First-line therapy with daratumumab, lenalidomide and dexamethasone for patient with POEMS syndrome: A case report

POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M–protein, skin changes syndrome) is a rare condition due to an underlying plasma cell neoplasm whose clinical presentation can be various so it could lead to delayed diagnosis and treatment. The pathogenesis of the syndrome is not well u...

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Main Authors: E. Amabile, F. Fazio, M. Martelli, MT. Petrucci
Format: Article
Language:English
Published: Elsevier 2024-01-01
Series:Leukemia Research Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2213048924000815
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author E. Amabile
F. Fazio
M. Martelli
MT. Petrucci
author_facet E. Amabile
F. Fazio
M. Martelli
MT. Petrucci
author_sort E. Amabile
collection DOAJ
description POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M–protein, skin changes syndrome) is a rare condition due to an underlying plasma cell neoplasm whose clinical presentation can be various so it could lead to delayed diagnosis and treatment. The pathogenesis of the syndrome is not well understood, and its therapy is adapted from other plasma cell disorders with the aim of alleviating symptoms, decreasing end-organ damage, improving quality of life and prolonging overall survival. We report a case of a 71 years-old woman who has been treated with continuous DRd (daratumumab, lenalidomide and dexamethasone) scheme.
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publishDate 2024-01-01
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series Leukemia Research Reports
spelling doaj-art-42deabaece1d482a9d30c5112dfa0be52025-08-20T02:36:03ZengElsevierLeukemia Research Reports2213-04892024-01-012210049110.1016/j.lrr.2024.100491First-line therapy with daratumumab, lenalidomide and dexamethasone for patient with POEMS syndrome: A case reportE. Amabile0F. Fazio1M. Martelli2MT. Petrucci3Corresponding author.; Hematology, Department of Translational and Precision Medicine, Sapienza University of Rome, Azienda Policlinico Umberto I, Rome, ItalyHematology, Department of Translational and Precision Medicine, Sapienza University of Rome, Azienda Policlinico Umberto I, Rome, ItalyHematology, Department of Translational and Precision Medicine, Sapienza University of Rome, Azienda Policlinico Umberto I, Rome, ItalyHematology, Department of Translational and Precision Medicine, Sapienza University of Rome, Azienda Policlinico Umberto I, Rome, ItalyPOEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M–protein, skin changes syndrome) is a rare condition due to an underlying plasma cell neoplasm whose clinical presentation can be various so it could lead to delayed diagnosis and treatment. The pathogenesis of the syndrome is not well understood, and its therapy is adapted from other plasma cell disorders with the aim of alleviating symptoms, decreasing end-organ damage, improving quality of life and prolonging overall survival. We report a case of a 71 years-old woman who has been treated with continuous DRd (daratumumab, lenalidomide and dexamethasone) scheme.http://www.sciencedirect.com/science/article/pii/S2213048924000815POEMSPlasma cell disorderVEGF
spellingShingle E. Amabile
F. Fazio
M. Martelli
MT. Petrucci
First-line therapy with daratumumab, lenalidomide and dexamethasone for patient with POEMS syndrome: A case report
Leukemia Research Reports
POEMS
Plasma cell disorder
VEGF
title First-line therapy with daratumumab, lenalidomide and dexamethasone for patient with POEMS syndrome: A case report
title_full First-line therapy with daratumumab, lenalidomide and dexamethasone for patient with POEMS syndrome: A case report
title_fullStr First-line therapy with daratumumab, lenalidomide and dexamethasone for patient with POEMS syndrome: A case report
title_full_unstemmed First-line therapy with daratumumab, lenalidomide and dexamethasone for patient with POEMS syndrome: A case report
title_short First-line therapy with daratumumab, lenalidomide and dexamethasone for patient with POEMS syndrome: A case report
title_sort first line therapy with daratumumab lenalidomide and dexamethasone for patient with poems syndrome a case report
topic POEMS
Plasma cell disorder
VEGF
url http://www.sciencedirect.com/science/article/pii/S2213048924000815
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