Sharing Diagnostic and Therapeutic Pathways in Pulmonary Arterial Hypertension: A Roadmap for the Triveneto Region
Background: Pulmonary arterial hypertension (PAH) is a rare and progressive disease characterized by high mortality and a significant impact on quality of life. Despite therapeutic advances, considerable heterogeneity persists in Italy’s diagnostic and therapeutic pathways, leading to delays in dia...
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2025-05-01
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| author | Davide Stolfo Nicoletta Bellini Edoardo Bonsante Giacomo Cavalli Emma Di Poi Mauro Driussi Giulia Famoso Irene Ferrari Pietro Geri Martina Perazzolo Marra Claudio Picariello Francesca Tedoldi Elisa Tinazzi Elisabetta Zanatta Daniele Prati |
| author_facet | Davide Stolfo Nicoletta Bellini Edoardo Bonsante Giacomo Cavalli Emma Di Poi Mauro Driussi Giulia Famoso Irene Ferrari Pietro Geri Martina Perazzolo Marra Claudio Picariello Francesca Tedoldi Elisa Tinazzi Elisabetta Zanatta Daniele Prati |
| author_sort | Davide Stolfo |
| collection | DOAJ |
| description |
Background: Pulmonary arterial hypertension (PAH) is a rare and progressive disease characterized by high mortality and a significant impact on quality of life. Despite therapeutic advances, considerable heterogeneity persists in Italy’s diagnostic and therapeutic pathways, leading to delays in diagnosis and disparities in access to care.
Objective: With this work we aim to define a roadmap for a shared diagnostic, therapeutic, and care pathway for
PAH in the Triveneto region, aiming to reduce management variability, improve continuity of care, and optimize
the use of available resources.
Methods: A multidisciplinary group of cardiologists, pulmonologists, and rheumatologists from Triveneto, along
with a representative from the Pulmonary Hypertension Patients’ Association, convened in a series of meetings
to discuss diagnostic and therapeutic pathways.
Results: Early identification of PAH should be based on the classification of symptomatic patients into three main
phenotypes (cardiac, pulmonary, and not better specified), followed by a specific diagnostic process based on
updated hemodynamic criteria.
Therapeutic strategies should be defined according to risk stratification, with clear guidelines for comorbidity
management and monitoring through quality indicators (Key Performance Indicators) to assess the effectiveness
of care pathways.
Conclusions: The proposed roadmap represents a shared model for PAH management in the Triveneto region,
promoting a multidisciplinary and integrated approach. Its adoption could enhance care quality, reduce regional
disparities, and align with European guidelines, ultimately improving patient prognosis and quality of life.
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| format | Article |
| id | doaj-art-48bd248dc2f14ef5b008d1c023d68570 |
| institution | DOAJ |
| issn | 2465-2628 |
| language | English |
| publishDate | 2025-05-01 |
| publisher | AboutScience Srl |
| record_format | Article |
| series | AboutOpen |
| spelling | doaj-art-48bd248dc2f14ef5b008d1c023d685702025-08-20T03:07:27ZengAboutScience SrlAboutOpen2465-26282025-05-0112110.33393/ao.2025.3443Sharing Diagnostic and Therapeutic Pathways in Pulmonary Arterial Hypertension: A Roadmap for the Triveneto RegionDavide Stolfo0Nicoletta Bellini1Edoardo Bonsante2Giacomo Cavalli3Emma Di Poi4Mauro Driussi5Giulia Famoso6Irene Ferrari7Pietro Geri8Martina Perazzolo Marra9Claudio Picariello10Francesca Tedoldi11Elisa Tinazzi12Elisabetta Zanatta13Daniele Prati14Cardiothoracovascular Department, Azienda Sanitaria Universitaria Giuliano Isontina, Università di Trieste, Trieste - ItalyUOC Cardiologia, ULSS 8 Berica, Ospedale San Bortolo, Vicenza - ItalyUOC Cardiologia, Ospedale Centrale di Bolzano, Bolzano - ItalyUOC Cardiologia, USSL 3, Mestre - ItalyClinica Reumatologica, Dipartimento di Medicina e Scienze Biologiche, Azienda Sanitaria Universitaria Friuli Centrale (ASUFC), Udine - ItalySOC Cardiologia, Dipartimento Cardiotoracico, Azienda Sanitaria Universitaria Friuli Centrale, Ospedale S. Maria della Misericordia, Udine - ItalyDipartimento di Scienze Cardiache, Toraciche e Vascolari e di Sanità Pubblica, Ospedale Universitario