Predicting survival outcomes in dedifferentiated chondrosarcoma: a prognostic factor analysis from a National Registry

Introduction: Dedifferentiated chondrosarcoma (DDCS) is a high-grade subtype of chondrosarcoma with a poor prognosis. Treatment for localized DDCS generally involves wide resection; the effectiveness of adjuvant radiotherapy and chemotherapy is questionable. This research was designed to find progno...

Full description

Saved in:
Bibliographic Details
Main Authors: Masunaga Tomoya, Tsukamoto Shinji, Honoki Kanya, Fujii Hiromasa, Kido Akira, Akahane Manabu, Tanaka Yasuhito, Mavrogenis Andreas F., Errani Costantino, Kawai Akira
Format: Article
Language:English
Published: EDP Sciences 2025-01-01
Series:SICOT-J
Subjects:
Online Access:https://www.sicot-j.org/articles/sicotj/full_html/2025/01/sicotj250012/sicotj250012.html
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849761757296328704
author Masunaga Tomoya
Tsukamoto Shinji
Honoki Kanya
Fujii Hiromasa
Kido Akira
Akahane Manabu
Tanaka Yasuhito
Mavrogenis Andreas F.
Errani Costantino
Kawai Akira
author_facet Masunaga Tomoya
Tsukamoto Shinji
Honoki Kanya
Fujii Hiromasa
Kido Akira
Akahane Manabu
Tanaka Yasuhito
Mavrogenis Andreas F.
Errani Costantino
Kawai Akira
author_sort Masunaga Tomoya
collection DOAJ
description Introduction: Dedifferentiated chondrosarcoma (DDCS) is a high-grade subtype of chondrosarcoma with a poor prognosis. Treatment for localized DDCS generally involves wide resection; the effectiveness of adjuvant radiotherapy and chemotherapy is questionable. This research was designed to find prognostic factors for DDCS and evaluate the impact of adjuvant therapies on localized cases. Methods: One hundred thirty-two patients with DDCS diagnosed by pathology in the period 2006 to 2022 were identified in the Japanese National Bone and Soft Tissue Tumor Registry database and were retrospectively analyzed. Results: Patients with distant metastases at diagnosis (n = 34) had significantly poorer survival than those without metastases (n = 98), with a 5-year disease-specific survival (DSS) of 9.7% vs. 37.1% (P < 0.0001). For patients without distant metastasis at diagnosis, uni- and multivariate analysis showed that R1 or R2 surgical margin was an independent risk factor linked with unfavorable local recurrence (hazard ratio [HR] 3.39 [95% CI: 1.35–8.52]; P = 0.010). Adjuvant radiotherapy was not associated with local recurrence (HR 2.41 [95% CI: 0.87–6.64]; P = 0.090). Larger size (HR 1.13 [95% CI: 1.06–1.19]; P < 0.001) and no surgery (HR 3.87 [95% CI: 1.61–9.28]; P = 0.002) were independent risk factors for unfavorable DSS. Previous surgery (HR 0.19 [95% CI: 0.04–0.84]; P = 0.028) and adjuvant chemotherapy (HR 0.36 [95% CI: 0.16–0.77]; P = 0.009) were independent risk factors for favorable DSS. Discussion: Survival may have been improved by chemotherapy, but the effect of adjuvant radiotherapy in controlling the local spread of the tumor appears to have been limited in DDCS cases that were localized.
format Article
id doaj-art-4a38642fe0c246f6affbeba52016f7f5
institution DOAJ
issn 2426-8887
language English
publishDate 2025-01-01
publisher EDP Sciences
record_format Article
series SICOT-J
spelling doaj-art-4a38642fe0c246f6affbeba52016f7f52025-08-20T03:05:55ZengEDP SciencesSICOT-J2426-88872025-01-01111610.1051/sicotj/2025011sicotj250012Predicting survival outcomes in dedifferentiated chondrosarcoma: a prognostic factor analysis from a National RegistryMasunaga Tomoya0Tsukamoto Shinji1https://orcid.org/0000-0002-8419-2008Honoki Kanya2https://orcid.org/0000-0001-6763-0478Fujii Hiromasa3Kido Akira4https://orcid.org/0000-0002-7658-3690Akahane Manabu5https://orcid.org/0000-0003-4184-2151Tanaka Yasuhito6https://orcid.org/0000-0002-2300-611XMavrogenis Andreas F.7https://orcid.org/0000-0003-0807-0719Errani Costantino8https://orcid.org/0000-0002-4504-2867Kawai Akira9Department of Orthopaedic Surgery, Nara Medical UniversityDepartment of Orthopaedic Surgery, Nara Medical UniversityDepartment of Orthopaedic Surgery, Nara Medical UniversityDepartment of Orthopaedic Surgery, Nara Medical UniversityDepartment of Rehabilitation Medicine, Nara Medical UniversityDepartment of Health and Welfare Services, National Institute of Public HealthDepartment of