AMPK-dependent and -independent coordination of mitochondrial function and muscle fiber type by FNIP1.

Mitochondria are essential for maintaining skeletal muscle metabolic homeostasis during adaptive response to a myriad of physiologic or pathophysiological stresses. The mechanisms by which mitochondrial function and contractile fiber type are concordantly regulated to ensure muscle function remain p...

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Main Authors: Liwei Xiao, Jing Liu, Zongchao Sun, Yujing Yin, Yan Mao, Dengqiu Xu, Lin Liu, Zhisheng Xu, Qiqi Guo, Chenyun Ding, Wanping Sun, Likun Yang, Zheng Zhou, Danxia Zhou, Tingting Fu, Wenjing Zhou, Yuangang Zhu, Xiao-Wei Chen, John Zhong Li, Shuai Chen, Xiaoduo Xie, Zhenji Gan
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2021-03-01
Series:PLoS Genetics
Online Access:https://journals.plos.org/plosgenetics/article/file?id=10.1371/journal.pgen.1009488&type=printable
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author Liwei Xiao
Jing Liu
Zongchao Sun
Yujing Yin
Yan Mao
Dengqiu Xu
Lin Liu
Zhisheng Xu
Qiqi Guo
Chenyun Ding
Wanping Sun
Likun Yang
Zheng Zhou
Danxia Zhou
Tingting Fu
Wenjing Zhou
Yuangang Zhu
Xiao-Wei Chen
John Zhong Li
Shuai Chen
Xiaoduo Xie
Zhenji Gan
author_facet Liwei Xiao
Jing Liu
Zongchao Sun
Yujing Yin
Yan Mao
Dengqiu Xu
Lin Liu
Zhisheng Xu
Qiqi Guo
Chenyun Ding
Wanping Sun
Likun Yang
Zheng Zhou
Danxia Zhou
Tingting Fu
Wenjing Zhou
Yuangang Zhu
Xiao-Wei Chen
John Zhong Li
Shuai Chen
Xiaoduo Xie
Zhenji Gan
author_sort Liwei Xiao
collection DOAJ
description Mitochondria are essential for maintaining skeletal muscle metabolic homeostasis during adaptive response to a myriad of physiologic or pathophysiological stresses. The mechanisms by which mitochondrial function and contractile fiber type are concordantly regulated to ensure muscle function remain poorly understood. Evidence is emerging that the Folliculin interacting protein 1 (Fnip1) is involved in skeletal muscle fiber type specification, function, and disease. In this study, Fnip1 was specifically expressed in skeletal muscle in Fnip1-transgenic (Fnip1Tg) mice. Fnip1Tg mice were crossed with Fnip1-knockout (Fnip1KO) mice to generate Fnip1TgKO mice expressing Fnip1 only in skeletal muscle but not in other tissues. Our results indicate that, in addition to the known role in type I fiber program, FNIP1 exerts control upon muscle mitochondrial oxidative program through AMPK signaling. Indeed, basal levels of FNIP1 are sufficient to inhibit AMPK but not mTORC1 activity in skeletal muscle cells. Gain-of-function and loss-of-function strategies in mice, together with assessment of primary muscle cells, demonstrated that skeletal muscle mitochondrial program is suppressed via the inhibitory actions of FNIP1 on AMPK. Surprisingly, the FNIP1 actions on type I fiber program is independent of AMPK and its downstream PGC-1α. These studies provide a vital framework for understanding the intrinsic role of FNIP1 as a crucial factor in the concerted regulation of mitochondrial function and muscle fiber type that determine muscle fitness.
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publisher Public Library of Science (PLoS)
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spelling doaj-art-3b1a00c5bdac44c2a91bbf246ff541a32025-08-20T02:01:04ZengPublic Library of Science (PLoS)PLoS Genetics1553-73901553-74042021-03-01173e100948810.1371/journal.pgen.1009488AMPK-dependent and -independent coordination of mitochondrial function and muscle fiber type by FNIP1.Liwei XiaoJing LiuZongchao SunYujing YinYan MaoDengqiu XuLin LiuZhisheng XuQiqi GuoChenyun DingWanping SunLikun YangZheng ZhouDanxia ZhouTingting FuWenjing ZhouYuangang ZhuXiao-Wei ChenJohn Zhong LiShuai ChenXiaoduo XieZhenji GanMitochondria are essential for maintaining skeletal muscle metabolic homeostasis during adaptive response to a myriad of physiologic or pathophysiological stresses. The mechanisms by which mitochondrial function and contractile fiber type are concordantly regulated to ensure muscle function remain poorly understood. Evidence is emerging that the Folliculin interacting protein 1 (Fnip1) is involved in skeletal muscle fiber type specification, function, and disease. In this study, Fnip1 was specifically expressed in skeletal muscle in Fnip1-transgenic (Fnip1Tg) mice. Fnip1Tg mice were crossed with Fnip1-knockout (Fnip1KO) mice to generate Fnip1TgKO mice expressing Fnip1 only in skeletal muscle but not in other tissues. Our results indicate that, in addition to the known role in type I fiber program, FNIP1 exerts control upon muscle mitochondrial oxidative program through AMPK signaling. Indeed, basal levels of FNIP1 are sufficient to inhibit AMPK but not mTORC1 activity in skeletal muscle cells. Gain-of-function and loss-of-function strategies in mice, together with assessment of primary muscle cells, demonstrated that skeletal muscle mitochondrial program is suppressed via the inhibitory actions of FNIP1 on AMPK. Surprisingly, the FNIP1 actions on type I fiber program is independent of AMPK and its downstream PGC-1α. These studies provide a vital framework for understanding the intrinsic role of FNIP1 as a crucial factor in the concerted regulation of mitochondrial function and muscle fiber type that determine muscle fitness.https://journals.plos.org/plosgenetics/article/file?id=10.1371/journal.pgen.1009488&type=printable
spellingShingle Liwei Xiao
Jing Liu
Zongchao Sun
Yujing Yin
Yan Mao
Dengqiu Xu
Lin Liu
Zhisheng Xu
Qiqi Guo
Chenyun Ding
Wanping Sun
Likun Yang
Zheng Zhou
Danxia Zhou
Tingting Fu
Wenjing Zhou
Yuangang Zhu
Xiao-Wei Chen
John Zhong Li
Shuai Chen
Xiaoduo Xie
Zhenji Gan
AMPK-dependent and -independent coordination of mitochondrial function and muscle fiber type by FNIP1.
PLoS Genetics
title AMPK-dependent and -independent coordination of mitochondrial function and muscle fiber type by FNIP1.
title_full AMPK-dependent and -independent coordination of mitochondrial function and muscle fiber type by FNIP1.
title_fullStr AMPK-dependent and -independent coordination of mitochondrial function and muscle fiber type by FNIP1.
title_full_unstemmed AMPK-dependent and -independent coordination of mitochondrial function and muscle fiber type by FNIP1.
title_short AMPK-dependent and -independent coordination of mitochondrial function and muscle fiber type by FNIP1.
title_sort ampk dependent and independent coordination of mitochondrial function and muscle fiber type by fnip1
url https://journals.plos.org/plosgenetics/article/file?id=10.1371/journal.pgen.1009488&type=printable
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