di Padova, Padova - ItalyAzienda Ospedaliera Universitaria Integrata Verona, Verona - ItalyPneumologia, Dipartimento di Scienze Medico-Chirurgiche e della Salute, Ospedale di Cattinara, Università di Trieste, Trieste - ItalyDipartimento di Scienze Cardiache, Toraciche e Vascolari e di Sanità Pubblica, Ospedale Universitario di Padova, Padova - ItalyUOC Cardiologia, ULSS 5 Polesana, Ospedale Santa Maria della Misericordia, Rovigo - ItalyDipartimento di Cardiologia, Ospedale S. Chiara, Trento - ItalyDipartimento di Medicina, Università di Verona, Verona - ItalyDipartimento di Scienze Cardiache, Toraciche e Vascolari e di Sanità Pubblica, Ospedale Universitario di Padova, Padova - Italy and Unità di Reumatologia, Dipartimento di Medicina-DIMED, Ospedale Universitario di Padova, Padova - ItalyAzienda Ospedaliera Universitaria Integrata Verona, Verona - Italy Background: Pulmonary arterial hypertension (PAH) is a rare and progressive disease characterized by high mortality and a significant impact on quality of life. Despite therapeutic advances, considerable heterogeneity persists in Italy’s diagnostic and therapeutic pathways, leading to delays in diagnosis and disparities in access to care. Objective: With this work we aim to define a roadmap for a shared diagnostic, therapeutic, and care pathway for PAH in the Triveneto region, aiming to reduce management variability, improve continuity of care, and optimize the use of available resources. Methods: A multidisciplinary group of cardiologists, pulmonologists, and rheumatologists from Triveneto, along with a representative from the Pulmonary Hypertension Patients’ Association, convened in a series of meetings to discuss diagnostic and therapeutic pathways. Results: Early identification of PAH should be based on the classification of symptomatic patients into three main phenotypes (cardiac, pulmonary, and not better specified), followed by a specific diagnostic process based on updated hemodynamic criteria. Therapeutic strategies should be defined according to risk stratification, with clear guidelines for comorbidity management and monitoring through quality indicators (Key Performance Indicators) to assess the effectiveness of care pathways. Conclusions: The proposed roadmap represents a shared model for PAH management in the Triveneto region, promoting a multidisciplinary and integrated approach. Its adoption could enhance care quality, reduce regional disparities, and align with European guidelines, ultimately improving patient prognosis and quality of life. https://journals.aboutscience.eu/index.php/aboutopen/article/view/3443CardiologyDiagnostic and therapeutic pathwayPneumologyPulmonary arterial hypertension (PAH)Quality of life |
| spellingShingle | Davide Stolfo Nicoletta Bellini Edoardo Bonsante Giacomo Cavalli Emma Di Poi Mauro Driussi Giulia Famoso Irene Ferrari Pietro Geri Martina Perazzolo Marra Claudio Picariello Francesca Tedoldi Elisa Tinazzi Elisabetta Zanatta Daniele Prati Sharing Diagnostic and Therapeutic Pathways in Pulmonary Arterial Hypertension: A Roadmap for the Triveneto Region AboutOpen Cardiology Diagnostic and therapeutic pathway Pneumology Pulmonary arterial hypertension (PAH) Quality of life |
| title | Sharing Diagnostic and Therapeutic Pathways in Pulmonary Arterial Hypertension: A Roadmap for the Triveneto Region |
| title_full | Sharing Diagnostic and Therapeutic Pathways in Pulmonary Arterial Hypertension: A Roadmap for the Triveneto Region |
| title_fullStr | Sharing Diagnostic and Therapeutic Pathways in Pulmonary Arterial Hypertension: A Roadmap for the Triveneto Region |
| title_full_unstemmed | Sharing Diagnostic and Therapeutic Pathways in Pulmonary Arterial Hypertension: A Roadmap for the Triveneto Region |
| title_short | Sharing Diagnostic and Therapeutic Pathways in Pulmonary Arterial Hypertension: A Roadmap for the Triveneto Region |
| title_sort | sharing diagnostic and therapeutic pathways in pulmonary arterial hypertension a roadmap for the triveneto region |
| topic | Cardiology Diagnostic and therapeutic pathway Pneumology Pulmonary arterial hypertension (PAH) Quality of life |
| url | https://journals.aboutscience.eu/index.php/aboutopen/article/view/3443 |
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