Trends in Life Expectancy of Cystic Fibrosis Patients in Moscow and their Connection with the Treatment Received: Retrospective Analysis for 1993–2013

Cystic fibrosis is multiple organ pathology that requires a complex treatment. Its standardization and pharmacoeconomic analysis are absolutely necessary. We performed a retrospective analysis of the trends in life expectancy of cystic fibrosis patients who lived inMoscow in 1993, 1998, 2003, 2008,...

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Main Authors: N. Yu. Kashirskaya, S. A. Krasovsky, A. V. Chernyak, V. D. Sherman, A. Yu. Voronkova, L. A. Shabalova, V. S. Nikonova, Yu. V. Gorinova, O. I. Simonova, E. L. Amelina, E. I. Kondrat’eva, N. I. Kapranov, N. V. Petrova, R. A. Zinchenko
Format: Article
Language:English
Published: "Paediatrician" Publishers LLC 2015-09-01
Series:Вопросы современной педиатрии
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Online Access:https://vsp.spr-journal.ru/jour/article/view/1083
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author N. Yu. Kashirskaya
S. A. Krasovsky
A. V. Chernyak
V. D. Sherman
A. Yu. Voronkova
L. A. Shabalova
V. S. Nikonova
Yu. V. Gorinova
O. I. Simonova
E. L. Amelina
E. I. Kondrat’eva
N. I. Kapranov
N. V. Petrova
R. A. Zinchenko
author_facet N. Yu. Kashirskaya
S. A. Krasovsky
A. V. Chernyak
V. D. Sherman
A. Yu. Voronkova
L. A. Shabalova
V. S. Nikonova
Yu. V. Gorinova
O. I. Simonova
E. L. Amelina
E. I. Kondrat’eva
N. I. Kapranov
N. V. Petrova
R. A. Zinchenko
author_sort N. Yu. Kashirskaya
collection DOAJ
description Cystic fibrosis is multiple organ pathology that requires a complex treatment. Its standardization and pharmacoeconomic analysis are absolutely necessary. We performed a retrospective analysis of the trends in life expectancy of cystic fibrosis patients who lived inMoscow in 1993, 1998, 2003, 2008, and 2013. It was found that the survival rate of these patients depended on the choice of drug therapy (pancreatic enzymes, dornase alfa, intravenous and inhaled antipseudomonal antibiotics), changes in diet, active dispensary observation at a specialized center for cystic fibrosis, and neonatal screening. We determined the cost of drug therapy per patient. From 1993 to 2013, the survival rate of patients who lived in Moscow increased by more than 20 years (from 16 to 39 years, respectively). The average cost of therapy increased more than 10 times (from USD 1.8 to 21.9 thousand, respectively).
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publishDate 2015-09-01
publisher "Paediatrician" Publishers LLC
record_format Article
series Вопросы современной педиатрии
spelling doaj-art-469ac005c5ab44a3b76219cbd0d47e2f2025-08-20T03:59:52Zeng"Paediatrician" Publishers LLCВопросы современной педиатрии1682-55271682-55352015-09-0114450350810.15690/vsp.v14.i4.13901084Trends in Life Expectancy of Cystic Fibrosis Patients in Moscow and their Connection with the Treatment Received: Retrospective Analysis for 1993–2013N. Yu. Kashirskaya0S. A. Krasovsky1A. V. Chernyak2V. D. Sherman3A. Yu. Voronkova4L. A. Shabalova5V. S. Nikonova6Yu. V. Gorinova7O. I. Simonova8E. L. Amelina9E. I. Kondrat’eva10N. I. Kapranov11N. V. Petrova12R. A. Zinchenko13Research Centre of Medical Genetics, Moscow, Russian FederationResearch Institute of Pulmonology, Moscow, Russian FederationResearch Institute of Pulmonology, Moscow, Russian FederationResearch Centre of Medical Genetics, Moscow, Russian FederationResearch Centre of Medical Genetics, Moscow, Russian FederationResearch Centre of Medical Genetics, Moscow, Russian FederationResearch Centre of Medical Genetics, Moscow, Russian FederationScientific Center of Children’s Health, Moscow, Russian FederationScientific Center of Children’s Health, Moscow, Russian FederationResearch Institute of Pulmonology, Moscow, Russian FederationResearch Centre of Medical Genetics, Moscow, Russian FederationResearch Centre of Medical Genetics, Moscow, Russian FederationResearch Centre of Medical Genetics, Moscow, Russian FederationResearch Centre of Medical Genetics, Moscow, Russian Federation Moscow State University of Medicine and Dentistry n.a. A.I. Evdokimov, Moscow, Russian FederationCystic fibrosis is multiple organ pathology that requires a complex treatment. Its standardization and pharmacoeconomic analysis are absolutely necessary. We performed a retrospective analysis of the trends in life expectancy of cystic fibrosis patients who lived inMoscow in 1993, 1998, 2003, 2008, and 2013. It was found that the survival rate of these patients depended on the choice of drug therapy (pancreatic enzymes, dornase alfa, intravenous and inhaled antipseudomonal antibiotics), changes in diet, active dispensary observation at a specialized center for cystic fibrosis, and neonatal screening. We determined the cost of drug therapy per patient. From 1993 to 2013, the survival rate of patients who lived in Moscow increased by more than 20 years (from 16 to 39 years, respectively). The average cost of therapy increased more than 10 times (from USD 1.8 to 21.9 thousand, respectively).https://vsp.spr-journal.ru/jour/article/view/1083cystic fibrosissurvival ratetreatmentcostdornase alfa.
spellingShingle N. Yu. Kashirskaya
S. A. Krasovsky
A. V. Chernyak
V. D. Sherman
A. Yu. Voronkova
L. A. Shabalova
V. S. Nikonova
Yu. V. Gorinova
O. I. Simonova
E. L. Amelina
E. I. Kondrat’eva
N. I. Kapranov
N. V. Petrova
R. A. Zinchenko
Trends in Life Expectancy of Cystic Fibrosis Patients in Moscow and their Connection with the Treatment Received: Retrospective Analysis for 1993–2013
Вопросы современной педиатрии
cystic fibrosis
survival rate
treatment
cost
dornase alfa.
title Trends in Life Expectancy of Cystic Fibrosis Patients in Moscow and their Connection with the Treatment Received: Retrospective Analysis for 1993–2013
title_full Trends in Life Expectancy of Cystic Fibrosis Patients in Moscow and their Connection with the Treatment Received: Retrospective Analysis for 1993–2013
title_fullStr Trends in Life Expectancy of Cystic Fibrosis Patients in Moscow and their Connection with the Treatment Received: Retrospective Analysis for 1993–2013
title_full_unstemmed Trends in Life Expectancy of Cystic Fibrosis Patients in Moscow and their Connection with the Treatment Received: Retrospective Analysis for 1993–2013
title_short Trends in Life Expectancy of Cystic Fibrosis Patients in Moscow and their Connection with the Treatment Received: Retrospective Analysis for 1993–2013
title_sort trends in life expectancy of cystic fibrosis patients in moscow and their connection with the treatment received retrospective analysis for 1993 2013
topic cystic fibrosis
survival rate
treatment
cost
dornase alfa.
url https://vsp.spr-journal.ru/jour/article/view/1083
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