A Case of Amyloidosis Presenting as Lymphadenopathy at the Porta Hepatis

We report a rare case of systemic amyloidosis with gastrointestinal and lymph node involvement. A 64-year-old woman was admitted to our hospital with dyspepsia and weight loss. Initial esophagogastroduodenoscopy (EGD) revealed nonspecific findings, and abdominal computed tomography showed necrotizin...

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Main Authors: Ja In Lee, Joon Sung Kim, Byung Wook Kim
Format: Article
Language:English
Published: Korean College of Helicobacter and Upper Gastrointestinal Research 2018-09-01
Series:The Korean Journal of Helicobacter and Upper Gastrointestinal Research
Subjects:
Online Access:http://www.helicojournal.org/journal/view.html?doi=10.7704/kjhugr.2018.18.3.209
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author Ja In Lee
Joon Sung Kim
Byung Wook Kim
author_facet Ja In Lee
Joon Sung Kim
Byung Wook Kim
author_sort Ja In Lee
collection DOAJ
description We report a rare case of systemic amyloidosis with gastrointestinal and lymph node involvement. A 64-year-old woman was admitted to our hospital with dyspepsia and weight loss. Initial esophagogastroduodenoscopy (EGD) revealed nonspecific findings, and abdominal computed tomography showed necrotizing lymphadenopathy at the porta hepatis. Laparoscopic lymph node biopsy was performed under suspicion of tuberculous lymphadenopathy, but a definite diagnosis was not established. Follow-up EGD performed 6 months later revealed multiple telangiectasia-like lesions at the gastric body, and endoscopic biopsy revealed amyloid deposition. Through additional blood and urine protein electrophoresis, the patient was finally diagnosed with systemic amyloidosis associated with multiple myeloma. She was treated with dexamethasone, thalidomide, and bortezomib; however, she died 3 months after diagnosis because of pneumonia and multiple organ failure.
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spelling doaj-art-4cd258bf819947338dafe648fb00a4492025-08-20T03:58:23ZengKorean College of Helicobacter and Upper Gastrointestinal ResearchThe Korean Journal of Helicobacter and Upper Gastrointestinal Research1738-33312018-09-0118320921210.7704/kjhugr.2018.18.3.209kjhugr.2018.18.3.209A Case of Amyloidosis Presenting as Lymphadenopathy at the Porta HepatisJa In Lee0Joon Sung Kim1Byung Wook Kim2Division of Gastroenterology, Department of Internal Medicine, Incheon St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Incheon, KoreaDivision of Gastroenterology, Department of Internal Medicine, Incheon St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Incheon, KoreaDivision of Gastroenterology, Department of Internal Medicine, Incheon St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Incheon, KoreaWe report a rare case of systemic amyloidosis with gastrointestinal and lymph node involvement. A 64-year-old woman was admitted to our hospital with dyspepsia and weight loss. Initial esophagogastroduodenoscopy (EGD) revealed nonspecific findings, and abdominal computed tomography showed necrotizing lymphadenopathy at the porta hepatis. Laparoscopic lymph node biopsy was performed under suspicion of tuberculous lymphadenopathy, but a definite diagnosis was not established. Follow-up EGD performed 6 months later revealed multiple telangiectasia-like lesions at the gastric body, and endoscopic biopsy revealed amyloid deposition. Through additional blood and urine protein electrophoresis, the patient was finally diagnosed with systemic amyloidosis associated with multiple myeloma. She was treated with dexamethasone, thalidomide, and bortezomib; however, she died 3 months after diagnosis because of pneumonia and multiple organ failure.http://www.helicojournal.org/journal/view.html?doi=10.7704/kjhugr.2018.18.3.209AmyloidosisLymphadenopathyMultiple myeloma
spellingShingle Ja In Lee
Joon Sung Kim
Byung Wook Kim
A Case of Amyloidosis Presenting as Lymphadenopathy at the Porta Hepatis
The Korean Journal of Helicobacter and Upper Gastrointestinal Research
Amyloidosis
Lymphadenopathy
Multiple myeloma
title A Case of Amyloidosis Presenting as Lymphadenopathy at the Porta Hepatis
title_full A Case of Amyloidosis Presenting as Lymphadenopathy at the Porta Hepatis
title_fullStr A Case of Amyloidosis Presenting as Lymphadenopathy at the Porta Hepatis
title_full_unstemmed A Case of Amyloidosis Presenting as Lymphadenopathy at the Porta Hepatis
title_short A Case of Amyloidosis Presenting as Lymphadenopathy at the Porta Hepatis
title_sort case of amyloidosis presenting as lymphadenopathy at the porta hepatis
topic Amyloidosis
Lymphadenopathy
Multiple myeloma
url http://www.helicojournal.org/journal/view.html?doi=10.7704/kjhugr.2018.18.3.209
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