Atypical presentation of primary Ewing's sarcoma
Ewing's sarcoma is the second most common bone tumor in children and adolescents. Its annual incidence is 0.6/million total population worldwide, and in some populations in India, its incidence can account for 15%–19.4% of the primary bone tumors. Ewing's sarcoma is a highly malignant roun...
Saved in:
| Main Authors: | , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Thieme Medical and Scientific Publishers Pvt. Ltd.
2018-01-01
|
| Series: | Indian Journal of Medical and Paediatric Oncology |
| Subjects: | |
| Online Access: | http://www.ijmpo.org/article.asp?issn=0971-5851;year=2018;volume=39;issue=3;spage=398;epage=399;aulast=Jeniffer |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| _version_ | 1849728035063857152 |
|---|---|
| author | Nancy V Jeniffer Arpitha Panduranga B P Karunakara |
| author_facet | Nancy V Jeniffer Arpitha Panduranga B P Karunakara |
| author_sort | Nancy V Jeniffer |
| collection | DOAJ |
| description | Ewing's sarcoma is the second most common bone tumor in children and adolescents. Its annual incidence is 0.6/million total population worldwide, and in some populations in India, its incidence can account for 15%–19.4% of the primary bone tumors. Ewing's sarcoma is a highly malignant round cell tumor, affecting the metadiaphyseal and the diaphyseal regions of the long bones. Spine involvement, as a primary focus in Ewings sarcoma is uncommon, but when present, usually affects the sacrum. Origin from non sacral region is extremely rare. We report a case of acute onset of paraplegia progressing to quadriplegia in a child with metastatic involvement of the spine, primary focus being the nonsacral spine which is inherently challenging to an early diagnosis. Ewing's sarcoma though has improved survival with chemotherapy and radiotherapy, primary spine focus has poor prognosis. |
| format | Article |
| id | doaj-art-44da3672dfa648b39aced455a2f28dcf |
| institution | DOAJ |
| issn | 0971-5851 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Thieme Medical and Scientific Publishers Pvt. Ltd. |
| record_format | Article |
| series | Indian Journal of Medical and Paediatric Oncology |
| spelling | doaj-art-44da3672dfa648b39aced455a2f28dcf2025-08-20T03:09:41ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Medical and Paediatric Oncology0971-58512018-01-0139339839910.4103/ijmpo.ijmpo_71_17Atypical presentation of primary Ewing's sarcomaNancy V JenifferArpitha PandurangaB P KarunakaraEwing's sarcoma is the second most common bone tumor in children and adolescents. Its annual incidence is 0.6/million total population worldwide, and in some populations in India, its incidence can account for 15%–19.4% of the primary bone tumors. Ewing's sarcoma is a highly malignant round cell tumor, affecting the metadiaphyseal and the diaphyseal regions of the long bones. Spine involvement, as a primary focus in Ewings sarcoma is uncommon, but when present, usually affects the sacrum. Origin from non sacral region is extremely rare. We report a case of acute onset of paraplegia progressing to quadriplegia in a child with metastatic involvement of the spine, primary focus being the nonsacral spine which is inherently challenging to an early diagnosis. Ewing's sarcoma though has improved survival with chemotherapy and radiotherapy, primary spine focus has poor prognosis.http://www.ijmpo.org/article.asp?issn=0971-5851;year=2018;volume=39;issue=3;spage=398;epage=399;aulast=JenifferAcute onset paraplegiacord compressionEwing's sarcomamalignant bone tumors of childhoodspine involvement |
| spellingShingle | Nancy V Jeniffer Arpitha Panduranga B P Karunakara Atypical presentation of primary Ewing's sarcoma Indian Journal of Medical and Paediatric Oncology Acute onset paraplegia cord compression Ewing's sarcoma malignant bone tumors of childhood spine involvement |
| title | Atypical presentation of primary Ewing's sarcoma |
| title_full | Atypical presentation of primary Ewing's sarcoma |
| title_fullStr | Atypical presentation of primary Ewing's sarcoma |
| title_full_unstemmed | Atypical presentation of primary Ewing's sarcoma |
| title_short | Atypical presentation of primary Ewing's sarcoma |
| title_sort | atypical presentation of primary ewing s sarcoma |
| topic | Acute onset paraplegia cord compression Ewing's sarcoma malignant bone tumors of childhood spine involvement |
| url | http://www.ijmpo.org/article.asp?issn=0971-5851;year=2018;volume=39;issue=3;spage=398;epage=399;aulast=Jeniffer |
| work_keys_str_mv | AT nancyvjeniffer atypicalpresentationofprimaryewingssarcoma AT arpithapanduranga atypicalpresentationofprimaryewingssarcoma AT bpkarunakara atypicalpresentationofprimaryewingssarcoma |