SPATS2L is a positive feedback regulator of the type I interferon signaling pathway and plays a vital role in lupus

Through genome-wide association studies (GWAS) and integrated expression quantitative trait locus (eQTL) analyses, numerous susceptibility genes (“eGenes”, whose expressions are significantly associated with common variants) associated with systemic lupus erythematosus (SLE) have been identified. No...

Full description

Saved in:
Bibliographic Details
Main Authors: Chen Mengke, Zhang Yutong, Shi Weiwen, Song Xuejiao, Yang Yue, Hou Guojun, Ding Huihua, Chen Sheng, Yang Wanling, Shen Nan, Cui Yong, Zuo Xianbo, Tang Yuanjia
Format: Article
Language:English
Published: China Science Publishing & Media Ltd. 2024-08-01
Series:Acta Biochimica et Biophysica Sinica
Subjects:
Online Access:https://www.sciengine.com/doi/10.3724/abbs.2024132
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849733584067231744
author Chen Mengke
Zhang Yutong
Shi Weiwen
Song Xuejiao
Yang Yue
Hou Guojun
Ding Huihua
Chen Sheng
Yang Wanling
Shen Nan
Cui Yong
Zuo Xianbo
Tang Yuanjia
author_facet Chen Mengke
Zhang Yutong
Shi Weiwen
Song Xuejiao
Yang Yue
Hou Guojun
Ding Huihua
Chen Sheng
Yang Wanling
Shen Nan
Cui Yong
Zuo Xianbo
Tang Yuanjia
author_sort Chen Mengke
collection DOAJ
description Through genome-wide association studies (GWAS) and integrated expression quantitative trait locus (eQTL) analyses, numerous susceptibility genes (“eGenes”, whose expressions are significantly associated with common variants) associated with systemic lupus erythematosus (SLE) have been identified. Notably, a subset of these eGenes is correlated with disease activity. However, the precise mechanisms through which these genes contribute to the initiation and progression of the disease remain to be fully elucidated. In this investigation, we initially identify SPATS2L as an SLE eGene correlated with disease activity. eSignaling and transcriptomic analyses suggest its involvement in the type I interferon (IFN) pathway. We observe a significant increase in SPATS2L expression following type I IFN stimulation, and the expression levels are dependent on both the concentration and duration of stimulation. Furthermore, through dual-luciferase reporter assays, western blot analysis, and imaging flow cytometry, we confirm that SPATS2L positively modulates the type I IFN pathway, acting as a positive feedback regulator. Notably, siRNA-mediated intervention targeting SPATS2L, an interferon-inducible gene, in peripheral blood mononuclear cells (PBMCs) from patients with SLE reverses the activation of the interferon pathway. In conclusion, our research highlights the pivotal role of SPATS2L as a positive-feedback regulatory molecule within the type I IFN pathway. Our findings suggest that SPATS2L plays a critical role in the onset and progression of SLE and may serve as a promising target for disease activity assessment and intervention strategies.
format Article
id doaj-art-402003b49c064160aebaa145a314e194
institution DOAJ
issn 1672-9145
language English
publishDate 2024-08-01
publisher China Science Publishing & Media Ltd.
record_format Article
series Acta Biochimica et Biophysica Sinica
spelling doaj-art-402003b49c064160aebaa145a314e1942025-08-20T03:08:00ZengChina Science Publishing & Media Ltd.Acta Biochimica et Biophysica Sinica1672-91452024-08-01561659167210.3724/abbs.202413220d259ccSPATS2L is a positive feedback regulator of the type I interferon signaling pathway and plays a vital role in lupusChen Mengke0Zhang Yutong1Shi Weiwen2Song Xuejiao3Yang Yue4Hou Guojun5Ding Huihua6Chen Sheng7Yang Wanling8Shen Nan9Cui Yong10Zuo Xianbo11Tang Yuanjia12["Shanghai Institute of Rheumatology, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200001, China"]["Shanghai Institute of Rheumatology, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200001, China"]["Shanghai Institute of Rheumatology, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200001, China"]["Department of Dermatology, China-Japan Friendship Hospital, Beijing 100029, China"]["Department of Dermatology, China-Japan Friendship Hospital, Beijing 100029, China","Department of Pharmacy, China-Japan Friendship Hospital, Beijing 100029, China"]["Shanghai Institute of Rheumatology, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200001, China"]["Shanghai Institute of Rheumatology, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200001, China"]["Shanghai Institute of Rheumatology, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200001, China"]["of Paediatrics and Adolescent Medicine, The University of Hong Kong, Hong Kong 999077, China"]["Shanghai Institute of Rheumatology, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200001, China","State