Polycystic kidney with Caroli syndrome: a case report

<正>多囊肾是一种遗传性疾病,通常在40~60岁时导致终末期肾病,其特征是肾脏进行性增大,伴有较多囊肿、肾区疼痛、血尿和高血压。多囊肾常伴有肝、脾、卵巢等器官囊肿,以多囊肝最为多见。因此,有时会单纯认为多囊肝为多囊肾的并发症,但是这些囊性综合征与Caroli病之间的联系也是极其密切的。怀疑、筛查和及时诊断多囊肾患者中是否存在Caroli病,可延长患者的生存期及判断患者的预后<sup>[1]</sup>。病例资料患者,男性,34岁,于1997年因肉眼血尿发现有多囊肾,尿培养显示为结核菌感染,经正规治疗后痊愈。2010年...

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Main Authors: ZHAN Tian-tian, SHAO Ming-hai, YE Chao-yang, WANG Chen, ZHOU Yuan, CAO Xiao-juan, QIAN Yi-ling
Format: Article
Language:zho
Published: Editorial Department of Journal of Clinical Nephrology 2020-01-01
Series:Linchuang shenzangbing zazhi
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Online Access:http://www.lcszb.com/thesisDetails?columnId=57910047&Fpath=home&index=0
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author ZHAN Tian-tian
SHAO Ming-hai
YE Chao-yang
WANG Chen
ZHOU Yuan
CAO Xiao-juan
QIAN Yi-ling
author_facet ZHAN Tian-tian
SHAO Ming-hai
YE Chao-yang
WANG Chen
ZHOU Yuan
CAO Xiao-juan
QIAN Yi-ling
author_sort ZHAN Tian-tian
collection DOAJ
description <正>多囊肾是一种遗传性疾病,通常在40~60岁时导致终末期肾病,其特征是肾脏进行性增大,伴有较多囊肿、肾区疼痛、血尿和高血压。多囊肾常伴有肝、脾、卵巢等器官囊肿,以多囊肝最为多见。因此,有时会单纯认为多囊肝为多囊肾的并发症,但是这些囊性综合征与Caroli病之间的联系也是极其密切的。怀疑、筛查和及时诊断多囊肾患者中是否存在Caroli病,可延长患者的生存期及判断患者的预后<sup>[1]</sup>。病例资料患者,男性,34岁,于1997年因肉眼血尿发现有多囊肾,尿培养显示为结核菌感染,经正规治疗后痊愈。2010年
format Article
id doaj-art-4db79c854087416e89faf202db745e2c
institution Kabale University
issn 1671-2390
language zho
publishDate 2020-01-01
publisher Editorial Department of Journal of Clinical Nephrology
record_format Article
series Linchuang shenzangbing zazhi
spelling doaj-art-4db79c854087416e89faf202db745e2c2025-08-20T03:52:51ZzhoEditorial Department of Journal of Clinical NephrologyLinchuang shenzangbing zazhi1671-23902020-01-01868857910047Polycystic kidney with Caroli syndrome: a case reportZHAN Tian-tianSHAO Ming-haiYE Chao-yangWANG ChenZHOU YuanCAO Xiao-juanQIAN Yi-ling<正>多囊肾是一种遗传性疾病,通常在40~60岁时导致终末期肾病,其特征是肾脏进行性增大,伴有较多囊肿、肾区疼痛、血尿和高血压。多囊肾常伴有肝、脾、卵巢等器官囊肿,以多囊肝最为多见。因此,有时会单纯认为多囊肝为多囊肾的并发症,但是这些囊性综合征与Caroli病之间的联系也是极其密切的。怀疑、筛查和及时诊断多囊肾患者中是否存在Caroli病,可延长患者的生存期及判断患者的预后<sup>[1]</sup>。病例资料患者,男性,34岁,于1997年因肉眼血尿发现有多囊肾,尿培养显示为结核菌感染,经正规治疗后痊愈。2010年http://www.lcszb.com/thesisDetails?columnId=57910047&Fpath=home&index=0Caroli综合征多囊肾病例报告
spellingShingle ZHAN Tian-tian
SHAO Ming-hai
YE Chao-yang
WANG Chen
ZHOU Yuan
CAO Xiao-juan
QIAN Yi-ling
Polycystic kidney with Caroli syndrome: a case report
Linchuang shenzangbing zazhi
Caroli综合征
多囊肾
病例报告
title Polycystic kidney with Caroli syndrome: a case report
title_full Polycystic kidney with Caroli syndrome: a case report
title_fullStr Polycystic kidney with Caroli syndrome: a case report
title_full_unstemmed Polycystic kidney with Caroli syndrome: a case report
title_short Polycystic kidney with Caroli syndrome: a case report
title_sort polycystic kidney with caroli syndrome a case report
topic Caroli综合征
多囊肾
病例报告
url http://www.lcszb.com/thesisDetails?columnId=57910047&Fpath=home&index=0
work_keys_str_mv AT zhantiantian polycystickidneywithcarolisyndromeacasereport
AT shaominghai polycystickidneywithcarolisyndromeacasereport
AT yechaoyang polycystickidneywithcarolisyndromeacasereport
AT wangchen polycystickidneywithcarolisyndromeacasereport
AT zhouyuan polycystickidneywithcarolisyndromeacasereport
AT caoxiaojuan polycystickidneywithcarolisyndromeacasereport
AT qianyiling polycystickidneywithcarolisyndromeacasereport