Diabetic Striatopathy: A Rare Case Report of Chorea, Hyperglycemia, Basal Ganglia (C-H-BG) Syndrome

Chorea-hyperglycemia-basal ganglia syndrome is a rare complication of hyperglycemia and unilateral hemichorea-hemiballismus syndrome. Synonyms include diabetic striatopathy and non-ketotic hyperglycemic hemichorea. This occurs in 90% of individuals of Asian descent, particularly female patients with...

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Bibliographic Details
Main Authors: Ifeoma Kwentoh, Phone Win, Fnu Allah Yar, Sabeena Shaikh, Tasheka McPherson, Terrence Henry, Leszek Pisinski, Raji Ayinla
Format: Article
Language:English
Published: American College of Physicians 2024-05-01
Series:Annals of Internal Medicine: Clinical Cases
Online Access:https://www.acpjournals.org/doi/10.7326/aimcc.2023.1342
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Summary:Chorea-hyperglycemia-basal ganglia syndrome is a rare complication of hyperglycemia and unilateral hemichorea-hemiballismus syndrome. Synonyms include diabetic striatopathy and non-ketotic hyperglycemic hemichorea. This occurs in 90% of individuals of Asian descent, particularly female patients with type 2 diabetes. Diagnosis is made when the mean serum glucose level is 481.5 mg/dL, HbA1c level 14.4%, and serum osmolarity of 305.9 mmol/kg. It is managed with antipsychotic drugs and insulin. We report an 80-year-old man with diabetes who presented with disabling unintentional movements of his left extremities affecting his quality of life. Computed tomography and magnetic resonance imaging of the head demonstrated findings of diabetic striatopathy. Risperidone and glycemic control resolved the chorea like-movements.
ISSN:2767-7664