Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the Literature
The Perivascular Epithelioid Cell tumours (PEComas) are rare mesenchymal neoplasms recognized as entity by the World Health Organization. The tumour cells have an uncertain origin and are characterized by distinctive histological and immunohistochemical features. We report a case of PEComa occurring...
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| Format: | Article |
| Language: | English |
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Wiley
2016-01-01
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| Series: | Case Reports in Pathology |
| Online Access: | http://dx.doi.org/10.1155/2016/1936421 |
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| author | Idania Lubo Ileana Fermín Olindo Massarelli Roberta Gobbi Paolo Cossu Rocca |
| author_facet | Idania Lubo Ileana Fermín Olindo Massarelli Roberta Gobbi Paolo Cossu Rocca |
| author_sort | Idania Lubo |
| collection | DOAJ |
| description | The Perivascular Epithelioid Cell tumours (PEComas) are rare mesenchymal neoplasms recognized as entity by the World Health Organization. The tumour cells have an uncertain origin and are characterized by distinctive histological and immunohistochemical features. We report a case of PEComa occurring as intraorbital lesion in a 47-year-old man. We found only two other cases described in the literature and we considered all three cases together in order of histology, immunohistochemistry, and clinical outcome. We found a strict histological overlapping and quite similar immunohistological results. All three cases showed a favourable clinical course probably related to small size of tumours (<5 cm), low mitotic rate (<2 mitoses in 50 HPF), and absence of necrosis. |
| format | Article |
| id | doaj-art-402ec06170c54bcaa8fdffa6928f8a96 |
| institution | DOAJ |
| issn | 2090-6781 2090-679X |
| language | English |
| publishDate | 2016-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pathology |
| spelling | doaj-art-402ec06170c54bcaa8fdffa6928f8a962025-08-20T02:39:15ZengWileyCase Reports in Pathology2090-67812090-679X2016-01-01201610.1155/2016/19364211936421Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the LiteratureIdania Lubo0Ileana Fermín1Olindo Massarelli2Roberta Gobbi3Paolo Cossu Rocca4Anatomy and Pathology Institute “Dr. José Antonio O’Daly”, Central University of Venezuela, Los Chaguaramos 1040, Caracas, VenezuelaAnatomy and Pathology Institute “Dr. José Antonio O’Daly”, Central University of Venezuela, Los Chaguaramos 1040, Caracas, VenezuelaMaxillofacial Surgery Unit, University of Sassari, ItalyMaxillofacial Surgery Unit, University of Sassari, ItalyDepartment of Histopathology and Anatomical Pathology, University of Sassari, ItalyThe Perivascular Epithelioid Cell tumours (PEComas) are rare mesenchymal neoplasms recognized as entity by the World Health Organization. The tumour cells have an uncertain origin and are characterized by distinctive histological and immunohistochemical features. We report a case of PEComa occurring as intraorbital lesion in a 47-year-old man. We found only two other cases described in the literature and we considered all three cases together in order of histology, immunohistochemistry, and clinical outcome. We found a strict histological overlapping and quite similar immunohistological results. All three cases showed a favourable clinical course probably related to small size of tumours (<5 cm), low mitotic rate (<2 mitoses in 50 HPF), and absence of necrosis.http://dx.doi.org/10.1155/2016/1936421 |
| spellingShingle | Idania Lubo Ileana Fermín Olindo Massarelli Roberta Gobbi Paolo Cossu Rocca Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the Literature Case Reports in Pathology |
| title | Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the Literature |
| title_full | Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the Literature |
| title_fullStr | Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the Literature |
| title_full_unstemmed | Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the Literature |
| title_short | Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the Literature |
| title_sort | perivascular epithelioid cell tumour with intraorbital location report of a case and review of the literature |
| url | http://dx.doi.org/10.1155/2016/1936421 |
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