Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT

Fibromuscular Dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disorder predominantly affecting women aged 18 to 65 years. This case report highlights a 74-year-old female diagnosed with FMD incidentally during evaluation for deep vein thrombosis (DVT). Imaging revealed significant...

Full description

Saved in:
Bibliographic Details
Main Authors: Abderrahmane Ibenyahia, MD, Oumaima Elkaddouri, MD, Mounir Salek, MD, Salma Boustani, MD, Soufiane Bigi, MD, Said Adnor, MD, Wassila Bouissar, MD, Soukaina Wakrim, MD
Format: Article
Language:English
Published: Elsevier 2025-03-01
Series:Radiology Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S1930043324013803
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1832595749224841216
author Abderrahmane Ibenyahia, MD
Oumaima Elkaddouri, MD
Mounir Salek, MD
Salma Boustani, MD
Soufiane Bigi, MD
Said Adnor, MD
Wassila Bouissar, MD
Soukaina Wakrim, MD
author_facet Abderrahmane Ibenyahia, MD
Oumaima Elkaddouri, MD
Mounir Salek, MD
Salma Boustani, MD
Soufiane Bigi, MD
Said Adnor, MD
Wassila Bouissar, MD
Soukaina Wakrim, MD
author_sort Abderrahmane Ibenyahia, MD
collection DOAJ
description Fibromuscular Dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disorder predominantly affecting women aged 18 to 65 years. This case report highlights a 74-year-old female diagnosed with FMD incidentally during evaluation for deep vein thrombosis (DVT). Imaging revealed significant vascular anomalies, including a giant intracranial carotid aneurysm and a hypoplastic iliac vein with extensive collateral formation. Early detection and tailored management are crucial to prevent complications such as arterial dissections, aneurysms, and stroke. The patient showed favorable evolution without anticoagulation therapy, and interventional embolization was planned to mitigate rupture risks. Differential diagnosis includes atherosclerotic aneurysms, Ehlers-Danlos syndrome, Marfan syndrome, neurofibromatosis type 1, and polyarteritis nodosa, which must be distinguished through comprehensive imaging and clinical evaluation. The prognosis of FMD varies widely and depends on the extent and location of arterial involvement. This case underscores the importance of advanced imaging in accurately diagnosing and guiding long-term follow-up for FMD management.
format Article
id doaj-art-45ce22f7251f4eb093f4c26074ef74cb
institution Kabale University
issn 1930-0433
language English
publishDate 2025-03-01
publisher Elsevier
record_format Article
series Radiology Case Reports
spelling doaj-art-45ce22f7251f4eb093f4c26074ef74cb2025-01-18T05:04:07ZengElsevierRadiology Case Reports1930-04332025-03-0120316311636Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVTAbderrahmane Ibenyahia, MD0Oumaima Elkaddouri, MD1Mounir Salek, MD2Salma Boustani, MD3Soufiane Bigi, MD4Said Adnor, MD5Wassila Bouissar, MD6Soukaina Wakrim, MD7Radiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, Morocco; Corresponding author.Department of Internal Medicine, Faculty of Medicine and Pharmacy of Agadir, University Ibn Zohr, Agadir, MoroccoRadiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, MoroccoDepartment of Internal Medicine, Faculty of Medicine and Pharmacy of Agadir, University Ibn Zohr, Agadir, MoroccoRadiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, MoroccoRadiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, MoroccoDepartment of Internal Medicine, Faculty of Medicine and Pharmacy of Agadir, University Ibn Zohr, Agadir, MoroccoRadiology Department, University Hospital Center of Souss Massa, Faculty of Medicine and Pharmacy, Ibn Zohr Agadir University, Agadir, MoroccoFibromuscular Dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disorder predominantly affecting women aged 18 to 65 years. This case report highlights a 74-year-old female diagnosed with FMD incidentally during evaluation for deep vein thrombosis (DVT). Imaging revealed significant vascular anomalies, including a giant intracranial carotid aneurysm and a hypoplastic iliac vein with extensive collateral formation. Early detection and tailored management are crucial to prevent complications such as arterial dissections, aneurysms, and stroke. The patient showed favorable evolution without anticoagulation therapy, and interventional embolization was planned to mitigate rupture risks. Differential diagnosis includes atherosclerotic aneurysms, Ehlers-Danlos syndrome, Marfan syndrome, neurofibromatosis type 1, and polyarteritis nodosa, which must be distinguished through comprehensive imaging and clinical evaluation. The prognosis of FMD varies widely and depends on the extent and location of arterial involvement. This case underscores the importance of advanced imaging in accurately diagnosing and guiding long-term follow-up for FMD management.http://www.sciencedirect.com/science/article/pii/S1930043324013803Fibromuscular dysplasiaFMDGiant carotid aneurysmBuds pearl signHypoplastic iliac veinBone island
spellingShingle Abderrahmane Ibenyahia, MD
Oumaima Elkaddouri, MD
Mounir Salek, MD
Salma Boustani, MD
Soufiane Bigi, MD
Said Adnor, MD
Wassila Bouissar, MD
Soukaina Wakrim, MD
Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT
Radiology Case Reports
Fibromuscular dysplasia
FMD
Giant carotid aneurysm
Buds pearl sign
Hypoplastic iliac vein
Bone island
title Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT
title_full Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT
title_fullStr Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT
title_full_unstemmed Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT
title_short Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT
title_sort radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected dvt
topic Fibromuscular dysplasia
FMD
Giant carotid aneurysm
Buds pearl sign
Hypoplastic iliac vein
Bone island
url http://www.sciencedirect.com/science/article/pii/S1930043324013803
work_keys_str_mv AT abderrahmaneibenyahiamd radiologicalinsightsintofibromusculardysplasiaunveiledbyintracranialaneurysmsandiliacveinhypoplasiainsuspecteddvt
AT oumaimaelkaddourimd radiologicalinsightsintofibromusculardysplasiaunveiledbyintracranialaneurysmsandiliacveinhypoplasiainsuspecteddvt
AT mounirsalekmd radiologicalinsightsintofibromusculardysplasiaunveiledbyintracranialaneurysmsandiliacveinhypoplasiainsuspecteddvt
AT salmaboustanimd radiologicalinsightsintofibromusculardysplasiaunveiledbyintracranialaneurysmsandiliacveinhypoplasiainsuspecteddvt
AT soufianebigimd radiologicalinsightsintofibromusculardysplasiaunveiledbyintracranialaneurysmsandiliacveinhypoplasiainsuspecteddvt
AT saidadnormd radiologicalinsightsintofibromusculardysplasiaunveiledbyintracranialaneurysmsandiliacveinhypoplasiainsuspecteddvt
AT wassilabouissarmd radiologicalinsightsintofibromusculardysplasiaunveiledbyintracranialaneurysmsandiliacveinhypoplasiainsuspecteddvt
AT soukainawakrimmd radiologicalinsightsintofibromusculardysplasiaunveiledbyintracranialaneurysmsandiliacveinhypoplasiainsuspecteddvt