Key Laboratory of Oncogenes and Related Genes, Shanghai Cancer Institute, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200032, China","Center for Autoimmune Genomics and Etiology, Cincinnati Children’s Hospital Medical Center, Cincinnati OH 45229, USA","Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati OH 45229, USA"]["Department of Dermatology, China-Japan Friendship Hospital, Beijing 100029, China"]["Department of Dermatology, China-Japan Friendship Hospital, Beijing 100029, China","Department of Pharmacy, China-Japan Friendship Hospital, Beijing 100029, China"]["Shanghai Institute of Rheumatology, Renji Hospital, Shanghai Jiao Tong University School of Medicine (SJTUSM), Shanghai 200001, China"]Through genome-wide association studies (GWAS) and integrated expression quantitative trait locus (eQTL) analyses, numerous susceptibility genes (“eGenes”, whose expressions are significantly associated with common variants) associated with systemic lupus erythematosus (SLE) have been identified. Notably, a subset of these eGenes is correlated with disease activity. However, the precise mechanisms through which these genes contribute to the initiation and progression of the disease remain to be fully elucidated. In this investigation, we initially identify SPATS2L as an SLE eGene correlated with disease activity. eSignaling and transcriptomic analyses suggest its involvement in the type I interferon (IFN) pathway. We observe a significant increase in SPATS2L expression following type I IFN stimulation, and the expression levels are dependent on both the concentration and duration of stimulation. Furthermore, through dual-luciferase reporter assays, western blot analysis, and imaging flow cytometry, we confirm that SPATS2L positively modulates the type I IFN pathway, acting as a positive feedback regulator. Notably, siRNA-mediated intervention targeting SPATS2L, an interferon-inducible gene, in peripheral blood mononuclear cells (PBMCs) from patients with SLE reverses the activation of the interferon pathway. In conclusion, our research highlights the pivotal role of SPATS2L as a positive-feedback regulatory molecule within the type I IFN pathway. Our findings suggest that SPATS2L plays a critical role in the onset and progression of SLE and may serve as a promising target for disease activity assessment and intervention strategies.https://www.sciengine.com/doi/10.3724/abbs.2024132systemic lupus erythematosusSPATS2Lquantitative trait locitype I interferon
spellingShingle Chen Mengke
Zhang Yutong
Shi Weiwen
Song Xuejiao
Yang Yue
Hou Guojun
Ding Huihua
Chen Sheng
Yang Wanling
Shen Nan
Cui Yong
Zuo Xianbo
Tang Yuanjia
SPATS2L is a positive feedback regulator of the type I interferon signaling pathway and plays a vital role in lupus
Acta Biochimica et Biophysica Sinica
systemic lupus erythematosus
SPATS2L
quantitative trait loci
type I interferon
title SPATS2L is a positive feedback regulator of the type I interferon signaling pathway and plays a vital role in lupus
title_full SPATS2L is a positive feedback regulator of the type I interferon signaling pathway and plays a vital role in lupus
title_fullStr SPATS2L is a positive feedback regulator of the type I interferon signaling pathway and plays a vital role in lupus
title_full_unstemmed SPATS2L is a positive feedback regulator of the type I interferon signaling pathway and plays a vital role in lupus
title_short SPATS2L is a positive feedback regulator of the type I interferon signaling pathway and plays a vital role in lupus
title_sort spats2l is a positive feedback regulator of the type i interferon signaling pathway and plays a vital role in lupus
topic systemic lupus erythematosus
SPATS2L
quantitative trait loci
type I interferon
url https://www.sciengine.com/doi/10.3724/abbs.2024132
work_keys_str_mv AT chenmengke spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT zhangyutong spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT shiweiwen spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT songxuejiao spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT yangyue spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT houguojun spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT dinghuihua spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT chensheng spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT yangwanling spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT shennan spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT cuiyong spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT zuoxianbo spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus
AT tangyuanjia spats2lisapositivefeedbackregulatorofthetypeiinterferonsignalingpathwayandplaysavitalroleinlupus