Orthopaedic Surgery, Nara Medical UniversityFirst Department of Orthopaedics, National and Kapodistrian University of Athens, School of MedicineDepartment of Orthopaedic Oncology, IRCCS Istituto Ortopedico RizzoliDivision of Musculoskeletal Oncology, National Cancer Center HospitalIntroduction: Dedifferentiated chondrosarcoma (DDCS) is a high-grade subtype of chondrosarcoma with a poor prognosis. Treatment for localized DDCS generally involves wide resection; the effectiveness of adjuvant radiotherapy and chemotherapy is questionable. This research was designed to find prognostic factors for DDCS and evaluate the impact of adjuvant therapies on localized cases. Methods: One hundred thirty-two patients with DDCS diagnosed by pathology in the period 2006 to 2022 were identified in the Japanese National Bone and Soft Tissue Tumor Registry database and were retrospectively analyzed. Results: Patients with distant metastases at diagnosis (n = 34) had significantly poorer survival than those without metastases (n = 98), with a 5-year disease-specific survival (DSS) of 9.7% vs. 37.1% (P < 0.0001). For patients without distant metastasis at diagnosis, uni- and multivariate analysis showed that R1 or R2 surgical margin was an independent risk factor linked with unfavorable local recurrence (hazard ratio [HR] 3.39 [95% CI: 1.35–8.52]; P = 0.010). Adjuvant radiotherapy was not associated with local recurrence (HR 2.41 [95% CI: 0.87–6.64]; P = 0.090). Larger size (HR 1.13 [95% CI: 1.06–1.19]; P < 0.001) and no surgery (HR 3.87 [95% CI: 1.61–9.28]; P = 0.002) were independent risk factors for unfavorable DSS. Previous surgery (HR 0.19 [95% CI: 0.04–0.84]; P = 0.028) and adjuvant chemotherapy (HR 0.36 [95% CI: 0.16–0.77]; P = 0.009) were independent risk factors for favorable DSS. Discussion: Survival may have been improved by chemotherapy, but the effect of adjuvant radiotherapy in controlling the local spread of the tumor appears to have been limited in DDCS cases that were localized.https://www.sicot-j.org/articles/sicotj/full_html/2025/01/sicotj250012/sicotj250012.htmldedifferentiated chondrosarcomaadjuvantchemotherapysurgeryradiotherapy
spellingShingle Masunaga Tomoya
Tsukamoto Shinji
Honoki Kanya
Fujii Hiromasa
Kido Akira
Akahane Manabu
Tanaka Yasuhito
Mavrogenis Andreas F.
Errani Costantino
Kawai Akira
Predicting survival outcomes in dedifferentiated chondrosarcoma: a prognostic factor analysis from a National Registry
SICOT-J
dedifferentiated chondrosarcoma
adjuvant
chemotherapy
surgery
radiotherapy
title Predicting survival outcomes in dedifferentiated chondrosarcoma: a prognostic factor analysis from a National Registry
title_full Predicting survival outcomes in dedifferentiated chondrosarcoma: a prognostic factor analysis from a National Registry
title_fullStr Predicting survival outcomes in dedifferentiated chondrosarcoma: a prognostic factor analysis from a National Registry
title_full_unstemmed Predicting survival outcomes in dedifferentiated chondrosarcoma: a prognostic factor analysis from a National Registry
title_short Predicting survival outcomes in dedifferentiated chondrosarcoma: a prognostic factor analysis from a National Registry
title_sort predicting survival outcomes in dedifferentiated chondrosarcoma a prognostic factor analysis from a national registry
topic dedifferentiated chondrosarcoma
adjuvant
chemotherapy
surgery
radiotherapy
url https://www.sicot-j.org/articles/sicotj/full_html/2025/01/sicotj250012/sicotj250012.html
work_keys_str_mv AT masunagatomoya predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT tsukamotoshinji predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT honokikanya predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT fujiihiromasa predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT kidoakira predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT akahanemanabu predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT tanakayasuhito predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT mavrogenisandreasf predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT erranicostantino predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry
AT kawaiakira predictingsurvivaloutcomesindedifferentiatedchondrosarcomaaprognosticfactoranalysisfromanationalregistry