A Puzzling Case of Rapidly Progressive Global CNS Deterioration From Intravascular Large-Cell Lymphoma

Intravascular large-cell lymphoma is a rare, aggressive subtype of B-cell lymphoma leading to microvascular organ dysfunction. It often presents nonspecifically and is difficult to diagnose, with a rapidly progressive course. It classically presents with “B” symptoms, although any organ system can b...

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Main Authors: Chloe Weidenbaum, Akanksha Kushwah, Henry Edwards, Rachel Ward, Joy Underwood, Dyveke Pratt
Format: Article
Language:English
Published: American College of Physicians 2023-01-01
Series:Annals of Internal Medicine: Clinical Cases
Online Access:https://www.acpjournals.org/doi/10.7326/aimcc.2022.0356
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author Chloe Weidenbaum
Akanksha Kushwah
Henry Edwards
Rachel Ward
Joy Underwood
Dyveke Pratt
author_facet Chloe Weidenbaum
Akanksha Kushwah
Henry Edwards
Rachel Ward
Joy Underwood
Dyveke Pratt
author_sort Chloe Weidenbaum
collection DOAJ
description Intravascular large-cell lymphoma is a rare, aggressive subtype of B-cell lymphoma leading to microvascular organ dysfunction. It often presents nonspecifically and is difficult to diagnose, with a rapidly progressive course. It classically presents with “B” symptoms, although any organ system can be affected. Neurologic symptoms vary but can involve rapid neurologic deterioration. It lacks association with a primary tumor or malignant cells in the blood or bone marrow, so diagnosis is difficult, made only by biopsy of affected tissues. Because of its rarity and often aggressive course, increased clinician familiarity is key to facilitating early diagnosis and proper management.
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issn 2767-7664
language English
publishDate 2023-01-01
publisher American College of Physicians
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series Annals of Internal Medicine: Clinical Cases
spelling doaj-art-4d76a9e7a447415c94347b498282467e2025-08-20T03:18:45ZengAmerican College of PhysiciansAnnals of Internal Medicine: Clinical Cases2767-76642023-01-012110.7326/aimcc.2022.0356A Puzzling Case of Rapidly Progressive Global CNS Deterioration From Intravascular Large-Cell LymphomaChloe Weidenbaum0Akanksha Kushwah1Henry Edwards2Rachel Ward3Joy Underwood4Dyveke Pratt51Department of Internal Medicine, University of Tennessee Health Science Center – Nashville, Nashville, Tennessee1Department of Internal Medicine, University of Tennessee Health Science Center – Nashville, Nashville, Tennessee2Ascension Saint Thomas Hospitals, Nashville, Tennessee1Department of Internal Medicine, University of Tennessee Health Science Center – Nashville, Nashville, Tennessee1Department of Internal Medicine, University of Tennessee Health Science Center – Nashville, Nashville, Tennessee2Ascension Saint Thomas Hospitals, Nashville, TennesseeIntravascular large-cell lymphoma is a rare, aggressive subtype of B-cell lymphoma leading to microvascular organ dysfunction. It often presents nonspecifically and is difficult to diagnose, with a rapidly progressive course. It classically presents with “B” symptoms, although any organ system can be affected. Neurologic symptoms vary but can involve rapid neurologic deterioration. It lacks association with a primary tumor or malignant cells in the blood or bone marrow, so diagnosis is difficult, made only by biopsy of affected tissues. Because of its rarity and often aggressive course, increased clinician familiarity is key to facilitating early diagnosis and proper management.https://www.acpjournals.org/doi/10.7326/aimcc.2022.0356
spellingShingle Chloe Weidenbaum
Akanksha Kushwah
Henry Edwards
Rachel Ward
Joy Underwood
Dyveke Pratt
A Puzzling Case of Rapidly Progressive Global CNS Deterioration From Intravascular Large-Cell Lymphoma
Annals of Internal Medicine: Clinical Cases
title A Puzzling Case of Rapidly Progressive Global CNS Deterioration From Intravascular Large-Cell Lymphoma
title_full A Puzzling Case of Rapidly Progressive Global CNS Deterioration From Intravascular Large-Cell Lymphoma
title_fullStr A Puzzling Case of Rapidly Progressive Global CNS Deterioration From Intravascular Large-Cell Lymphoma
title_full_unstemmed A Puzzling Case of Rapidly Progressive Global CNS Deterioration From Intravascular Large-Cell Lymphoma
title_short A Puzzling Case of Rapidly Progressive Global CNS Deterioration From Intravascular Large-Cell Lymphoma
title_sort puzzling case of rapidly progressive global cns deterioration from intravascular large cell lymphoma
url https://www.acpjournals.org/doi/10.7326/aimcc.2022.0356
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