养显示为结核菌感染,经正规治疗后痊愈。2010年 |
| format | Article |
| id | doaj-art-4db79c854087416e89faf202db745e2c |
| institution | Kabale University |
| issn | 1671-2390 |
| language | zho |
| publishDate | 2020-01-01 |
| publisher | Editorial Department of Journal of Clinical Nephrology |
| record_format | Article |
| series | Linchuang shenzangbing zazhi |
| spelling | doaj-art-4db79c854087416e89faf202db745e2c2025-08-20T03:52:51ZzhoEditorial Department of Journal of Clinical NephrologyLinchuang shenzangbing zazhi1671-23902020-01-01868857910047Polycystic kidney with Caroli syndrome: a case reportZHAN Tian-tianSHAO Ming-haiYE Chao-yangWANG ChenZHOU YuanCAO Xiao-juanQIAN Yi-ling<正>多囊肾是一种遗传性疾病,通常在40~60岁时导致终末期肾病,其特征是肾脏进行性增大,伴有较多囊肿、肾区疼痛、血尿和高血压。多囊肾常伴有肝、脾、卵巢等器官囊肿,以多囊肝最为多见。因此,有时会单纯认为多囊肝为多囊肾的并发症,但是这些囊性综合征与Caroli病之间的联系也是极其密切的。怀疑、筛查和及时诊断多囊肾患者中是否存在Caroli病,可延长患者的生存期及判断患者的预后<sup>[1]</sup>。病例资料患者,男性,34岁,于1997年因肉眼血尿发现有多囊肾,尿培养显示为结核菌感染,经正规治疗后痊愈。2010年http://www.lcszb.com/thesisDetails?columnId=57910047&Fpath=home&index=0Caroli综合征多囊肾病例报告 |
| spellingShingle | ZHAN Tian-tian SHAO Ming-hai YE Chao-yang WANG Chen ZHOU Yuan CAO Xiao-juan QIAN Yi-ling Polycystic kidney with Caroli syndrome: a case report Linchuang shenzangbing zazhi Caroli综合征 多囊肾 病例报告 |
| title | Polycystic kidney with Caroli syndrome: a case report |
| title_full | Polycystic kidney with Caroli syndrome: a case report |
| title_fullStr | Polycystic kidney with Caroli syndrome: a case report |
| title_full_unstemmed | Polycystic kidney with Caroli syndrome: a case report |
| title_short | Polycystic kidney with Caroli syndrome: a case report |
| title_sort | polycystic kidney with caroli syndrome a case report |
| topic | Caroli综合征 多囊肾 病例报告 |
| url | http://www.lcszb.com/thesisDetails?columnId=57910047&Fpath=home&index=0 |
| work_keys_str_mv | AT zhantiantian polycystickidneywithcarolisyndromeacasereport AT shaominghai polycystickidneywithcarolisyndromeacasereport AT yechaoyang polycystickidneywithcarolisyndromeacasereport AT wangchen polycystickidneywithcarolisyndromeacasereport AT zhouyuan polycystickidneywithcarolisyndromeacasereport AT caoxiaojuan polycystickidneywithcarolisyndromeacasereport AT qianyiling polycystickidneywithcarolisyndromeacasereport |