Rosai–Dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post-COVID-19 infection

We report a rare presentation of Rosai–Dorfman disease (RDD) as scleritis transforming to a nodule in a female with multisystem inflammatory syndrome following COVID-19 infection. A 54-year-old female presented to us first in August 2022 with redness and slight discomfort in both eyes of 2 weeks’ du...

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Main Authors: Nashra Alma, Smitha Kuthyar Shambu, Kalpana Babu
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2025-04-01
Series:Taiwan Journal of Ophthalmology
Subjects:
Online Access:https://journals.lww.com/10.4103/tjo.TJO-D-25-00009
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author Nashra Alma
Smitha Kuthyar Shambu
Kalpana Babu
author_facet Nashra Alma
Smitha Kuthyar Shambu
Kalpana Babu
author_sort Nashra Alma
collection DOAJ
description We report a rare presentation of Rosai–Dorfman disease (RDD) as scleritis transforming to a nodule in a female with multisystem inflammatory syndrome following COVID-19 infection. A 54-year-old female presented to us first in August 2022 with redness and slight discomfort in both eyes of 2 weeks’ duration. She had a history of multisystem inflammatory syndrome post-COVID-19 infection. Although she presented with scleritis (oculus uterque), it continued to persist with a course of oral and topical steroids. Laboratory investigations including autoimmune profile were negative. Only QuantiFERON-TB Gold test was positive. High-resolution computed tomography showed a few subcentimeter enlarged mediastinal lymph nodes and a cluster of enlarged cervical lymph nodes. Biopsy showed chronic granulomatous inflammation with no caseation, negative for Mycobacterium tuberculosis. Over a year, this transformed to a scleral nodule. Excision biopsy confirmed RDD disease. Whole body positron emission tomography-computerized tomography confirmed no active lesions elsewhere. She was started on methotrexate. At 1-year follow-up, there was no recurrence.
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institution Kabale University
issn 2211-5056
2211-5072
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publisher Wolters Kluwer Medknow Publications
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series Taiwan Journal of Ophthalmology
spelling doaj-art-391576b30cf3422bbe801e54f8a78c6e2025-08-20T03:29:35ZengWolters Kluwer Medknow PublicationsTaiwan Journal of Ophthalmology2211-50562211-50722025-04-0115231932210.4103/tjo.TJO-D-25-00009Rosai–Dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post-COVID-19 infectionNashra AlmaSmitha Kuthyar ShambuKalpana BabuWe report a rare presentation of Rosai–Dorfman disease (RDD) as scleritis transforming to a nodule in a female with multisystem inflammatory syndrome following COVID-19 infection. A 54-year-old female presented to us first in August 2022 with redness and slight discomfort in both eyes of 2 weeks’ duration. She had a history of multisystem inflammatory syndrome post-COVID-19 infection. Although she presented with scleritis (oculus uterque), it continued to persist with a course of oral and topical steroids. Laboratory investigations including autoimmune profile were negative. Only QuantiFERON-TB Gold test was positive. High-resolution computed tomography showed a few subcentimeter enlarged mediastinal lymph nodes and a cluster of enlarged cervical lymph nodes. Biopsy showed chronic granulomatous inflammation with no caseation, negative for Mycobacterium tuberculosis. Over a year, this transformed to a scleral nodule. Excision biopsy confirmed RDD disease. Whole body positron emission tomography-computerized tomography confirmed no active lesions elsewhere. She was started on methotrexate. At 1-year follow-up, there was no recurrence.https://journals.lww.com/10.4103/tjo.TJO-D-25-00009biopsycovid-19 exposureimmunosuppressionmultisystem inflammatory syndromerosai–dorfman diseasescleral nodulescleritis
spellingShingle Nashra Alma
Smitha Kuthyar Shambu
Kalpana Babu
Rosai–Dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post-COVID-19 infection
Taiwan Journal of Ophthalmology
biopsy
covid-19 exposure
immunosuppression
multisystem inflammatory syndrome
rosai–dorfman disease
scleral nodule
scleritis
title Rosai–Dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post-COVID-19 infection
title_full Rosai–Dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post-COVID-19 infection
title_fullStr Rosai–Dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post-COVID-19 infection
title_full_unstemmed Rosai–Dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post-COVID-19 infection
title_short Rosai–Dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post-COVID-19 infection
title_sort rosai dorfman disease presenting as a scleral nodule in a female with multisystem inflammatory syndrome post covid 19 infection
topic biopsy
covid-19 exposure
immunosuppression
multisystem inflammatory syndrome
rosai–dorfman disease
scleral nodule
scleritis
url https://journals.lww.com/10.4103/tjo.TJO-D-25-00009
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AT smithakuthyarshambu rosaidorfmandiseasepresentingasascleralnoduleinafemalewithmultisysteminflammatorysyndromepostcovid19infection
AT kalpanababu rosaidorfmandiseasepresentingasascleralnoduleinafemalewithmultisysteminflammatorysyndromepostcovid19infection