Central retinal vein occlusion: A patient with systemic sclerosis

Introduction. Scleroderma (systemic sclerosis) is a severe chronic connective tissue disease, which results in involvement of numerous internal organs. Changes in the eye are the consequences of organ-specific manifestations of scleroderma or adverse effects of immunosuppressive treatment applied. C...

Full description

Saved in:
Bibliographic Details
Main Authors: Karadžić Jelena, Radosavljević Aleksandra, Kovačević Igor
Format: Article
Language:English
Published: Ministry of Defence of the Republic of Serbia, University of Defence, Belgrade 2016-01-01
Series:Vojnosanitetski Pregled
Subjects:
Online Access:http://www.doiserbia.nb.rs/img/doi/0042-8450/2016/0042-84501600073K.pdf
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849406498875113472
author Karadžić Jelena
Radosavljević Aleksandra
Kovačević Igor
author_facet Karadžić Jelena
Radosavljević Aleksandra
Kovačević Igor
author_sort Karadžić Jelena
collection DOAJ
description Introduction. Scleroderma (systemic sclerosis) is a severe chronic connective tissue disease, which results in involvement of numerous internal organs. Changes in the eye are the consequences of organ-specific manifestations of scleroderma or adverse effects of immunosuppressive treatment applied. Case report. We reported a 42-year-old woman with systemic sclerosis and acute deterioration of vision in the left eye, with visual acuity 0.9. After thorough clinical examination, including fluorescein angiography and optical coherence tomography, the diagnosis of nonischemic central retinal vein occlusion was made. Further biochemical, rheumatological and immunological investigation, apart from inactive systemic sclerosis, showed normal findings. Therefore, the cause of central retinal vein occlusion could only be attributed to the microvascular changes in systemic sclerosis. After three months, visual acuity deteriorated to 0.6 due to the development of cystoid macular edema. The patient received intravitreal injection of bevacizumab and after a single dose visual acuity improved to 0.9. After a 6- month follow-up, macular edema resolved and visual acuity stabilized. Conclusion. According to our knowledge and current data from the literature, central retinal vein occlusion is a rare vision threatening manifestation of scleroderma. There are only few published case reports on central vein occlusion in scleroderma patients. Examination of the ocular fundus is recommended for evaluation of vascular disease in patients with systemic sclerosis.
format Article
id doaj-art-4da58b2a24cd42d4b3f08951745f3629
institution Kabale University
issn 0042-8450
2406-0720
language English
publishDate 2016-01-01
publisher Ministry of Defence of the Republic of Serbia, University of Defence, Belgrade
record_format Article
series Vojnosanitetski Pregled
spelling doaj-art-4da58b2a24cd42d4b3f08951745f36292025-08-20T03:36:22ZengMinistry of Defence of the Republic of Serbia, University of Defence, BelgradeVojnosanitetski Pregled0042-84502406-07202016-01-0173986887210.2298/VSP141028073K0042-84501600073KCentral retinal vein occlusion: A patient with systemic sclerosisKaradžić Jelena0Radosavljević Aleksandra1Kovačević Igor2Clinical Centre of Serbia, Clinic for Eye Diseases, BelgradeClinical Centre of Serbia, Clinic for Eye Diseases, Belgrade + Faculty of Medicine, BelgradeClinical Centre of Serbia, Clinic for Eye Diseases, Belgrade + Faculty of Medicine, BelgradeIntroduction. Scleroderma (systemic sclerosis) is a severe chronic connective tissue disease, which results in involvement of numerous internal organs. Changes in the eye are the consequences of organ-specific manifestations of scleroderma or adverse effects of immunosuppressive treatment applied. Case report. We reported a 42-year-old woman with systemic sclerosis and acute deterioration of vision in the left eye, with visual acuity 0.9. After thorough clinical examination, including fluorescein angiography and optical coherence tomography, the diagnosis of nonischemic central retinal vein occlusion was made. Further biochemical, rheumatological and immunological investigation, apart from inactive systemic sclerosis, showed normal findings. Therefore, the cause of central retinal vein occlusion could only be attributed to the microvascular changes in systemic sclerosis. After three months, visual acuity deteriorated to 0.6 due to the development of cystoid macular edema. The patient received intravitreal injection of bevacizumab and after a single dose visual acuity improved to 0.9. After a 6- month follow-up, macular edema resolved and visual acuity stabilized. Conclusion. According to our knowledge and current data from the literature, central retinal vein occlusion is a rare vision threatening manifestation of scleroderma. There are only few published case reports on central vein occlusion in scleroderma patients. Examination of the ocular fundus is recommended for evaluation of vascular disease in patients with systemic sclerosis.http://www.doiserbia.nb.rs/img/doi/0042-8450/2016/0042-84501600073K.pdfscleroderma, systemicretinal vein occlusiondiagnosisangiogenesis inhibitorstreatment outcome
spellingShingle Karadžić Jelena
Radosavljević Aleksandra
Kovačević Igor
Central retinal vein occlusion: A patient with systemic sclerosis
Vojnosanitetski Pregled
scleroderma, systemic
retinal vein occlusion
diagnosis
angiogenesis inhibitors
treatment outcome
title Central retinal vein occlusion: A patient with systemic sclerosis
title_full Central retinal vein occlusion: A patient with systemic sclerosis
title_fullStr Central retinal vein occlusion: A patient with systemic sclerosis
title_full_unstemmed Central retinal vein occlusion: A patient with systemic sclerosis
title_short Central retinal vein occlusion: A patient with systemic sclerosis
title_sort central retinal vein occlusion a patient with systemic sclerosis
topic scleroderma, systemic
retinal vein occlusion
diagnosis
angiogenesis inhibitors
treatment outcome
url http://www.doiserbia.nb.rs/img/doi/0042-8450/2016/0042-84501600073K.pdf
work_keys_str_mv AT karadzicjelena centralretinalveinocclusionapatientwithsystemicsclerosis
AT radosavljevicaleksandra centralretinalveinocclusionapatientwithsystemicsclerosis
AT kovacevicigor centralretinalveinocclusionapatientwithsystemicsclerosis