Alanine Aminotransferase Deficiency in a Patient With Hyperferritinemia, Steatosis Hepatis, and Hepatosplenomegaly

The glutamate pyruvate transaminase enzyme, also called alanine aminotransferase (ALT), plays an important role in gluconeogenesis and amino acid metabolism. It catalyzes the reversible transamination of L-alanine and α-ketoglutarate to pyruvate and L-glutamate. ALT is mostly located in the liver bu...

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Main Authors: Alexander Olkus, Sebastian Sailer, Katharina Obeid, Katrin Hinderhofer, Uta Merle, Christian P. Schaaf
Format: Article
Language:English
Published: American College of Physicians 2022-10-01
Series:Annals of Internal Medicine: Clinical Cases
Online Access:https://www.acpjournals.org/doi/10.7326/aimcc.2022.0164
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author Alexander Olkus
Sebastian Sailer
Katharina Obeid
Katrin Hinderhofer
Uta Merle
Christian P. Schaaf
author_facet Alexander Olkus
Sebastian Sailer
Katharina Obeid
Katrin Hinderhofer
Uta Merle
Christian P. Schaaf
author_sort Alexander Olkus
collection DOAJ
description The glutamate pyruvate transaminase enzyme, also called alanine aminotransferase (ALT), plays an important role in gluconeogenesis and amino acid metabolism. It catalyzes the reversible transamination of L-alanine and α-ketoglutarate to pyruvate and L-glutamate. ALT is mostly located in the liver but is also present in other organs like kidney, heart, skeletal muscle, pancreas, and spleen. ALT deficiency was reported in a case of hepatitis B and hepatitis C infection, whereas complete absence of ALT, to our knowledge, has only been reported in 1 case of acute liver failure.
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series Annals of Internal Medicine: Clinical Cases
spelling doaj-art-4d343dafca4f4110880cdeccbb7f13022025-08-20T03:18:45ZengAmerican College of PhysiciansAnnals of Internal Medicine: Clinical Cases2767-76642022-10-011810.7326/aimcc.2022.0164Alanine Aminotransferase Deficiency in a Patient With Hyperferritinemia, Steatosis Hepatis, and HepatosplenomegalyAlexander Olkus0Sebastian Sailer1Katharina Obeid2Katrin Hinderhofer3Uta Merle4Christian P. Schaaf51Department of Internal Medicine IV, Heidelberg University Hospital, Heidelberg, Germany2Institute of Human Genetics, Heidelberg University, Heidelberg, Germany2Institute of Human Genetics, Heidelberg University, Heidelberg, Germany2Institute of Human Genetics, Heidelberg University, Heidelberg, Germany1Department of Internal Medicine IV, Heidelberg University Hospital, Heidelberg, Germany2Institute of Human Genetics, Heidelberg University, Heidelberg, GermanyThe glutamate pyruvate transaminase enzyme, also called alanine aminotransferase (ALT), plays an important role in gluconeogenesis and amino acid metabolism. It catalyzes the reversible transamination of L-alanine and α-ketoglutarate to pyruvate and L-glutamate. ALT is mostly located in the liver but is also present in other organs like kidney, heart, skeletal muscle, pancreas, and spleen. ALT deficiency was reported in a case of hepatitis B and hepatitis C infection, whereas complete absence of ALT, to our knowledge, has only been reported in 1 case of acute liver failure.https://www.acpjournals.org/doi/10.7326/aimcc.2022.0164
spellingShingle Alexander Olkus
Sebastian Sailer
Katharina Obeid
Katrin Hinderhofer
Uta Merle
Christian P. Schaaf
Alanine Aminotransferase Deficiency in a Patient With Hyperferritinemia, Steatosis Hepatis, and Hepatosplenomegaly
Annals of Internal Medicine: Clinical Cases
title Alanine Aminotransferase Deficiency in a Patient With Hyperferritinemia, Steatosis Hepatis, and Hepatosplenomegaly
title_full Alanine Aminotransferase Deficiency in a Patient With Hyperferritinemia, Steatosis Hepatis, and Hepatosplenomegaly
title_fullStr Alanine Aminotransferase Deficiency in a Patient With Hyperferritinemia, Steatosis Hepatis, and Hepatosplenomegaly
title_full_unstemmed Alanine Aminotransferase Deficiency in a Patient With Hyperferritinemia, Steatosis Hepatis, and Hepatosplenomegaly
title_short Alanine Aminotransferase Deficiency in a Patient With Hyperferritinemia, Steatosis Hepatis, and Hepatosplenomegaly
title_sort alanine aminotransferase deficiency in a patient with hyperferritinemia steatosis hepatis and hepatosplenomegaly
url https://www.acpjournals.org/doi/10.7326/aimcc.2022.0164
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