Mixed Acinar-Endocrine Carcinoma (MAEC) Arising in Duodenal Pancreatic Heterotopia

Mixed acinar-endocrine carcinoma (MAEC) of the pancreas is a rare neoplasm, consisting of at least 25%–30% of acinar and neuroendocrine populations. Patients are often middle-aged and present with nonspecific symptoms. Imaging typically reveals a solid lesion in the pancreatic head. Management invol...

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Main Authors: Phoenix D. Bell, Tom C. DeRoche, Aaron R. Huber
Format: Article
Language:English
Published: Wiley 2019-01-01
Series:Case Reports in Pathology
Online Access:http://dx.doi.org/10.1155/2019/1713546
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author Phoenix D. Bell
Tom C. DeRoche
Aaron R. Huber
author_facet Phoenix D. Bell
Tom C. DeRoche
Aaron R. Huber
author_sort Phoenix D. Bell
collection DOAJ
description Mixed acinar-endocrine carcinoma (MAEC) of the pancreas is a rare neoplasm, consisting of at least 25%–30% of acinar and neuroendocrine populations. Patients are often middle-aged and present with nonspecific symptoms. Imaging typically reveals a solid lesion in the pancreatic head. Management involves surgical resection and the overall prognosis is variable. Here, we present a case of a 48-year-old male who presented with a MAEC arising from duodenal pancreatic heterotopia. This is the one of the first cases, with histologic evidence, of MAEC arising from pancreatic heterotopia.
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institution Kabale University
issn 2090-6781
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language English
publishDate 2019-01-01
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series Case Reports in Pathology
spelling doaj-art-3c8b8f481bab445dab1187ad2084624d2025-02-03T05:50:41ZengWileyCase Reports in Pathology2090-67812090-679X2019-01-01201910.1155/2019/17135461713546Mixed Acinar-Endocrine Carcinoma (MAEC) Arising in Duodenal Pancreatic HeterotopiaPhoenix D. Bell0Tom C. DeRoche1Aaron R. Huber2Department of Pathology, University of Rochester Medical Center, Rochester, NY, USADepartment of Pathology, Kaiser Permanente, Portland, OR, USADepartment of Pathology, University of Rochester Medical Center, Rochester, NY, USAMixed acinar-endocrine carcinoma (MAEC) of the pancreas is a rare neoplasm, consisting of at least 25%–30% of acinar and neuroendocrine populations. Patients are often middle-aged and present with nonspecific symptoms. Imaging typically reveals a solid lesion in the pancreatic head. Management involves surgical resection and the overall prognosis is variable. Here, we present a case of a 48-year-old male who presented with a MAEC arising from duodenal pancreatic heterotopia. This is the one of the first cases, with histologic evidence, of MAEC arising from pancreatic heterotopia.http://dx.doi.org/10.1155/2019/1713546
spellingShingle Phoenix D. Bell
Tom C. DeRoche
Aaron R. Huber
Mixed Acinar-Endocrine Carcinoma (MAEC) Arising in Duodenal Pancreatic Heterotopia
Case Reports in Pathology
title Mixed Acinar-Endocrine Carcinoma (MAEC) Arising in Duodenal Pancreatic Heterotopia
title_full Mixed Acinar-Endocrine Carcinoma (MAEC) Arising in Duodenal Pancreatic Heterotopia
title_fullStr Mixed Acinar-Endocrine Carcinoma (MAEC) Arising in Duodenal Pancreatic Heterotopia
title_full_unstemmed Mixed Acinar-Endocrine Carcinoma (MAEC) Arising in Duodenal Pancreatic Heterotopia
title_short Mixed Acinar-Endocrine Carcinoma (MAEC) Arising in Duodenal Pancreatic Heterotopia
title_sort mixed acinar endocrine carcinoma maec arising in duodenal pancreatic heterotopia
url http://dx.doi.org/10.1155/2019/1713546
work_keys_str_mv AT phoenixdbell mixedacinarendocrinecarcinomamaecarisinginduodenalpancreaticheterotopia
AT tomcderoche mixedacinarendocrinecarcinomamaecarisinginduodenalpancreaticheterotopia
AT aaronrhuber mixedacinarendocrinecarcinomamaecarisinginduodenalpancreaticheterotopia