Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological Implications
Congenital middle ear malformations are rare. Most part of them are usually associated with other malformations, such as aural atresia, microtia, and dysmorphic craniofacial features. A clinical case of a 24-year-old male with a right-sided conductive hearing loss since his childhood, without cranio...
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| Format: | Article |
| Language: | English |
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Wiley
2016-01-01
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| Series: | Case Reports in Otolaryngology |
| Online Access: | http://dx.doi.org/10.1155/2016/2598962 |
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| author | Vânia Henriques Rafaela Teles Ana Sousa Roberto Estevão Jorge Rodrigues Alexandra Gomes Francisco Silva Ângelo Fernandes Fausto Fernandes |
| author_facet | Vânia Henriques Rafaela Teles Ana Sousa Roberto Estevão Jorge Rodrigues Alexandra Gomes Francisco Silva Ângelo Fernandes Fausto Fernandes |
| author_sort | Vânia Henriques |
| collection | DOAJ |
| description | Congenital middle ear malformations are rare. Most part of them are usually associated with other malformations, such as aural atresia, microtia, and dysmorphic craniofacial features. A clinical case of a 24-year-old male with a right-sided conductive hearing loss since his childhood, without craniofacial malformation, is presented. He was proposed for exploratory tympanotomy under the suspicious diagnosis of otosclerosis. The surgery revealed an abnormal location of stapes’ superstructure, which was attached to the promontory and had an isolated and mobile osseous footplate in the oval window. A stapes prosthesis was inserted and resulted in closure of the air-bone gap by 25 dB. A review of the literature was also performed using MEDLINE. Two theories diverge on the embryologic origin of the stapes. Our findings seem to be in favour of the theory that defines two different embryologic origins to the stapes. |
| format | Article |
| id | doaj-art-40c7839d2e274fb082af44137a500e77 |
| institution | Kabale University |
| issn | 2090-6765 2090-6773 |
| language | English |
| publishDate | 2016-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Otolaryngology |
| spelling | doaj-art-40c7839d2e274fb082af44137a500e772025-02-03T07:25:09ZengWileyCase Reports in Otolaryngology2090-67652090-67732016-01-01201610.1155/2016/25989622598962Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological ImplicationsVânia Henriques0Rafaela Teles1Ana Sousa2Roberto Estevão3Jorge Rodrigues4Alexandra Gomes5Francisco Silva6Ângelo Fernandes7Fausto Fernandes8Otorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalOtorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalOtorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalOtorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalOtorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalOtorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalOtorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalOtorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalOtorhinolaryngology Department, Hospital de Guimarães, Rua dos Cutileiros, 4835-044 Guimarães, PortugalCongenital middle ear malformations are rare. Most part of them are usually associated with other malformations, such as aural atresia, microtia, and dysmorphic craniofacial features. A clinical case of a 24-year-old male with a right-sided conductive hearing loss since his childhood, without craniofacial malformation, is presented. He was proposed for exploratory tympanotomy under the suspicious diagnosis of otosclerosis. The surgery revealed an abnormal location of stapes’ superstructure, which was attached to the promontory and had an isolated and mobile osseous footplate in the oval window. A stapes prosthesis was inserted and resulted in closure of the air-bone gap by 25 dB. A review of the literature was also performed using MEDLINE. Two theories diverge on the embryologic origin of the stapes. Our findings seem to be in favour of the theory that defines two different embryologic origins to the stapes.http://dx.doi.org/10.1155/2016/2598962 |
| spellingShingle | Vânia Henriques Rafaela Teles Ana Sousa Roberto Estevão Jorge Rodrigues Alexandra Gomes Francisco Silva Ângelo Fernandes Fausto Fernandes Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological Implications Case Reports in Otolaryngology |
| title | Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological Implications |
| title_full | Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological Implications |
| title_fullStr | Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological Implications |
| title_full_unstemmed | Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological Implications |
| title_short | Abnormal Congenital Location of Stapes’ Superstructure: Clinical and Embryological Implications |
| title_sort | abnormal congenital location of stapes superstructure clinical and embryological implications |
| url | http://dx.doi.org/10.1155/2016/2598962 |
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