Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment Pattern

In patients with atypical hemolytic uremic syndrome (aHUS), complement blocking by eculizumab rapidly halts the process of thrombotic microangiopathy and it is associated with clear long-term hematologic and renal improvements. Eculizumab treatment consists of a 4-week initial phase with weekly IV a...

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Main Authors: Camino García Monteavaro, Carmen Peralta Roselló, Borja Quiroga, José María Baltar Martín, Lorena Castillo Eraso, Fernando de Álvaro Moreno, Alberto Martínez Vea, María Teresa Visus-Fernández de Manzanos
Format: Article
Language:English
Published: Wiley 2016-01-01
Series:Case Reports in Nephrology
Online Access:http://dx.doi.org/10.1155/2016/7471082
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author Camino García Monteavaro
Carmen Peralta Roselló
Borja Quiroga
José María Baltar Martín
Lorena Castillo Eraso
Fernando de Álvaro Moreno
Alberto Martínez Vea
María Teresa Visus-Fernández de Manzanos
author_facet Camino García Monteavaro
Carmen Peralta Roselló
Borja Quiroga
José María Baltar Martín
Lorena Castillo Eraso
Fernando de Álvaro Moreno
Alberto Martínez Vea
María Teresa Visus-Fernández de Manzanos
author_sort Camino García Monteavaro
collection DOAJ
description In patients with atypical hemolytic uremic syndrome (aHUS), complement blocking by eculizumab rapidly halts the process of thrombotic microangiopathy and it is associated with clear long-term hematologic and renal improvements. Eculizumab treatment consists of a 4-week initial phase with weekly IV administration of 900 mg doses, followed by a maintenance phase with a 1,200 mg dose in the fifth week and every 14±2 days thereafter. We present three patients with aHUS and suboptimal response to eculizumab treatment at the usual administration dosage who showed hematologic and renal improvements after an adjustment in the eculizumab treatment protocol.
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publishDate 2016-01-01
publisher Wiley
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series Case Reports in Nephrology
spelling doaj-art-3b2397d942df41aeb1de76a37f08fadf2025-08-20T02:08:03ZengWileyCase Reports in Nephrology2090-66412090-665X2016-01-01201610.1155/2016/74710827471082Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment PatternCamino García Monteavaro0Carmen Peralta Roselló1Borja Quiroga2José María Baltar Martín3Lorena Castillo Eraso4Fernando de Álvaro Moreno5Alberto Martínez Vea6María Teresa Visus-Fernández de Manzanos7Nephrology Service, Hospital San Agustín, Camino de Heros 6, 33401 Avilés, SpainNephrology Service, Hospital Universitari Joan XXIII, C/Dr. Mallafrè Guasch 4, 43005 Tarragona, SpainNephrology Service, Hospital Universitario de Guadalajara, C/Donante de Sangre s/n, 19002 Guadalajara, SpainNephrology Service, Hospital San Agustín, Camino de Heros 6, 33401 Avilés, SpainNephrology Service, Hospital Universitari Joan XXIII, C/Dr. Mallafrè Guasch 4, 43005 Tarragona, SpainNephrology Service, Hospitales Madrid, Pl. del Conde del Valle de Súchil 16, 28015 Madrid, SpainNephrology Service, Hospital Universitari Joan XXIII, C/Dr. Mallafrè Guasch 4, 43005 Tarragona, SpainNephrology Service, Hospital San Agustín, Camino de Heros 6, 33401 Avilés, SpainIn patients with atypical hemolytic uremic syndrome (aHUS), complement blocking by eculizumab rapidly halts the process of thrombotic microangiopathy and it is associated with clear long-term hematologic and renal improvements. Eculizumab treatment consists of a 4-week initial phase with weekly IV administration of 900 mg doses, followed by a maintenance phase with a 1,200 mg dose in the fifth week and every 14±2 days thereafter. We present three patients with aHUS and suboptimal response to eculizumab treatment at the usual administration dosage who showed hematologic and renal improvements after an adjustment in the eculizumab treatment protocol.http://dx.doi.org/10.1155/2016/7471082
spellingShingle Camino García Monteavaro
Carmen Peralta Roselló
Borja Quiroga
José María Baltar Martín
Lorena Castillo Eraso
Fernando de Álvaro Moreno
Alberto Martínez Vea
María Teresa Visus-Fernández de Manzanos
Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment Pattern
Case Reports in Nephrology
title Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment Pattern
title_full Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment Pattern
title_fullStr Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment Pattern
title_full_unstemmed Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment Pattern
title_short Adjustment of Eculizumab Dosage Pattern in Patients with Atypical Hemolytic Uremic Syndrome with Suboptimal Response to Standard Treatment Pattern
title_sort adjustment of eculizumab dosage pattern in patients with atypical hemolytic uremic syndrome with suboptimal response to standard treatment pattern
url http://dx.doi.org/10.1155/2016/7471082
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