Scimitar syndrome: unveiling the complexities of a rare congenital cardiopulmonary anomaly
Scimitar syndrome is a rare congenital anomaly characterised by anomalous pulmonary venous drainage of the right lung into the inferior vena cava, often accompanied by right lung hypoplasia and dextroposition of the heart. Here, we present the case of a 24-year-old female with scimitar syndrome and...
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| Language: | English |
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SMC MEDIA SRL
2025-02-01
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| Series: | European Journal of Case Reports in Internal Medicine |
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| Online Access: | https://www.ejcrim.com/index.php/EJCRIM/article/view/5044 |
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| author | Nargis Mateen Abraam Rezkalla Nagihan Orhun |
| author_facet | Nargis Mateen Abraam Rezkalla Nagihan Orhun |
| author_sort | Nargis Mateen |
| collection | DOAJ |
| description | Scimitar syndrome is a rare congenital anomaly characterised by anomalous pulmonary venous drainage of the right lung into the inferior vena cava, often accompanied by right lung hypoplasia and dextroposition of the heart. Here, we present the case of a 24-year-old female with scimitar syndrome and a history of asthma who presented with acute exacerbation of asthma. A chest X-ray revealed opacification of the right hemithorax, and a CT angiography revealed congenital hypoplasia of the right lung and dextrocardia. This report provides a detailed description of scimitar syndrome to spread awareness of this rare diagnosis and highlights the unique and various constellations of anatomical abnormalities seen in scimitar syndrome that make diagnosis difficult. |
| format | Article |
| id | doaj-art-4d5e32e4f452402c88d27e50b4ed0363 |
| institution | DOAJ |
| issn | 2284-2594 |
| language | English |
| publishDate | 2025-02-01 |
| publisher | SMC MEDIA SRL |
| record_format | Article |
| series | European Journal of Case Reports in Internal Medicine |
| spelling | doaj-art-4d5e32e4f452402c88d27e50b4ed03632025-08-20T03:00:55ZengSMC MEDIA SRLEuropean Journal of Case Reports in Internal Medicine2284-25942025-02-0110.12890/2025_0050444579Scimitar syndrome: unveiling the complexities of a rare congenital cardiopulmonary anomalyNargis Mateen0Abraam Rezkalla1Nagihan Orhun2Department of Internal Medicine, St. Josephs University Medical Center, Paterson, USADepartment of Internal Medicine, St. Josephs University Medical Center, Paterson, USADepartment of Internal Medicine, St. Josephs University Medical Center, Paterson, USAScimitar syndrome is a rare congenital anomaly characterised by anomalous pulmonary venous drainage of the right lung into the inferior vena cava, often accompanied by right lung hypoplasia and dextroposition of the heart. Here, we present the case of a 24-year-old female with scimitar syndrome and a history of asthma who presented with acute exacerbation of asthma. A chest X-ray revealed opacification of the right hemithorax, and a CT angiography revealed congenital hypoplasia of the right lung and dextrocardia. This report provides a detailed description of scimitar syndrome to spread awareness of this rare diagnosis and highlights the unique and various constellations of anatomical abnormalities seen in scimitar syndrome that make diagnosis difficult.https://www.ejcrim.com/index.php/EJCRIM/article/view/5044scimitar syndromepulmonary hypoplasiaasthma exacerbationdextrocardiarare congenital anomaly |
| spellingShingle | Nargis Mateen Abraam Rezkalla Nagihan Orhun Scimitar syndrome: unveiling the complexities of a rare congenital cardiopulmonary anomaly European Journal of Case Reports in Internal Medicine scimitar syndrome pulmonary hypoplasia asthma exacerbation dextrocardia rare congenital anomaly |
| title | Scimitar syndrome: unveiling the complexities of a rare congenital cardiopulmonary anomaly |
| title_full | Scimitar syndrome: unveiling the complexities of a rare congenital cardiopulmonary anomaly |
| title_fullStr | Scimitar syndrome: unveiling the complexities of a rare congenital cardiopulmonary anomaly |
| title_full_unstemmed | Scimitar syndrome: unveiling the complexities of a rare congenital cardiopulmonary anomaly |
| title_short | Scimitar syndrome: unveiling the complexities of a rare congenital cardiopulmonary anomaly |
| title_sort | scimitar syndrome unveiling the complexities of a rare congenital cardiopulmonary anomaly |
| topic | scimitar syndrome pulmonary hypoplasia asthma exacerbation dextrocardia rare congenital anomaly |
| url | https://www.ejcrim.com/index.php/EJCRIM/article/view/5044 |
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