Gasdermin D deficiency aggravates nephrocalcinosis-related chronic kidney disease with rendering macrophages vulnerable to necroptosis

Abstract Several forms of regulated necrosis contribute to the pathogenesis of crystal nephropathy, however, the role of pyroptosis, an inflammatory form of cell death involving the formation of gasdermin-D pores in internal and external cell membranes, in this condition remains unknown. Our transcr...

Full description

Saved in:
Bibliographic Details
Main Authors: Yoshihiro Kusunoki, Chenyu Li, Hao Long, Kanako Watanabe-Kusunoki, Meisi Kuang, Julian Aurelio Marschner, Andreas Linkermann, Stefanie Steiger, Hans-Joachim Anders
Format: Article
Language:English
Published: Nature Publishing Group 2025-04-01
Series:Cell Death and Disease
Online Access:https://doi.org/10.1038/s41419-025-07620-1
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849737748432289792
author Yoshihiro Kusunoki
Chenyu Li
Hao Long
Kanako Watanabe-Kusunoki
Meisi Kuang
Julian Aurelio Marschner
Andreas Linkermann
Stefanie Steiger
Hans-Joachim Anders
author_facet Yoshihiro Kusunoki
Chenyu Li
Hao Long
Kanako Watanabe-Kusunoki
Meisi Kuang
Julian Aurelio Marschner
Andreas Linkermann
Stefanie Steiger
Hans-Joachim Anders
author_sort Yoshihiro Kusunoki
collection DOAJ
description Abstract Several forms of regulated necrosis contribute to the pathogenesis of crystal nephropathy, however, the role of pyroptosis, an inflammatory form of cell death involving the formation of gasdermin-D pores in internal and external cell membranes, in this condition remains unknown. Our transcriptional and histological analyses suggest that Gsdmd in tubulointerstitital cells may contribute to the pathogenesis of chronic oxalate nephropathy. However, genetic deletion of Gsdmd exacerbated oxalate nephropathy in mice in association with enhanced CaOx crystal deposition and accelerated tubular epithelial cell injury. Pharmacological inhibition of necroptosis reversed this effect. Indeed, Gsdmd −/− bone marrow-derived macrophages were more prone to undergo necroptosis when stimulated with CaOx crystals compared to their wildtype counterparts. We conclude that gasdermin D suppresses the necroptosis pathway, which determines the outcome of oxalate nephropathy-related nephrocalcinosis.
format Article
id doaj-art-39edf185fc3e43d2a2351cf78bee139d
institution DOAJ
issn 2041-4889
language English
publishDate 2025-04-01
publisher Nature Publishing Group
record_format Article
series Cell Death and Disease
spelling doaj-art-39edf185fc3e43d2a2351cf78bee139d2025-08-20T03:06:50ZengNature Publishing GroupCell Death and Disease2041-48892025-04-0116111210.1038/s41419-025-07620-1Gasdermin D deficiency aggravates nephrocalcinosis-related chronic kidney disease with rendering macrophages vulnerable to necroptosisYoshihiro Kusunoki0Chenyu Li1Hao Long2Kanako Watanabe-Kusunoki3Meisi Kuang4Julian Aurelio Marschner5Andreas Linkermann6Stefanie Steiger7Hans-Joachim Anders8Renal Division, Department of Medicine IV, Hospital of the Ludwig-Maximilians-UniversityRenal Division, Department of Medicine IV, Hospital of the Ludwig-Maximilians-UniversityRenal Division, Department of Medicine IV, Hospital of the Ludwig-Maximilians-UniversityRenal Division, Department of Medicine IV, Hospital of the Ludwig-Maximilians-UniversityRenal Division, Department of Medicine IV, Hospital of the Ludwig-Maximilians-UniversityDepartment of Pharmacy, Ludwig-Maximilians-UniversityDepartment of Medicine V, University Medical Centre Mannheim, University of HeidelbergRenal Division, Department of Medicine IV, Hospital of the Ludwig-Maximilians-UniversityRenal Division, Department of Medicine IV, Hospital of the Ludwig-Maximilians-UniversityAbstract Several forms of regulated necrosis contribute to the pathogenesis of crystal nephropathy, however, the role of pyroptosis, an inflammatory form of cell death involving the formation of gasdermin-D pores in internal and external cell membranes, in this condition remains unknown. Our transcriptional and histological analyses suggest that Gsdmd in tubulointerstitital cells may contribute to the pathogenesis of chronic oxalate nephropathy. However, genetic deletion of Gsdmd exacerbated oxalate nephropathy in mice in association with enhanced CaOx crystal deposition and accelerated tubular epithelial cell injury. Pharmacological inhibition of necroptosis reversed this effect. Indeed, Gsdmd −/− bone marrow-derived macrophages were more prone to undergo necroptosis when stimulated with CaOx crystals compared to their wildtype counterparts. We conclude that gasdermin D suppresses the necroptosis pathway, which determines the outcome of oxalate nephropathy-related nephrocalcinosis.https://doi.org/10.1038/s41419-025-07620-1
spellingShingle Yoshihiro Kusunoki
Chenyu Li
Hao Long
Kanako Watanabe-Kusunoki
Meisi Kuang
Julian Aurelio Marschner
Andreas Linkermann
Stefanie Steiger
Hans-Joachim Anders
Gasdermin D deficiency aggravates nephrocalcinosis-related chronic kidney disease with rendering macrophages vulnerable to necroptosis
Cell Death and Disease
title Gasdermin D deficiency aggravates nephrocalcinosis-related chronic kidney disease with rendering macrophages vulnerable to necroptosis
title_full Gasdermin D deficiency aggravates nephrocalcinosis-related chronic kidney disease with rendering macrophages vulnerable to necroptosis
title_fullStr Gasdermin D deficiency aggravates nephrocalcinosis-related chronic kidney disease with rendering macrophages vulnerable to necroptosis
title_full_unstemmed Gasdermin D deficiency aggravates nephrocalcinosis-related chronic kidney disease with rendering macrophages vulnerable to necroptosis
title_short Gasdermin D deficiency aggravates nephrocalcinosis-related chronic kidney disease with rendering macrophages vulnerable to necroptosis
title_sort gasdermin d deficiency aggravates nephrocalcinosis related chronic kidney disease with rendering macrophages vulnerable to necroptosis
url https://doi.org/10.1038/s41419-025-07620-1
work_keys_str_mv AT yoshihirokusunoki gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis
AT chenyuli gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis
AT haolong gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis
AT kanakowatanabekusunoki gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis
AT meisikuang gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis
AT julianaureliomarschner gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis
AT andreaslinkermann gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis
AT stefaniesteiger gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis
AT hansjoachimanders gasderminddeficiencyaggravatesnephrocalcinosisrelatedchronickidneydiseasewithrenderingmacrophagesvulnerabletonecroptosis