Audiological findings in Brown Vialetto-Van-Laere Syndrome: A scoping review

Audiological findings in Brown Vialetto-Van-Laere Syndrome: A scoping review

Objective: This study aimed to characterize audiological porfile in inviduals with Brown-Vialetto-Van Laere syndrome (BVVLS). Methods: This is a scoping review following the methodological structure developed by the Joana Briggs Institute (JBI). The PCC mnemonic was used to elaborate the research qu...

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Main Authors: Débora de Oliveira Rolim, Leticia Cristina Vicente, Hugo Amilton Santos de Carvalho, Rebeca Lorrane Santana Santos, Rivadávio Fernandes Batista de Amorim, Fayez Bahmad, Jr
Format: Article
Language:English
Published: Elsevier 2025-05-01
Series:Brazilian Journal of Otorhinolaryngology
Subjects:
Progressive bulbar palsy with sensorineural deafness
BrownVialetto-Van Laere Syndrome
Audiometries
Audition
Online Access:http://www.sciencedirect.com/science/article/pii/S1808869425000011
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Summary:Objective: This study aimed to characterize audiological porfile in inviduals with Brown-Vialetto-Van Laere syndrome (BVVLS). Methods: This is a scoping review following the methodological structure developed by the Joana Briggs Institute (JBI). The PCC mnemonic was used to elaborate the research question, which resulted in the research question: “What are the audiological findings in individuals with BVVLS?”. Results: All of the studies included in this review were case reports. The main audiological findings are sensorineural hearing loss and Auditory Neuropathy Spectrum Disorder (ANSD). Conclusion: All individuals presented a severe to profound bilateral hearing loss, related to ANSD.
ISSN:1808-8694

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