Aggressive intracranial fibromatosis: case report Fibromatose agressiva intracraniana: relato de caso
Fibromatosis is a locally aggressive, proliferative fibroblastic lesion affecting musculoaponeurotic structures, most often in the limbs and trunk. Intracranial fibromatosis is extremely rare and requires aggressive treatment to prevent recurrence. Case Description - We present the case of a 20 year...
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| Format: | Article |
| Language: | English |
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Thieme Revinter Publicações
2006-06-01
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| Series: | Arquivos de Neuro-Psiquiatria |
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| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2006000300031 |
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| author | Oswaldo Inácio de Tella Jr Luciano Ricardo França Silva João Norberto Stavale Marco Antonio Herculano Manoel Antonio de Paiva Neto Celso Agner |
| author_facet | Oswaldo Inácio de Tella Jr Luciano Ricardo França Silva João Norberto Stavale Marco Antonio Herculano Manoel Antonio de Paiva Neto Celso Agner |
| author_sort | Oswaldo Inácio de Tella Jr |
| collection | DOAJ |
| description | Fibromatosis is a locally aggressive, proliferative fibroblastic lesion affecting musculoaponeurotic structures, most often in the limbs and trunk. Intracranial fibromatosis is extremely rare and requires aggressive treatment to prevent recurrence. Case Description - We present the case of a 20 year old woman with aggressive skull base fibromatosis. The lesion extended through the sphenoid, ethmoid sinus and nasal cavity, destroying the right roof of the orbit and penetrating in anterior skull base. A combined anterior craniofacial approach was performed; complete resection with surgical margin was impossible due to the localization of the tumor and relation to important neurovascular structures. Complete resection with surgical margin is often impossible because of its widely infiltrative nature. Radiotherapy and chemotherapy are often required to improve local control of the lesion.<br>Fibromatose é lesão fibroblástica proliferativa com agressividade localizada, afetando as estruturas músculo-aponeuróticas e acometendo, mais freqüentemente, os membros e tronco. A fibromatose intracraniana é rara e requer tratamento agressivo para evitar recidiva. Descrevemos uma paciente de 20 anos portadora de fibromatose agressiva de base de crânio. A lesão se estendia através da cavidade nasal, seios esfenoidal e etmoidal, destruindo o teto da órbita direita e invadindo a porção anterior da base do crânio. A paciente foi submetida a uma via craniofacial anterior combinada, não sendo possível uma ressecção completa devido ao envolvimento de estruturas neurovasculares. A ressecção completa é, freqüentemente, impossível devido sua natureza infiltrativa. Radioterapia e quimioterapia são indicadas para melhorar o controle da lesão. |
| format | Article |
| id | doaj-art-4d8656b41e924f339e3f0add694366f6 |
| institution | OA Journals |
| issn | 0004-282X 1678-4227 |
| language | English |
| publishDate | 2006-06-01 |
| publisher | Thieme Revinter Publicações |
| record_format | Article |
| series | Arquivos de Neuro-Psiquiatria |
| spelling | doaj-art-4d8656b41e924f339e3f0add694366f62025-08-20T02:38:43ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria0004-282X1678-42272006-06-01642b51651910.1590/S0004-282X2006000300031Aggressive intracranial fibromatosis: case report Fibromatose agressiva intracraniana: relato de casoOswaldo Inácio de Tella JrLuciano Ricardo França SilvaJoão Norberto StavaleMarco Antonio HerculanoManoel Antonio de Paiva NetoCelso AgnerFibromatosis is a locally aggressive, proliferative fibroblastic lesion affecting musculoaponeurotic structures, most often in the limbs and trunk. Intracranial fibromatosis is extremely rare and requires aggressive treatment to prevent recurrence. Case Description - We present the case of a 20 year old woman with aggressive skull base fibromatosis. The lesion extended through the sphenoid, ethmoid sinus and nasal cavity, destroying the right roof of the orbit and penetrating in anterior skull base. A combined anterior craniofacial approach was performed; complete resection with surgical margin was impossible due to the localization of the tumor and relation to important neurovascular structures. Complete resection with surgical margin is often impossible because of its widely infiltrative nature. Radiotherapy and chemotherapy are often required to improve local control of the lesion.<br>Fibromatose é lesão fibroblástica proliferativa com agressividade localizada, afetando as estruturas músculo-aponeuróticas e acometendo, mais freqüentemente, os membros e tronco. A fibromatose intracraniana é rara e requer tratamento agressivo para evitar recidiva. Descrevemos uma paciente de 20 anos portadora de fibromatose agressiva de base de crânio. A lesão se estendia através da cavidade nasal, seios esfenoidal e etmoidal, destruindo o teto da órbita direita e invadindo a porção anterior da base do crânio. A paciente foi submetida a uma via craniofacial anterior combinada, não sendo possível uma ressecção completa devido ao envolvimento de estruturas neurovasculares. A ressecção completa é, freqüentemente, impossível devido sua natureza infiltrativa. Radioterapia e quimioterapia são indicadas para melhorar o controle da lesão.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2006000300031fibromatose intracranianabase do crâniovia craniofacialintracranial fibromatosisskull basecraniofacial approach |
| spellingShingle | Oswaldo Inácio de Tella Jr Luciano Ricardo França Silva João Norberto Stavale Marco Antonio Herculano Manoel Antonio de Paiva Neto Celso Agner Aggressive intracranial fibromatosis: case report Fibromatose agressiva intracraniana: relato de caso Arquivos de Neuro-Psiquiatria fibromatose intracraniana base do crânio via craniofacial intracranial fibromatosis skull base craniofacial approach |
| title | Aggressive intracranial fibromatosis: case report Fibromatose agressiva intracraniana: relato de caso |
| title_full | Aggressive intracranial fibromatosis: case report Fibromatose agressiva intracraniana: relato de caso |
| title_fullStr | Aggressive intracranial fibromatosis: case report Fibromatose agressiva intracraniana: relato de caso |
| title_full_unstemmed | Aggressive intracranial fibromatosis: case report Fibromatose agressiva intracraniana: relato de caso |
| title_short | Aggressive intracranial fibromatosis: case report Fibromatose agressiva intracraniana: relato de caso |
| title_sort | aggressive intracranial fibromatosis case report fibromatose agressiva intracraniana relato de caso |
| topic | fibromatose intracraniana base do crânio via craniofacial intracranial fibromatosis skull base craniofacial approach |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2006000300031 |
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