Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report

Solid pseudopapillary tumors (SPTs) of the pancreas are rare tumors with low potential for malignancy, uncertain lineage, and favorable prognosis in most cases. The SPT has an excellent prognosis, and the standard treatment is surgical resection. The agenesis of the dorsal pancreas (ADP) is an extre...

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Main Authors: Daniel Paulino Santana, Diogo Viana Abreu, Edmilson Celso Santos, Bruno de Lima Rodrigues, Anna Carolina D’Ascenção Maia, Marcos Campos Wanderley Reis
Format: Article
Language:English
Published: Thieme Revinter Publicações Ltda. 2021-10-01
Series:Brazilian Journal of Oncology
Subjects:
Online Access:http://www.brazilianjournalofoncology.com.br/details/178/en-US/solid-pseudopapillary-tumor-associated-with-agenesis-of-the-dorsal-pancreas--a-case-report
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author Daniel Paulino Santana
Diogo Viana Abreu
Edmilson Celso Santos
Bruno de Lima Rodrigues
Anna Carolina D’Ascenção Maia
Marcos Campos Wanderley Reis
author_facet Daniel Paulino Santana
Diogo Viana Abreu
Edmilson Celso Santos
Bruno de Lima Rodrigues
Anna Carolina D’Ascenção Maia
Marcos Campos Wanderley Reis
author_sort Daniel Paulino Santana
collection DOAJ
description Solid pseudopapillary tumors (SPTs) of the pancreas are rare tumors with low potential for malignancy, uncertain lineage, and favorable prognosis in most cases. The SPT has an excellent prognosis, and the standard treatment is surgical resection. The agenesis of the dorsal pancreas (ADP) is an extremely rare type of congenital pancreatic malformation and is characterized by partial or total loss of the body and tail of the gland. Its association with SPT has been reported only in two studies. We report a case of SPT associated with total ADP. A 36-year-old woman was diagnosed with a complex mass on pancreatic head topography, measuring 7.8×5.5cm, associated with complete agenesis of the body and tail of the pancreas. She underwent gastropancreatoduodenectomy with a successful postoperative outcome. The anatomopathological examination suggested an SPT and it was confirmed by immunohistochemistry.
format Article
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institution Kabale University
issn 2526-8732
language English
publishDate 2021-10-01
publisher Thieme Revinter Publicações Ltda.
record_format Article
series Brazilian Journal of Oncology
spelling doaj-art-44feb30a7a9a46a9a82e628f460fe70a2025-08-20T03:36:44ZengThieme Revinter Publicações Ltda.Brazilian Journal of Oncology2526-87322021-10-01170010.5935/2526-8732.20210031Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case reportDaniel Paulino Santana0Diogo Viana Abreu1Edmilson Celso Santos2Bruno de Lima Rodrigues3Anna Carolina D’Ascenção Maia4Marcos Campos Wanderley Reis5Hospital Integrado do Câncer - Rede Mater Dei de Saúde, Surgical Oncology - Belo Horizonte - MG - BrazilFundação Benjamim Guimarães - Hospital da Baleia, General Surgery - Belo Horizonte - MG - BrazilHospital Integrado do Câncer - Rede Mater Dei de Saúde, Surgical Oncology - Belo Horizonte - MG - BrazilHospital Integrado do Câncer - Rede Mater Dei de Saúde, Surgical Oncology - Belo Horizonte - MG - BrazilHospital Integrado do Câncer - Rede Mater Dei de Saúde, Clinical Oncology - Belo Horizonte - MG - BrazilHospital Integrado do Câncer - Rede Mater Dei de Saúde, Surgical Oncology - Belo Horizonte - MG - BrazilSolid pseudopapillary tumors (SPTs) of the pancreas are rare tumors with low potential for malignancy, uncertain lineage, and favorable prognosis in most cases. The SPT has an excellent prognosis, and the standard treatment is surgical resection. The agenesis of the dorsal pancreas (ADP) is an extremely rare type of congenital pancreatic malformation and is characterized by partial or total loss of the body and tail of the gland. Its association with SPT has been reported only in two studies. We report a case of SPT associated with total ADP. A 36-year-old woman was diagnosed with a complex mass on pancreatic head topography, measuring 7.8×5.5cm, associated with complete agenesis of the body and tail of the pancreas. She underwent gastropancreatoduodenectomy with a successful postoperative outcome. The anatomopathological examination suggested an SPT and it was confirmed by immunohistochemistry.http://www.brazilianjournalofoncology.com.br/details/178/en-US/solid-pseudopapillary-tumor-associated-with-agenesis-of-the-dorsal-pancreas--a-case-reportpancreatic neoplasmspancreatic cancerpancreatectomypancreasagenesis
spellingShingle Daniel Paulino Santana
Diogo Viana Abreu
Edmilson Celso Santos
Bruno de Lima Rodrigues
Anna Carolina D’Ascenção Maia
Marcos Campos Wanderley Reis
Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report
Brazilian Journal of Oncology
pancreatic neoplasms
pancreatic cancer
pancreatectomy
pancreas
agenesis
title Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report
title_full Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report
title_fullStr Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report
title_full_unstemmed Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report
title_short Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report
title_sort solid pseudopapillary tumor associated with agenesis of the dorsal pancreas a case report
topic pancreatic neoplasms
pancreatic cancer
pancreatectomy
pancreas
agenesis
url http://www.brazilianjournalofoncology.com.br/details/178/en-US/solid-pseudopapillary-tumor-associated-with-agenesis-of-the-dorsal-pancreas--a-case-report
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