A Case of Sirenomelia Associated with Hypoplastic Left Heart with a Healthy Co-Twin: A Rare Entity
Sirenomelia is a rare developmental malformation and is incompatible to life. The incidence of sirenomelia, as recorded in the literature, is estimated to be approximately between 1.5 and 4.2 per 1,00,000 births. Around 15% of sirenomelia cases are associated with twin pregnancy, most often in monoz...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Pediatrics |
| Online Access: | http://dx.doi.org/10.1155/2018/9361745 |
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| author | Houda Nasser Al Yaqoubi Muna Mubarak Al Badi Farida Mohsin Ambu Saidi Nasser Shaikhan Taaeeb Al Shafouri |
| author_facet | Houda Nasser Al Yaqoubi Muna Mubarak Al Badi Farida Mohsin Ambu Saidi Nasser Shaikhan Taaeeb Al Shafouri |
| author_sort | Houda Nasser Al Yaqoubi |
| collection | DOAJ |
| description | Sirenomelia is a rare developmental malformation and is incompatible to life. The incidence of sirenomelia, as recorded in the literature, is estimated to be approximately between 1.5 and 4.2 per 1,00,000 births. Around 15% of sirenomelia cases are associated with twin pregnancy, most often in monozygotic cases with an incidence of 7%. In monozygotic twins, the risk of sirenomelia is nearly 100–150 times higher as compared to dizygotic twins or singleton pregnancies. Until now, only two cases of sirenomelia associated with hypoplastic left heart have been reported in the literature. Here, we present a monozygotic twin pregnancy, where one fetus was diagnosed with sirenomelia associated with hypoplastic left heart syndrome and the co-twin was absolutely healthy. |
| format | Article |
| id | doaj-art-3dd6a711263d44e98471fcdc5d445212 |
| institution | Kabale University |
| issn | 2090-6803 2090-6811 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Pediatrics |
| spelling | doaj-art-3dd6a711263d44e98471fcdc5d4452122025-02-03T01:09:50ZengWileyCase Reports in Pediatrics2090-68032090-68112018-01-01201810.1155/2018/93617459361745A Case of Sirenomelia Associated with Hypoplastic Left Heart with a Healthy Co-Twin: A Rare EntityHouda Nasser Al Yaqoubi0Muna Mubarak Al Badi1Farida Mohsin Ambu Saidi2Nasser Shaikhan Taaeeb Al Shafouri3Department of Obstetrics and Gynaecology, Ministry of Health, Ibri Regional Hospital, Ibri, OmanDepartment of Obstetrics and Gynaecology, Ministry of Health, Ibri Regional Hospital, Ibri, OmanDepartment of Obstetrics and Gynaecology, Ministry of Health, Ibri Regional Hospital, Ibri, OmanDepartment of Obstetrics and Gynaecology, Ministry of Health, Ibri Regional Hospital, Ibri, OmanSirenomelia is a rare developmental malformation and is incompatible to life. The incidence of sirenomelia, as recorded in the literature, is estimated to be approximately between 1.5 and 4.2 per 1,00,000 births. Around 15% of sirenomelia cases are associated with twin pregnancy, most often in monozygotic cases with an incidence of 7%. In monozygotic twins, the risk of sirenomelia is nearly 100–150 times higher as compared to dizygotic twins or singleton pregnancies. Until now, only two cases of sirenomelia associated with hypoplastic left heart have been reported in the literature. Here, we present a monozygotic twin pregnancy, where one fetus was diagnosed with sirenomelia associated with hypoplastic left heart syndrome and the co-twin was absolutely healthy.http://dx.doi.org/10.1155/2018/9361745 |
| spellingShingle | Houda Nasser Al Yaqoubi Muna Mubarak Al Badi Farida Mohsin Ambu Saidi Nasser Shaikhan Taaeeb Al Shafouri A Case of Sirenomelia Associated with Hypoplastic Left Heart with a Healthy Co-Twin: A Rare Entity Case Reports in Pediatrics |
| title | A Case of Sirenomelia Associated with Hypoplastic Left Heart with a Healthy Co-Twin: A Rare Entity |
| title_full | A Case of Sirenomelia Associated with Hypoplastic Left Heart with a Healthy Co-Twin: A Rare Entity |
| title_fullStr | A Case of Sirenomelia Associated with Hypoplastic Left Heart with a Healthy Co-Twin: A Rare Entity |
| title_full_unstemmed | A Case of Sirenomelia Associated with Hypoplastic Left Heart with a Healthy Co-Twin: A Rare Entity |
| title_short | A Case of Sirenomelia Associated with Hypoplastic Left Heart with a Healthy Co-Twin: A Rare Entity |
| title_sort | case of sirenomelia associated with hypoplastic left heart with a healthy co twin a rare entity |
| url | http://dx.doi.org/10.1155/2018/9361745 |
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